Anti-Neutrophil Cytoplasmic Antibody-Associated Vasculitis [ANCA-asociované vaskulitidy]

topical
119
Terms

ANCA-asociovaná vaskulitida
pauciimunní vaskulitida

 

ANCA-Associated Vasculitides
ANCA-Associated Vasculitis
Pauci-Immune Vasculitis

Persistent link   https://www.medvik.cz/link/D056648
Definition

Group of systemic vasculitis with a strong association with ANCA. The disorders are characterized by necrotizing inflammation of small and medium size vessels, with little or no immune-complex deposits in vessel walls.

DUI
D056648 MeSH Browser
CUI
M0528192
History note
2010
Public note
2010

C Diseases
C14.907 Vascular Diseases 1 789
C14.907.940 Vasculitis 480
C14.907.940.897 Systemic Vasculitis 18
C14.907.940.897.249.249 Churg-Strauss Syndrome 81
C14.907.940.897.249.500 Microscopic Polyangiitis 30
C14.907.940.897.249.750 Granulomatosis with Polyangiitis 218
C14.907.940.897.500 Polyarteritis Nodosa 92
C14.907.940.897.750 Rheumatoid Vasculitis 5
C17.800 Skin Diseases 2 796
C17.800.862.060 Angiomatosis, Bacillary 5
C17.800.862.105.500 Churg-Strauss Syndrome 81
C17.800.862.105.750 Microscopic Polyangiitis 30
C17.800.862.105.875 Granulomatosis with Polyangiitis 218
C17.800.862.150 Behcet Syndrome 56
C17.800.862.201 Cryoglobulinemia 72
C17.800.862.252 Giant Cell Arteritis 138
C17.800.862.329 IgA Vasculitis 76
C17.800.862.406 Livedoid Vasculopathy
C17.800.862.625 Polyarteritis Nodosa 92
C17.800.862.675 Pyoderma Gangrenosum 77
C17.800.862.775 Sneddon Syndrome 2
C17.800.862.875 Takayasu Arteritis 92
C17.800.862.945 Urticaria 298
C20.111 Autoimmune Diseases 1 932
C20.111.163 Addison Disease 128
C20.111.193.500 Churg-Strauss Syndrome 81
C20.111.193.750 Microscopic Polyangiitis 30
C20.111.198 Arthritis, Juvenile 474
C20.111.199 Arthritis, Rheumatoid 3 114
C20.111.327 Diabetes Mellitus, Type 1 3 001
C20.111.555 Graves Disease 255
C20.111.730 Pemphigoid, Bullous 87
C20.111.736 Pemphigus 207