Job Syndrome [Jobův syndrom]

topical
15
Terms

hyper-IgE syndrom
hyper-IgE syndrom, autozomálně-dominantní
hyper-IgE syndrom, autozomálně-recesivní

 

Buckley Syndrome
HIE Syndrome
HIES, Autosomal Dominant
HIES, Autosomal Recessive
Hyper-IgE Recurrent Infection Syndrome, Autosomal Recessive
Hyper-IgE Syndrome
Hyper-IgE Syndrome, Autosomal Dominant
Hyper-IgE Syndrome, Autosomal Recessive
Hyper-Immunoglobulin E Syndrome, Autosomal Dominant
Hyper-Immunoglobulin E Syndrome, Autosomal Recessive
Hyperimmunoglobulin E-Recurrent Infection Syndrome
Hyperimmunoglobulin E, Recurrent Infection Syndrome
Hyperimmunoglobulinemia E Syndrome
Job-Buckley Syndrome
Job's Syndrome

Persistent link   https://www.medvik.cz/link/D007589
Definition

Primary immunodeficiency syndrome characterized by recurrent infections and hyperimmunoglobulinemia E. Most cases are sporadic. Of the rare familial forms, the dominantly inherited subtype has additional connective tissue, dental and skeletal involvement that the recessive type does not share.

DUI
D007589 MeSH Browser
CUI
M0011856
History note
2014 (1975);use PHAGOCYTE BACTERICIDAL DYSFUNCTION 1975-1990
Public note
2014; see JOB'S SYNDROME 1991-2013; see PHAGOCYTE BACTERICIDAL DYSFUNCTION 1975-1990

C Diseases
C15.378.553 Leukocyte Disorders 18
C15.378.553.774.257 Chediak-Higashi Syndrome 4
C15.378.553.774.535 Granulomatous Disease, Chronic 54
C15.378.553.774.600 Job Syndrome 15
C16.320.798.250 Ataxia Telangiectasia 47
C16.320.798.313 Bloom Syndrome 11
C16.320.798.375 Chediak-Higashi Syndrome 4
C16.320.798.688 Job Syndrome 15
C16.320.798.875 Wiskott-Aldrich Syndrome 20
C20.673.774.257 Chediak-Higashi Syndrome 4
C20.673.774.600 Job Syndrome 15
C20.673.795.250 Ataxia Telangiectasia 47
C20.673.795.313 Bloom Syndrome 11
C20.673.795.375 Chediak-Higashi Syndrome 4
C20.673.795.688 Job Syndrome 15
C20.673.795.875 Wiskott-Aldrich Syndrome 20

Hyper-Ige Recurrent Infection Syndrome, Autosomal Dominant Disease MeSH Browser

Tyrosine Kinase 2 Deficiency Disease MeSH Browser