Mitochondrial Trifunctional Protein [mitochondriální trifunkční protein]

topical
2
Terms

FA beta-OMC
Mitochondrial Fatty Acid beta-Oxidation Trifunctional Protein
Mitochondrial Long Chain Enoyl CoA Hydratase 3 Hydroxyacyl CoA Dehydrogenase 3 Ketoacyl CoA Thiolase Trifunctional Protein

Persistent link   https://www.medvik.cz/link/D063991
Definition

A mitochondrial protein consisting of four alpha-subunits and four beta-subunits. It contains enoyl-CoA hydratase, long-chain-3-hydroxyacyl-CoA dehydrogenase, and acetyl-CoA C-acyltransferase activities and plays an important role in the metabolism of long chain FATTY ACIDS.

DUI
D063991 MeSH Browser
CUI
M0578881
History note
2014
Public note
2014; MITOCHONDRIAL FATTY ACID BETA-OXIDATION TRIFUNCTIONAL PROTEIN (now MITOCHONDRIAL TRIFUNCTIONAL PROTEIN) was indexed under MULTIENZYME COMPLEXES 1994-2013

D Chemicals and Drugs
D08.811 Enzymes 1 547
D08.811.520 Lyases 22
D08.811.520.241 Carbon-Oxygen Lyases 1
D08.811.520.241.300 Hydro-Lyases 32
D08.811.520.241.300.250 Enoyl-CoA Hydratase 2
D08.811.520.241.300.250.249 Mitochondrial Trifunctional Protein 2
D08.811.520.241.300.250.750 Peroxisomal Bifunctional Enzyme
D08.811.641.249 Acetyl-CoA Carboxylase 4
D08.811.641.752 Cyclin-Dependent Kinase 9 8
D08.811.641.773 Peroxiredoxin VI 3
D08.811.641.843 Phosphofructokinase-2
D08.811.682 Oxidoreductases 446
D08.811.682.047 Alcohol Oxidoreductases 97
D08.811.682.047.820.150 3-Hydroxyacyl CoA Dehydrogenases 15
D08.811.682.047.820.150.707 Long-Chain-3-Hydroxyacyl-CoA Dehydrogenase 2
D08.811.682.047.820.150.707.249 Mitochondrial Trifunctional Protein 2
D08.811.682.047.820.150.707.249.500 Mitochondrial Trifunctional Protein, alpha Subunit
D08.811.913 Transferases 72
D08.811.913.050 Acyltransferases 169
D08.811.913.050.080 Acetyl-CoA C-Acyltransferase 4
D08.811.913.050.080.249 Mitochondrial Trifunctional Protein 2
D12.776 Proteins 2 577
D12.776.543 Membrane Proteins 849
D12.776.543.029 Amphiregulin 3
D12.776.543.080 Ankyrins 10
D12.776.543.090 Arrestins 6
D12.776.543.095 B7 Antigens 3
D12.776.543.116 Bcl-2-Like Protein 11 5
D12.776.543.131 Cadherin Related Proteins 1
D12.776.543.162 Calnexin 4
D12.776.543.178 Carbonic Anhydrase IX 19
D12.776.543.193 Chemokine CX3CL1 3
D12.776.543.225 Dysferlin
D12.776.543.250 Dystrophin 46
D12.776.543.287 Ephrins 1
D12.776.543.306 gp100 Melanoma Antigen 1
D12.776.543.484 Lipid-Linked Proteins 1
D12.776.543.550 Membrane Glycoproteins 200
D12.776.543.585 Membrane Transport Proteins 207
D12.776.543.620 Myelin Proteins 32
D12.776.543.653 NADPH Oxidases 44
D12.776.543.685 Neurofibromin 2 3
D12.776.543.696 Presenilins 6
D12.776.543.750 Receptors, Cell Surface 511
D12.776.543.800 Serrate-Jagged Proteins 1
D12.776.543.850 Spectrin 20
D12.776.543.900 Tetraspanins 13
D12.776.543.940 Tight Junction Proteins 5
D12.776.543.985 Utrophin 1
D12.776.575 Mitochondrial Proteins 208
D12.776.575.280 DNA Polymerase gamma 3
D12.776.575.374 Endopeptidase Clp
D12.776.575.562 Ferrochelatase 11
D12.776.575.609 Frataxin 2
D12.776.575.812 Peroxiredoxin III 2
D12.776.575.844 Prohibitins 1
D12.776.575.875 Sirtuin 3 5