Dandy-Walker Syndrome [Dandyův-Walkerův syndrom]

topical
6
Terms

Dandy Walkerův syndrom
Dandy-Walker syndrom
Dandy-Walkerova malformace
Dandyho-Walkerův syndrom
Dandyova-Walkerova malformace
Dandyův-Walkerův syndrom, familiární formy
malformace Dandy-Walker

 

Dandy-Walker Complex
Dandy-Walker Cyst
Dandy-Walker Deformity
Dandy-Walker Malformation
Dandy-Walker Syndrome, Familial
Hydrocephalus, Internal, Dandy-Walker Type
Hydrocephalus, Noncommunicating, Dandy-Walker Type
Luschka-Magendie Foramina Atresia

Persistent link   https://www.medvik.cz/link/D003616
Definition

A congenital abnormality of the central nervous system marked by failure of the midline structures of the cerebellum to develop, dilation of the fourth ventricle, and upward displacement of the transverse sinuses, tentorium, and torcula. Clinical features include occipital bossing, progressive head enlargement, bulging of anterior fontanelle, papilledema, ataxia, gait disturbances, nystagmus, and intellectual compromise. (From Menkes, Textbook of Child Neurology, 5th ed, pp294-5)

DUI
D003616 MeSH Browser
CUI
M0005653
Previous indexing
Cerebral Ventricles/abnormalities (1966-1969); Hydrocephalus (1966-1969)
History note
1991(1970)
Public note
1991; see HYDROCEPHALUS 1970-1990

C Diseases
C10.228.140 Brain Diseases 1 186
C10.228.140.252 Cerebellar Diseases 168
C10.228.140.252.190 Cerebellar Ataxia 65
C10.228.140.252.200 Cerebellar Neoplasms 66
C10.228.140.252.300 Dandy-Walker Syndrome 6
C10.228.140.252.500 Miller Fisher Syndrome 12
C10.228.140.252.700 Spinocerebellar Degenerations 30
C10.228.140.602 Hydrocephalus 405
C10.228.140.602.500 Dandy-Walker Syndrome 6
C10.228.140.602.750 Hydrocephalus, Normal Pressure 92
C10.500.450 Hydranencephaly 3
C10.500.680 Neural Tube Defects 78
C16.131.666.205 Dandy-Walker Syndrome 6
C16.131.666.450 Hydranencephaly 3
C16.131.666.680 Neural Tube Defects 78
C16.131.666.763 Optic Nerve Hypoplasia 1

3C syndrome Disease MeSH Browser

Chitayat Moore Del Bigio syndrome Disease MeSH Browser

Craniosynostosis, sagittal, with Dandy-Walker malformation and hydrocephalus Disease MeSH Browser

Dandy Walker cyst Disease MeSH Browser

Dandy Walker malformation postaxial polydactyly Disease MeSH Browser

Dandy Walker variant Disease MeSH Browser

Dandy-Walker Malformation With Occipital Cephalocele, Autosomal Dominant Disease MeSH Browser

Dandy-walker malformation with mental retardation, macrocephaly, myopia, and brachytelephalangy Disease MeSH Browser

Mental retardation, X-linked, syndromic 5 Disease MeSH Browser

Nasopharyngeal teratoma with Dandy Walker diaphragmatic hernia Disease MeSH Browser

Renal hepatic pancreatic dysplasia Dandy Walker cyst Disease MeSH Browser

Volcke Soekarman syndrome Disease MeSH Browser