Megalencephaly [megalencefalie]

topical
7
Terms

macrocephalus
makrocefalie
makrocefalus

 

Macrocephaly
Megacephaly
Megalocephaly

Persistent link   https://www.medvik.cz/link/D058627
Definition

A congenital abnormality in which the occipitofrontal circumference is greater than two standard deviations above the mean for a given age. It is associated with HYDROCEPHALUS; SUBDURAL EFFUSION; ARACHNOID CYSTS; or is part of a genetic condition (e.g., ALEXANDER DISEASE; SOTOS SYNDROME).

DUI
D058627 MeSH Browser
CUI
M0543765
Previous indexing
Craniofacial Abnormalities (1994-2010); Head/abnormalities (1970-2010)
History note
2011; use Macrocephaly 2011-2014, Megalencephaly was under Macrocephaly 2011-2014
Public note
2011; use Macrocephaly 2011-2014, Megalencephaly was under Macrocephaly 2011-2014

C Diseases
C05.660.207.103 22q11 Deletion Syndrome 2
C05.660.207.207 Cleidocranial Dysplasia 7
C05.660.207.219 Costello Syndrome 3
C05.660.207.231 Craniofacial Dysostosis 28
C05.660.207.240 Craniosynostoses 56
C05.660.207.325 Donohue Syndrome 1
C05.660.207.410 Holoprosencephaly 9
C05.660.207.525 LEOPARD Syndrome 11
C05.660.207.532 Loeys-Dietz Syndrome 7
C05.660.207.536 Megalencephaly 7
C05.660.207.536.500 Hemimegalencephaly 3
C05.660.207.620 Microcephaly 78
C05.660.207.690 Noonan Syndrome 52
C05.660.207.700 Orofaciodigital Syndromes 7
C05.660.207.707 Plagiocephaly 3
C05.660.207.720 Platybasia 12
C05.660.207.850 Rubinstein-Taybi Syndrome 12
C05.660.207.925 Silver-Russell Syndrome 3
C10.500.507.400.125 Focal Cortical Dysplasia 12
C10.500.507.400.187 Hippocampal Sclerosis 1
C10.500.507.400.249 Megalencephaly 7
C10.500.507.400.249.500 Hemimegalencephaly 3
C10.500.507.400.500 Microcephaly 78
C10.500.507.400.750 Tuberous Sclerosis 144
C16.131.621.207 Craniofacial Abnormalities 82
C16.131.621.207.103 22q11 Deletion Syndrome 2
C16.131.621.207.207 Cleidocranial Dysplasia 7
C16.131.621.207.231 Craniofacial Dysostosis 28
C16.131.621.207.240 Craniosynostoses 56
C16.131.621.207.410 Holoprosencephaly 9
C16.131.621.207.525 LEOPARD Syndrome 11
C16.131.621.207.532 Megalencephaly 7
C16.131.621.207.532.500 Hemimegalencephaly 3
C16.131.621.207.540 Maxillofacial Abnormalities 28
C16.131.621.207.620 Microcephaly 78
C16.131.621.207.690 Noonan Syndrome 52
C16.131.621.207.700 Orofaciodigital Syndromes 7
C16.131.621.207.707 Plagiocephaly 3
C16.131.621.207.720 Platybasia 12
C16.131.621.207.850 Rubinstein-Taybi Syndrome 12
C16.131.666.507.400.125 Focal Cortical Dysplasia 12
C16.131.666.507.400.187 Hippocampal Sclerosis 1
C16.131.666.507.400.249 Megalencephaly 7
C16.131.666.507.400.249.500 Hemimegalencephaly 3
C16.131.666.507.400.500 Microcephaly 78
C16.131.666.507.400.750 Tuberous Sclerosis 144

Bagatelle Cassidy syndrome Disease MeSH Browser

Chromosome 1q21.1 Deletion Syndrome, 1.35-Mb Disease MeSH Browser

Ehlers-Danlos Syndrome VI Phenotype with Macrocephaly Disease MeSH Browser

Facial Abnormalities, Kyphoscoliosis, and Mental Retardation Disease MeSH Browser

Fryns Macrocephaly Disease MeSH Browser

Kniest like dysplasia lethal Disease MeSH Browser

Macrocephaly Autism Syndrome Disease MeSH Browser

Macrocephaly with Multiple Epiphyseal Dysplasia and Distinctive Facies Disease MeSH Browser

Macrocephaly, Alopecia, Cutis Laxa, and Scoliosis Disease MeSH Browser

Macrocephaly, benign familial Disease MeSH Browser

Macrosomia obesity macrocephaly ocular abnormalities Disease MeSH Browser

Megalencephaly cutis marmorata telangiectatica congenita Disease MeSH Browser

Megalencephaly with Dysmyelination Disease MeSH Browser

Mental Retardation, X-Linked 93 Disease MeSH Browser

Mental Retardation, X-Linked, Syndromic, Turner Type Disease MeSH Browser

Mental retardation, macrocephaly, short stature and craniofacial dysmorphism Disease MeSH Browser

Neuhauser syndrome Disease MeSH Browser

Pectus Excavatum, Macrocephaly, Short Stature, Dysplastic Nails Disease MeSH Browser

Polyhydramnios, Megalencephaly, And Symptomatic Epilepsy Disease MeSH Browser

Vater Association With Hydrocephalus Disease MeSH Browser

Zori Stalker Williams syndrome Disease MeSH Browser