familiární kombinovaná hyperlipidemie [Hyperlipidemia, Familial Combined]

tematický
68
Termíny

familiární kombinovaná hyperlipemie
hyperlipémie familiární kombinovaná
hyperlipidémie familiární kombinovaná

 

Familial Combined Hyperlipidemia
Hyperlipidemia, Multiple Lipoprotein-Type

Perzistentní odkaz   https://www.medvik.cz/link/D006950
Definice

Geneticky podmíněná, poměrně častá hyperlipoproteinemie se vzestupem jak triacylglycerolů (hypertriacylglycerolemie), tak cholesterolu (hypercholesterolemie) a lipoproteinů LDL a VLDL. Je provázena zvýšeným rizikem ICHS. (cit. Velký lékařský slovník online, 2016 http://lekarske.slovniky.cz)

A type of familial lipid metabolism disorder characterized by a variable pattern of elevated plasma CHOLESTEROL and/or TRIGLYCERIDES. Multiple genes on different chromosomes may be involved, such as the major late transcription factor (UPSTREAM STIMULATORY FACTORS) on CHROMOSOME 1.

DUI
D006950 MeSH Prohlížeč
CUI
M0010832
Historická pozn.
80; HYPERLIPOPROTEINEMIA was see HYPERLIPEMIA 1975-79; HYPERLIPEMIA, ESSENTIAL FAMILIAL was heading 1963-79 (see note under HYPERLIPIDEMIA for former cross refs to it)
Online pozn.
search HYPERLIPOPROTEINEMIA under HYPERLIPIDEMIA 1975-79; search HYPERLIPEMIA, ESSENTIAL FAMILIAL under HYPERLIPIDEMIA/genetics 1966-79
Veřejná pozn.
80; HYPERLIPOPROTEINEMIA was see HYPERLIPEMIA 1975-79; HYPERLIPEMIA, ESSENTIAL FAMILIAL was heading 1963-79 (see note under HYPERLIPIDEMIA for former cross refs to it)

C Nemoci
C16.320.565.398.224 Barthův syndrom 6
C16.320.565.398.465 hyperlipoproteinemie typ I 21
C16.320.565.398.481 hyperlipoproteinemie typ II 455
C16.320.565.398.483 hyperlipoproteinemie typ III 19
C16.320.565.398.487 hyperlipoproteinemie typ IV 14
C16.320.565.398.493 hyperlipoproteinemie typ V 6
C16.320.565.398.500 hypolipoproteinemie 35
C16.320.565.398.641 lipidózy 35
C18.452 metabolické nemoci 1 196
C18.452.584.500 dyslipidemie 1 634
C18.452.584.500.500 hyperlipidemie 1 238
C18.452.584.500.500.396 hypercholesterolemie 1 194
C18.452.584.500.500.644 hyperlipoproteinemie 771
C18.452.584.500.500.851 hypertriglyceridemie 395
C18.452.584.563.224 Barthův syndrom 6
C18.452.584.563.465 hyperlipoproteinemie typ I 21
C18.452.584.563.481 hyperlipoproteinemie typ II 455
C18.452.584.563.483 hyperlipoproteinemie typ III 19
C18.452.584.563.487 hyperlipoproteinemie typ IV 14
C18.452.584.563.493 hyperlipoproteinemie typ V 6
C18.452.584.563.500 hypolipoproteinemie 35
C18.452.584.563.641 lipidózy 35
C18.452.584.563.824 Shwachmanův-Diamondův syndrom 2
C18.452.648.398.224 Barthův syndrom 6
C18.452.648.398.465 hyperlipoproteinemie typ I 21
C18.452.648.398.481 hyperlipoproteinemie typ II 455
C18.452.648.398.483 hyperlipoproteinemie typ III 19
C18.452.648.398.487 hyperlipoproteinemie typ IV 14
C18.452.648.398.493 hyperlipoproteinemie typ V 6
C18.452.648.398.500 hypolipoproteinemie 35
C18.452.648.398.641 lipidózy 35