Piebaldism [piebaldismus]

topical
1
Terms

albinismus kůže
částečný albinismus
parciální albinismus
parciální albinizmus
parciální piebaldismus

 

Albinism, Cutaneous
Albinism, Partial
Piebald Trait

Persistent link   https://www.medvik.cz/link/D016116
Definition

Autosomal dominant, congenital disorder characterized by localized hypomelanosis of the skin and hair. The most familiar feature is a white forelock presenting in 80 to 90 percent of the patients. The underlying defect is possibly related to the differentiation and migration of melanoblasts, as well as to defective development of the neural crest (neurocristopathy). Piebaldism may be closely related to WAARDENBURG SYNDROME.

DUI
D016116 MeSH Browser
CUI
M0024621
Previous indexing
Albinism (1966-1971); Pigmentation Disorders (1966-1990)
History note
91
Public note
91

C Diseases
C16.320.290.040 Albinism 17
C16.320.290.040.090 Albinism, Ocular 4
C16.320.290.040.100 Albinism, Oculocutaneous 7
C16.320.290.040.600 Piebaldism 1
C16.320.565.100.102 Albinism 17
C16.320.565.100.102.090 Albinism, Ocular 4
C16.320.565.100.102.100 Albinism, Oculocutaneous 7
C16.320.565.100.102.600 Piebaldism 1
C16.320.850.080 Albinism 17
C16.320.850.080.090 Albinism, Ocular 4
C16.320.850.080.100 Albinism, Oculocutaneous 7
C16.320.850.080.600 Piebaldism 1
C17.800 Skin Diseases 2 799
C17.800.621 Pigmentation Disorders 132
C17.800.621.440 Hypopigmentation 14
C17.800.621.440.102 Albinism 17
C17.800.621.440.102.090 Albinism, Ocular 4
C17.800.621.440.102.100 Albinism, Oculocutaneous 7
C17.800.621.440.102.600 Piebaldism 1
C17.800.827.080 Albinism 17
C17.800.827.080.090 Albinism, Ocular 4
C17.800.827.080.100 Albinism, Oculocutaneous 7
C17.800.827.080.600 Piebaldism 1
C18.452 Metabolic Diseases 1 196
C18.452.648.100.102 Albinism 17
C18.452.648.100.102.090 Albinism, Ocular 4
C18.452.648.100.102.100 Albinism, Oculocutaneous 7
C18.452.648.100.102.600 Piebaldism 1

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