Platelet Storage Pool Deficiency [porucha skladovací funkce trombocytů]

topical
1
Terms

dědičná porucha skladovací funkce trombocytů
porucha skladovacích granul
porucha skladovacích granulí
porucha skladovacího poolu
trombocyty - deficit ukládacího poolu
získaná porucha skladovací funkce trombocytů

 

Acquired Storage Pool Disease
Deficiency, Platelet Storage Pool
Deficiency, Storage Pool
Familial Platelet Storage Pool Disease
Platelet Storage Pool Deficiencies
Platelet Storage Pool Disease
Storage Pool Deficiency
Storage Pool Deficiency, Platelet
Storage Pool Platelet Disease

Persistent link   https://www.medvik.cz/link/D010981
Definition

Disorder characterized by a decrease or lack of platelet dense bodies in which the releasable pool of adenine nucleotides and 5HT are normally stored.

DUI
D010981 MeSH Browser
CUI
M0017023
Previous indexing
Blood Platelet Disorders (1967-1985)
History note
91(86); was see under BLOOD PLATELET DISORDERS 1986-90
Public note
91; was see under BLOOD PLATELET DISORDERS 1986-90

C Diseases
C15.378.100.452 Ecchymosis 10
C15.378.100.685.400 Hermanski-Pudlak Syndrome 7
C15.378.100.800 Protein S Deficiency 18
C15.378.100.802 Purpura 109
C15.378.100.832 Thrombocythemia, Essential 94
C15.378.100.876 Thromboinflammation 3
C15.378.100.920 Vitamin K Deficiency 42
C15.378.140.120 Bernard-Soulier Syndrome 9
C15.378.140.427 Gray Platelet Syndrome 1
C15.378.140.735.400 Hermanski-Pudlak Syndrome 7
C15.378.140.810 Thrombasthenia 7
C15.378.140.855 Thrombocytopenia 603
C15.378.140.860 Thrombocytosis 61
C15.378.140.900 von Willebrand Diseases 103
C15.378.463.067 Afibrinogenemia 39
C15.378.463.080 Bernard-Soulier Syndrome 9
C15.378.463.300 Factor V Deficiency 7
C15.378.463.310 Factor VII Deficiency 6
C15.378.463.320 Factor X Deficiency 2
C15.378.463.325 Factor XI Deficiency 12
C15.378.463.330 Factor XII Deficiency 8
C15.378.463.335 Factor XIII Deficiency 4
C15.378.463.500 Hemophilia A 691
C15.378.463.510 Hemophilia B 216
C15.378.463.515 Hemostatic Disorders 49
C15.378.463.550 Hypoprothrombinemias 4
C15.378.463.735.400 Hermanski-Pudlak Syndrome 7
C15.378.463.810 Thrombasthenia 7
C15.378.463.825 Thrombocythemia, Essential 94
C15.378.463.841 Vitamin K Deficiency 42
C15.378.463.920 von Willebrand Diseases 103
C15.378.463.960 Wiskott-Aldrich Syndrome 20

Platelet Alpha-Delta Storage Pool Deficiency Disease MeSH Browser