Gitelman Syndrome [Gitelmanův syndrom]

topical
17
Terms

primární renální tubulární hypomagnezémie-hypokalemie s hypokalciurií

 

Familial Hypokalemia-Hypomagnesemia
Gitelman's Syndrome
Hypokalemia-Hypomagnesemia, Primary Renotubular, with Hypocalciuria
Hypomagnesemia-Hypokalemia, Primary Renotubular, with Hypocalciuria
Potassium and Magnesium Depletion
Primary Renotubular, Hypokalemia-Hypomagnesemia with Hypocalciuria
Primary Renotubular, Hypomagnesemia-Hypokalemia with Hypocalciuria
Tubular Hypomagnesemia-Hypokalemia with Hypocalcuria

Persistent link   https://www.medvik.cz/link/D053579
Definition

An inherited renal disorder characterized by defective NaCl reabsorption in the convoluted DISTAL KIDNEY TUBULE leading to HYPOKALEMIA. In contrast with BARTTER SYNDROME, Gitelman syndrome includes hypomagnesemia and normocalcemic hypocalciuria, and is caused by mutations in the thiazide-sensitive SODIUM-POTASSIUM-CHLORIDE SYMPORTERS.

DUI
D053579 MeSH Browser
CUI
M0494801
Previous indexing
Bartter Syndrome (1994-2006); Hypokalemia (1987-2006); Magnesium (1987-2006)
History note
2007
Public note
2007

C Diseases
C12.050.351.968 Urologic Diseases 834
C12.050.351.968.419 Kidney Diseases 3 060
C12.050.351.968.419.815 Renal Tubular Transport, Inborn Errors 36
C12.050.351.968.419.815.093 Acidosis, Renal Tubular 59
C12.050.351.968.419.815.279 Bartter Syndrome 19
C12.050.351.968.419.815.364 Dent Disease 1
C12.050.351.968.419.815.450 Fanconi Syndrome 23
C12.050.351.968.419.815.491 Gitelman Syndrome 17
C12.050.351.968.419.815.532 Glycosuria, Renal 36
C12.050.351.968.419.815.647 Hypophosphatemia, Familial 12
C12.050.351.968.419.815.683 Liddle Syndrome 4
C12.050.351.968.419.815.720 Oculocerebrorenal Syndrome 9
C12.050.351.968.419.815.770 Pseudohypoaldosteronism 9
C12.050.351.968.419.815.885 Renal Aminoacidurias 27
C12.200.777 Urologic Diseases 834
C12.200.777.419 Kidney Diseases 3 060
C12.200.777.419.815.093 Acidosis, Renal Tubular 59
C12.200.777.419.815.279 Bartter Syndrome 19
C12.200.777.419.815.364 Dent Disease 1
C12.200.777.419.815.450 Fanconi Syndrome 23
C12.200.777.419.815.491 Gitelman Syndrome 17
C12.200.777.419.815.532 Glycosuria, Renal 36
C12.200.777.419.815.647 Hypophosphatemia, Familial 12
C12.200.777.419.815.683 Liddle Syndrome 4
C12.200.777.419.815.720 Oculocerebrorenal Syndrome 9
C12.200.777.419.815.770 Pseudohypoaldosteronism 9
C12.200.777.419.815.885 Renal Aminoacidurias 27
C12.950.419 Kidney Diseases 3 060
C12.950.419.815.093 Acidosis, Renal Tubular 59
C12.950.419.815.279 Bartter Syndrome 19
C12.950.419.815.364 Dent Disease 1
C12.950.419.815.450 Fanconi Syndrome 23
C12.950.419.815.491 Gitelman Syndrome 17
C12.950.419.815.532 Glycosuria, Renal 36
C12.950.419.815.647 Hypophosphatemia, Familial 12
C12.950.419.815.683 Liddle Syndrome 4
C12.950.419.815.720 Oculocerebrorenal Syndrome 9
C12.950.419.815.770 Pseudohypoaldosteronism 9
C12.950.419.815.885 Renal Aminoacidurias 27
C16.320.831.093 Acidosis, Renal Tubular 59
C16.320.831.271 Dent Disease 1
C16.320.831.450 Fanconi Syndrome 23
C16.320.831.491 Gitelman Syndrome 17
C16.320.831.532 Glycosuria, Renal 36
C16.320.831.647 Hypophosphatemia, Familial 12
C16.320.831.698 Liddle Syndrome 4
C16.320.831.770 Pseudohypoaldosteronism 9
C16.320.831.885 Renal Aminoacidurias 27