hyperlipoproteinemie typ II [Hyperlipoproteinemia Type II]

tematický
455
Termíny

autozomálně dominantní hypercholesterolemie
autozomálně dominantní hypercholesterolemie typu B
autozomálně dominantní hypercholesterolemie, typ B
esenciální hypercholesterolemie
familiární defekt apolipoproteinu B-100
familiární hypercholesterolemická xantomatóza
familiární hypercholesterolemie
familiární kombinovaná hypercholesterolemie
familiární kombinovaná hyperlipoproteinemie
hyperbetalipoproteinemie
hyperbetalipoproteinémie
hypercholesterolémie esenciální
hypercholesterolémie familiární
hyperlipoproteinémie typ II
hyperlipoproteinemie typ IIa
hyperlipoproteinémie typ IIa
hyperlipoproteinemie typ IIb
hyperlipoproteinémie typ IIb
porucha LDL receptorů

 

Apolipoprotein B-100, Familial Defective
Apolipoprotein B-100, Familial Ligand-Defective
Familial Combined Hyperlipoproteinemia
Hyper-beta-Lipoproteinemia
Hyper-Low Density Lipoproteinemia
Hyper-Low-Density-Lipoproteinemia
Hyperbetalipoproteinemia
Hypercholesterolemia, Autosomal Dominant
Hypercholesterolemia, Autosomal Dominant, Type B
Hypercholesterolemia, Essential
Hypercholesterolemia, Familial
Hypercholesterolemic Xanthomatosis, Familial
Hyperlipoproteinemia Type 2
Hyperlipoproteinemia Type IIa
Hyperlipoproteinemia Type IIb
Hyperlipoproteinemia, Type II
Hyperlipoproteinemia, Type IIa
LDL Receptor Disorder

Perzistentní odkaz   https://www.medvik.cz/link/D006938
Definice

Skupina familiárních onemocnění charakterizovaná zvýšenou cirkulací cholesterolu obsaženého buď v LIPOPTROTEINech LDL nebo v LIPOPTROTEINech VLDL (pre-beta lipoproteiny).

A group of familial disorders characterized by elevated circulating cholesterol contained in either LOW-DENSITY LIPOPROTEINS alone or also in VERY-LOW-DENSITY LIPOPROTEINS (pre-beta lipoproteins).

DUI
D006938 MeSH Prohlížeč
CUI
M0010819
Předchozí užití
Hypercholesterolemia (1966-1979); Hyperlipidemia/familial & genetic (1966-1979)
Historická pozn.
2007 (1980)
Veřejná pozn.
2007; see HYPERCHOLESTEROLEMIA, FAMILIAL 1980-2007

C Nemoci
C16.320.565.398.224 Barthův syndrom 6
C16.320.565.398.465 hyperlipoproteinemie typ I 21
C16.320.565.398.481 hyperlipoproteinemie typ II 455
C16.320.565.398.483 hyperlipoproteinemie typ III 19
C16.320.565.398.487 hyperlipoproteinemie typ IV 14
C16.320.565.398.493 hyperlipoproteinemie typ V 6
C16.320.565.398.500 hypolipoproteinemie 35
C16.320.565.398.641 lipidózy 35
C18.452 metabolické nemoci 1 196
C18.452.584.500 dyslipidemie 1 634
C18.452.584.500.500 hyperlipidemie 1 238
C18.452.584.500.500.644 hyperlipoproteinemie 771
C18.452.584.500.500.644.237 hyperlipoproteinemie typ I 21
C18.452.584.500.500.644.475 hyperlipoproteinemie typ II 455
C18.452.584.500.500.644.475.500 homozygotní familiární hypercholesterolemie 5
C18.452.584.500.500.644.485 hyperlipoproteinemie typ III 19
C18.452.584.500.500.644.490 hyperlipoproteinemie typ IV 14
C18.452.584.500.500.644.495 hyperlipoproteinemie typ V 6
C18.452.584.563.224 Barthův syndrom 6
C18.452.584.563.465 hyperlipoproteinemie typ I 21
C18.452.584.563.481 hyperlipoproteinemie typ II 455
C18.452.584.563.483 hyperlipoproteinemie typ III 19
C18.452.584.563.487 hyperlipoproteinemie typ IV 14
C18.452.584.563.493 hyperlipoproteinemie typ V 6
C18.452.584.563.500 hypolipoproteinemie 35
C18.452.584.563.641 lipidózy 35
C18.452.584.563.824 Shwachmanův-Diamondův syndrom 2
C18.452.648.398.224 Barthův syndrom 6
C18.452.648.398.465 hyperlipoproteinemie typ I 21
C18.452.648.398.481 hyperlipoproteinemie typ II 455
C18.452.648.398.483 hyperlipoproteinemie typ III 19
C18.452.648.398.487 hyperlipoproteinemie typ IV 14
C18.452.648.398.493 hyperlipoproteinemie typ V 6
C18.452.648.398.500 hypolipoproteinemie 35
C18.452.648.398.641 lipidózy 35