hyperlipoproteinemie typ V [Hyperlipoproteinemia Type V]

tematický
6
Termíny

familiární hyperchylomikronemie s hyperprebetalipoproteinemií
hyperlipidemie typ V
hyperlipidemie typu V
hyperlipoproteinémie typ V
hyperlipoproteinemie typu V
smíšená hyperlipemie
smíšená hyperlipidemie

 

Hyperchylomicronemia Late Onset
Hyperchylomicronemia With Hyperprebetalipoproteinemia, Familial
Hyperchylomicronemia, Late-Onset
Hyperlipemia, Combined Fat And Carbohydrate-Induced
Hyperlipemia, Mixed
Hyperlipidemia, Type V
Hyperlipoproteinemia Type 5
Hyperlipoproteinemia, Type V

Perzistentní odkaz   https://www.medvik.cz/link/D006954
Definice

Typ těžké hyperlipidemie, která může být vrozená. Je charakterizovaná zvýšenými koncentracemi chylomikronů a VLDL. V séru bývá hypercholesterolemie a zejm. výrazná triacylglycerolemie. Klinicky bývá xantomatóza, riziko pankreatitidy; riziko ICHS není zvýšeno. Často bývá přítomen diabetes mellitus 2. typu, obezita a steatóza jater. (cit. Velký lékařský slovník online, 2017 http://lekarske.slovniky.cz/)

A severe type of hyperlipidemia, sometimes familial, that is characterized by the elevation of both plasma CHYLOMICRONS and TRIGLYCERIDES contained in VERY-LOW-DENSITY LIPOPROTEINS. Type V hyperlipoproteinemia is often associated with DIABETES MELLITUS and is not caused by reduced LIPOPROTEIN LIPASE activity as in HYPERLIPOPROTEINEMIA TYPE I .

DUI
D006954 MeSH Prohlížeč
CUI
M0010836
Předchozí užití
Hyperlipidemia (1966-1979)
Historická pozn.
80
Veřejná pozn.
80

C Nemoci
C16.320.565.398.224 Barthův syndrom 6
C16.320.565.398.465 hyperlipoproteinemie typ I 21
C16.320.565.398.481 hyperlipoproteinemie typ II 456
C16.320.565.398.483 hyperlipoproteinemie typ III 19
C16.320.565.398.487 hyperlipoproteinemie typ IV 14
C16.320.565.398.493 hyperlipoproteinemie typ V 6
C16.320.565.398.500 hypolipoproteinemie 35
C16.320.565.398.641 lipidózy 35
C18.452 metabolické nemoci 1 200
C18.452.584.500 dyslipidemie 1 652
C18.452.584.500.500 hyperlipidemie 1 238
C18.452.584.500.500.644 hyperlipoproteinemie 771
C18.452.584.500.500.644.237 hyperlipoproteinemie typ I 21
C18.452.584.500.500.644.475 hyperlipoproteinemie typ II 456
C18.452.584.500.500.644.485 hyperlipoproteinemie typ III 19
C18.452.584.500.500.644.490 hyperlipoproteinemie typ IV 14
C18.452.584.500.500.644.495 hyperlipoproteinemie typ V 6
C18.452.584.500.500.851 hypertriglyceridemie 397
C18.452.584.500.500.851.500 hyperlipoproteinemie typ IV 14
C18.452.584.500.500.851.750 hyperlipoproteinemie typ V 6
C18.452.584.500.500.851.875 hypertriglyceridemický pas 5
C18.452.584.563.224 Barthův syndrom 6
C18.452.584.563.465 hyperlipoproteinemie typ I 21
C18.452.584.563.481 hyperlipoproteinemie typ II 456
C18.452.584.563.483 hyperlipoproteinemie typ III 19
C18.452.584.563.487 hyperlipoproteinemie typ IV 14
C18.452.584.563.493 hyperlipoproteinemie typ V 6
C18.452.584.563.500 hypolipoproteinemie 35
C18.452.584.563.641 lipidózy 35
C18.452.584.563.824 Shwachmanův-Diamondův syndrom 2
C18.452.648.398.224 Barthův syndrom 6
C18.452.648.398.465 hyperlipoproteinemie typ I 21
C18.452.648.398.481 hyperlipoproteinemie typ II 456
C18.452.648.398.483 hyperlipoproteinemie typ III 19
C18.452.648.398.487 hyperlipoproteinemie typ IV 14
C18.452.648.398.493 hyperlipoproteinemie typ V 6
C18.452.648.398.500 hypolipoproteinemie 35
C18.452.648.398.641 lipidózy 35