Mitochondrial Diseases [mitochondriální nemoci]

topical
160
Terms

deficit mitochondriálního elektronového transportního řetězce
mitochondriální dýchací řetězec - deficience
mitochondriopatie
oxidační fosforylace - deficience
poruchy mitochondriálního dýchacího řetězce
poruchy mitochondriálního elektronového transportního řetězce
poruchy oxidační fosforylace

 

Electron Transport Chain Deficiencies, Mitochondrial
Mitochondria Dysfunction
Mitochondrial Defect
Mitochondrial Disorders
Mitochondrial Dysfunction
Mitochondrial Electron Transport Chain Deficiencies
Mitochondrial Respiratory Chain Deficiencies
Oxidative Phosphorylation Deficiencies
Respiratory Chain Deficiencies, Mitochondrial

Persistent link   https://www.medvik.cz/link/D028361
Definition

Diseases caused by abnormal function of the MITOCHONDRIA. They may be caused by mutations, acquired or inherited, in mitochondrial DNA or in nuclear genes that code for mitochondrial components. They may also be the result of acquired mitochondria dysfunction due to adverse effects of drugs, infections, or other environmental causes.

Annotation
general or unspecified; prefer specifics
DUI
D028361 MeSH Browser
CUI
M0335637
Previous indexing
Mitochondria (1987-2001); Mitochondrial Myopathies (1992-2001)
History note
2002; use MITOCHONDRIAL MYOPATHIES 2000-2001
Public note
2002; see MITOCHONDRIAL MYOPATHIES 2000-2001

C Diseases
C01 Infections 2 027
C04 Neoplasms 12 832
C11 Eye Diseases 1 495
C18.452 Metabolic Diseases 1 200
C18.452.076 Acid-Base Imbalance 288
C18.452.479 Hyperlactatemia 5
C18.452.625 Metabolic Syndrome 2 001
C18.452.660 Mitochondrial Diseases 160
C18.452.660.300 Friedreich Ataxia 54
C18.452.660.520 Leigh Disease 26
C18.452.660.560 Mitochondrial Myopathies 40
C18.452.811 Porphyrias 252
C18.452.915 Wasting Syndrome 13

3-Hydroxy-3-Methylglutaryl-CoA Synthase 2 Deficiency Disease MeSH Browser

Acyl-CoA Dehydrogenase Family, Member 9, Deficiency of Disease MeSH Browser

Ataxia Neuropathy Spectrum Disease MeSH Browser

Ataxia and Polyneuropathy, Adult-Onset Disease MeSH Browser

Carnitine Palmitoyltransferase II Deficiency, Late-Onset Disease MeSH Browser

Carnitine Palmitoyltransferase II Deficiency, Lethal Neonatal Disease MeSH Browser

Childhood Myocerebrohepatopathy Spectrum Disease MeSH Browser

Coenzyme Q10 Deficiency Disease MeSH Browser

Combined Oxidative Phosphorylation Deficiency 4 Disease MeSH Browser

Combined Oxidative Phosphorylation Deficiency 5 Disease MeSH Browser

Cowden-Like Syndrome Disease MeSH Browser

Deoxyguanosine Kinase Deficiency Disease MeSH Browser

Hypermetabolism due to Defect in Mitochondria Disease MeSH Browser

Hypomyelination, Global Cerebral Disease MeSH Browser

Hypotonia-Cystinuria Syndrome Disease MeSH Browser

Leukodystrophy, Hypomyelinating, 4 Disease MeSH Browser

Leukoencephalopathy with Brainstem and Spinal Cord Involvement and Lactate Elevation Disease MeSH Browser

Medium Chain 3-Ketoacyl-CoA Thiolase Deficiency Disease MeSH Browser

Mitochondrial Complex II Deficiency Disease MeSH Browser

Mitochondrial Complex III Deficiency Disease MeSH Browser

Mitochondrial DNA Depletion Syndrome, Myopathic Form Disease MeSH Browser

Mitochondrial Phosphate Carrier Deficiency Disease MeSH Browser

Mitochondrial complex I deficiency Disease MeSH Browser

Multiple Mitochondrial Dysfunctions Syndrome Disease MeSH Browser

Myopathy with Giant Abnormal Mitochondria Disease MeSH Browser

Myopathy, Cataract, Hypogonadism Syndrome Disease MeSH Browser

Navajo neurohepatopathy Disease MeSH Browser

Noninsulin-dependent diabetes mellitus with deafness Disease MeSH Browser

Ophthalmoplegic Neuromuscular Disorder with Abnormal Mitochondria Disease MeSH Browser

Parkinson Disease, Mitochondrial Disease MeSH Browser

Phosphoenolpyruvate Carboxykinase Deficiency, Mitochondrial Disease MeSH Browser

Progressive External Ophthalmoplegia With Hypogonadism Disease MeSH Browser

Progressive External Ophthalmoplegia With Mitochondrial Dna Deletions, Autosomal Dominant, 5 Disease MeSH Browser

Progressive External Ophthalmoplegia with Mitochondrial DNA Deletions, Autosomal Dominant, 1 Disease MeSH Browser

Proximal Myopathy with Focal Depletion of Mitochondria Disease MeSH Browser

Sarcosinemia Disease MeSH Browser

Spinocerebellar Ataxia with Epilepsy Disease MeSH Browser

Succinate-Coa Ligase Deficiency Disease MeSH Browser

VDAC Deficiency Disease MeSH Browser

VLCAD deficiency Disease MeSH Browser

Wolfram Syndrome 2 Disease MeSH Browser