Immunoglobulin Light-chain Amyloidosis [primární amyloidóza]
topical
35
- Terms
-
AL amyloidóza
-
AL Amyloidosis
Amyloidosis, Immunoglobulin Light-chain
Amyloidosis, Primary
Monoclonal Immunoglobulin Deposition Disease
Primary Amyloidosis
Primary Systemic Amyloidosis
Persistent link
https://www.medvik.cz/link/D000075363
Definition
A nonproliferative disorder of PLASMA CELLS characterized by excessive production and misfolding of IMMUNOGLOBULIN LIGHT CHAINS that form insoluble amyloid fibrils (see AMYLOID DEPOSITS) in various tissues. Clinical features include LIVER FAILURE; MULTIPLE MYELOMA; NEPHROTIC SYNDROME; RESTRICTIVE CARDIOMYOPATHY, and neuropathies.
- DUI
- D000075363 MeSH Browser
- CUI
- M000630238
- History note
- 2018(2010)
- Public note
- 2018; PRIMARY AMYLOIDOSIS was indexed under AMYLOIDOSIS 2010-2017
Allowable subheadings
- BL
- blood 0
- CF
- cerebrospinal fluid 0
- CI
- chemically induced 0
- CL
- classification 0
- CO
- complications 1
- CN
- congenital 0
- DI
- diagnosis 18
- DG
- diagnostic imaging 0
- DH
- diet therapy 0
- DT
- drug therapy 7
- EC
- economics 1
- EM
- embryology 0
- EN
- enzymology 0
- EP
- epidemiology 2
- EH
- ethnology 0
- ET
- etiology 3
- GE
- genetics 3
- HI
- history 0
- IM
- immunology 1
- ME
- metabolism 0
- MI
- microbiology 0
- MO
- mortality 0
- NU
- nursing 0
- PS
- parasitology 0
- PA
- pathology 6
- PP
- physiopathology 0
- PC
- prevention & control 0
- PX
- psychology 0
- RT
- radiotherapy 0
- RH
- rehabilitation 0
- SU
- surgery 0
- TH
- therapy 11
- UR
- urine 0
- VE
- veterinary 0
- VI
- virology 0
...
Occurrences in Medvik records
C
Diseases