Leukocyte-Adhesion Deficiency Syndrome [LAD syndrom]

topical
3
Terms

deficience adhezivity leukocytů
syndrom defektní adhezivity leukocytů
syndrom deficience leukocytové adheze
syndrom LAD

 

Deficiency Syndrome, Leukocyte-Adhesion

Persistent link   https://www.medvik.cz/link/D018370
Definition

Rare, autosomal recessive disorder caused by deficiency of the beta 2 integrin receptors (RECEPTORS, LEUKOCYTE-ADHESION) comprising the CD11/CD18 family of glycoproteins. The syndrome is characterized by abnormal adhesion-dependent functions, especially defective tissue emigration of neutrophils, leading to recurrent infection.

DUI
D018370 MeSH Browser
CUI
M0027596
Previous indexing
Immunologic Deficiency Syndromes (1988-1994); Receptors, Leukocyte-Adhesion/deficiency (1988-1990)
History note
95
Public note
95

Leukocyte Adhesion Deficiency, Type III Disease MeSH Browser

Leukocyte adhesion deficiency type 1 Disease MeSH Browser