The association of enchondromatosis with malignant transformed chondrosarcoma and ovarian juvenile granulosa cell tumor (Ollier disease)
Language English Country China (Republic : 1949- ) Media print
Document type Case Reports, Journal Article
PubMed
28420520
DOI
10.1016/j.tjog.2017.02.002
PII: S1028-4559(17)30050-5
Knihovny.cz E-resources
- Keywords
- Ollier disease, chondrosarcoma, enchondromatosis, juvenile granulosa cell tumor, ultrasound,
- MeSH
- Chondrosarcoma complications diagnostic imaging MeSH
- Enchondromatosis complications diagnostic imaging MeSH
- Humans MeSH
- Young Adult MeSH
- Granulosa Cell Tumor complications diagnostic imaging MeSH
- Abdominal Neoplasms complications diagnostic imaging MeSH
- Ovarian Neoplasms complications diagnostic imaging MeSH
- Tomography, X-Ray Computed MeSH
- Ultrasonography MeSH
- Check Tag
- Humans MeSH
- Young Adult MeSH
- Female MeSH
- Publication type
- Journal Article MeSH
- Case Reports MeSH
OBJECTIVE: Ovarian juvenile granulosa cell tumor has an interesting association with multiple enchondromatosis (Ollier disease and Maffucci syndrome) and should be considered a leading diagnosis when an ovarian mass is found in young patients with these conditions. Besides the association with nonskeletal malignancies, there is a high risk of malignant transformation of enchondroma in chondrosarcoma as was also the case in this instance. CASE REPORT: The report uses multiple images to document the representative and characteristic markers of multiple enchondromas in a 22-year-old patient with Ollier disease complicated by malignant transformation of chondrosarcoma and in whom the disease is associated with ovarian juvenile granulosa cell tumor of the right ovary. CONCLUSION: It is important to recognize that when the female patient presents with enchondromatosis and a large unilateral multilocular-solid ovarian mass, the specific diagnosis of granulosa cell tumor can be made with high accuracy.
Department of Pathology 2nd Faculty of Medicine Charles University Czech Republic
Department of Pathology Bulovka Hospital 1st Faculty of Medicine Charles University Czech Republic
Orthopedic Clinic Bulovka Hospital 1st Faculty of Medicine Charles University Czech Republic
References provided by Crossref.org
