Pseudohypoaldosteronism [pseudohypoaldosteronismus]
- Terms
-
familiární hyperkalemie a hypertenze
Gordonův syndrom
pseudohypoaldosteronismus typu 1
pseudohypoaldosteronismus typu 2
pseudohypoaldosteronismus typu I
pseudohypoaldosteronismus typu I, autozomálně dominantní
pseudohypoaldosteronismus typu I, autozomálně recesivní
pseudohypoaldosteronismus typu II
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Familial Hyperpotassemia and Hypertension
Familial Hypertensive Hyperkalemia
Gordon Hyperkalemia-Hypertension Syndrome
Hyperpotassemia and Hypertension, Familial
Hypertensive Hyperkalemia, Familial
Pseudohypoaldosteronism Type 1
Pseudohypoaldosteronism Type 1, Autosomal Dominant
Pseudohypoaldosteronism Type 1, Autosomal Recessive
Pseudohypoaldosteronism Type 2
Pseudohypoaldosteronism Type I
Pseudohypoaldosteronism Type II
Pseudohypoaldosteronism, Type I
Pseudohypoaldosteronism, Type I, Autosomal Dominant
Pseudohypoaldosteronism, Type I, Autosomal Recessive
Pseudohypoaldosteronism, Type II
A heterogeneous group of disorders characterized by renal electrolyte transport dysfunctions. Congenital forms are rare autosomal disorders characterized by neonatal hypertension, HYPERKALEMIA, increased RENIN activity and ALDOSTERONE concentration. The Type I features HYPERKALEMIA with sodium wasting; Type II, HYPERKALEMIA without sodium wasting. Pseudohypoaldosteronism can be the result of a defective renal electrolyte transport protein or acquired after KIDNEY TRANSPLANTATION.
- DUI
- D011546 MeSH Browser
- CUI
- M0017948
- Previous indexing
- Aldosterone (1971-1987); Hyperaldosteronism (1975-1980); Renal Tubular Transport, Inborn Errors (1971-1987)
- History note
- 1991(1988); use RENAL TUBULAR TRANSPORT, INBORN ERRORS 1988-90
- Public note
- 1991; see RENAL TUBULAR TRANSPORT, INBORN ERRORS 1988-90
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