Albinism, Ocular [albinismus oční]

topical
4
Terms

albinismus očí
albinismus okulární
oční albinismus
okulární albinismus

 

Ocular Albinism

Persistent link   https://www.medvik.cz/link/D016117
Definition

Albinism affecting the eye in which pigment of the hair and skin is normal or only slightly diluted. The classic type is X-linked (Nettleship-Falls), but an autosomal recessive form also exists. Ocular abnormalities may include reduced pigmentation of the iris, nystagmus, photophobia, strabismus, and decreased visual acuity.

Annotation
hypopigmentation of eye; do not use /congen & do not coord with INFANT, NEWBORN, DISEASES
DUI
D016117 MeSH Browser
CUI
M0024622
Previous indexing
Albinism (1966-1990)
History note
91
Public note
91

C Diseases
C11 Eye Diseases 1 489
C11.270.040 Albinism 17
C11.270.040.090 Albinism, Ocular 4
C11.270.040.545 Albinism, Oculocutaneous 7
C11.270.040.772 Chediak-Higashi Syndrome 4
C16.320.290.040 Albinism 17
C16.320.290.040.090 Albinism, Ocular 4
C16.320.290.040.100 Albinism, Oculocutaneous 7
C16.320.290.040.600 Piebaldism 1
C16.320.565.100.102 Albinism 17
C16.320.565.100.102.090 Albinism, Ocular 4
C16.320.565.100.102.100 Albinism, Oculocutaneous 7
C16.320.565.100.102.600 Piebaldism 1
C16.320.850.080 Albinism 17
C16.320.850.080.090 Albinism, Ocular 4
C16.320.850.080.100 Albinism, Oculocutaneous 7
C16.320.850.080.600 Piebaldism 1
C17.800 Skin Diseases 2 799
C17.800.621 Pigmentation Disorders 132
C17.800.621.440 Hypopigmentation 14
C17.800.621.440.102 Albinism 17
C17.800.621.440.102.090 Albinism, Ocular 4
C17.800.621.440.102.100 Albinism, Oculocutaneous 7
C17.800.621.440.102.600 Piebaldism 1
C17.800.827.080 Albinism 17
C17.800.827.080.090 Albinism, Ocular 4
C17.800.827.080.100 Albinism, Oculocutaneous 7
C17.800.827.080.600 Piebaldism 1
C18.452 Metabolic Diseases 1 196
C18.452.648.100.102 Albinism 17
C18.452.648.100.102.090 Albinism, Ocular 4
C18.452.648.100.102.100 Albinism, Oculocutaneous 7
C18.452.648.100.102.600 Piebaldism 1

Aland Island Eye Disease Disease MeSH Browser

Albinism ocular late onset sensorineural deafness Disease MeSH Browser

Albinism, minimal pigment type Disease MeSH Browser

Ocular Albinism type 1 Disease MeSH Browser