Hyperlipoproteinemia Type IV [hyperlipoproteinemie typ IV]

topical
14
Terms

familiární hyperlipoproteinemie typ IV
familiární hypertriacylglycerolemie
familiární hypertriglyceridemie
FHTG
hyperlipoproteinémie typ IV
hyperprebetalipoproteinemie

 

Carbohydrate Inducible Hyperlipemia
Carbohydrate-Inducible Hyperlipemia
Familial Hyperlipoproteinemia Type 4
Familial Type IV Hyperlipoproteinemia
Hyper prebeta lipoproteinemia
Hyperlipoproteinemia, Type IV
Hyperprebetalipoproteinemia
Hypertriglyceridemia, Familial

Persistent link   https://www.medvik.cz/link/D006953
Definition

A hypertriglyceridemia disorder, often with autosomal dominant inheritance. It is characterized by the persistent elevations of plasma TRIGLYCERIDES, endogenously synthesized and contained predominantly in VERY-LOW-DENSITY LIPOPROTEINS (pre-beta lipoproteins). In contrast, the plasma CHOLESTEROL and PHOSPHOLIPIDS usually remain within normal limits.

DUI
D006953 MeSH Browser
CUI
M0010835
Previous indexing
Hyperlipidemia (1966-1979)
History note
80
Public note
80

C Diseases
C16.320.565.398.224 Barth Syndrome 6
C16.320.565.398.465 Hyperlipoproteinemia Type I 21
C16.320.565.398.481 Hyperlipoproteinemia Type II 455
C16.320.565.398.483 Hyperlipoproteinemia Type III 19
C16.320.565.398.487 Hyperlipoproteinemia Type IV 14
C16.320.565.398.493 Hyperlipoproteinemia Type V 6
C16.320.565.398.500 Hypolipoproteinemias 35
C16.320.565.398.641 Lipidoses 35
C16.320.565.398.850 Smith-Lemli-Opitz Syndrome 30
C18.452 Metabolic Diseases 1 196
C18.452.584.500 Dyslipidemias 1 634
C18.452.584.500.500 Hyperlipidemias 1 238
C18.452.584.500.500.644 Hyperlipoproteinemias 771
C18.452.584.500.500.644.237 Hyperlipoproteinemia Type I 21
C18.452.584.500.500.644.475 Hyperlipoproteinemia Type II 455
C18.452.584.500.500.644.485 Hyperlipoproteinemia Type III 19
C18.452.584.500.500.644.490 Hyperlipoproteinemia Type IV 14
C18.452.584.500.500.644.495 Hyperlipoproteinemia Type V 6
C18.452.584.500.500.851 Hypertriglyceridemia 395
C18.452.584.500.500.851.500 Hyperlipoproteinemia Type IV 14
C18.452.584.500.500.851.750 Hyperlipoproteinemia Type V 6
C18.452.584.500.500.851.875 Hypertriglyceridemic Waist 5
C18.452.584.563.224 Barth Syndrome 6
C18.452.584.563.465 Hyperlipoproteinemia Type I 21
C18.452.584.563.481 Hyperlipoproteinemia Type II 455
C18.452.584.563.483 Hyperlipoproteinemia Type III 19
C18.452.584.563.487 Hyperlipoproteinemia Type IV 14
C18.452.584.563.493 Hyperlipoproteinemia Type V 6
C18.452.584.563.500 Hypolipoproteinemias 35
C18.452.584.563.641 Lipidoses 35
C18.452.584.563.798 Lipodystrophy, Familial Partial 1
C18.452.584.563.824 Shwachman-Diamond Syndrome 2
C18.452.584.563.850 Smith-Lemli-Opitz Syndrome 30
C18.452.648.398.224 Barth Syndrome 6
C18.452.648.398.465 Hyperlipoproteinemia Type I 21
C18.452.648.398.481 Hyperlipoproteinemia Type II 455
C18.452.648.398.483 Hyperlipoproteinemia Type III 19
C18.452.648.398.487 Hyperlipoproteinemia Type IV 14
C18.452.648.398.493 Hyperlipoproteinemia Type V 6
C18.452.648.398.500 Hypolipoproteinemias 35
C18.452.648.398.641 Lipidoses 35
C18.452.648.398.850 Smith-Lemli-Opitz Syndrome 30