Muscular Dystrophies, Limb-Girdle [pletencové svalové dystrofie]

topical
22
Terms

LGMD
muskulární dystrofie s postižením svalstva končetinových pletenců
svalové dystrofie pletencové

 

Limb-Girdle Muscular Dystrophies
Limb-Girdle Muscular Dystrophy
Limb-Girdle Syndrome
Muscular Dystrophy, Limb-Girdle
Myopathic Limb-Girdle Syndrome

Persistent link   https://www.medvik.cz/link/D049288
Definition

A heterogenous group of inherited muscular dystrophy that can be autosomal dominant or autosomal recessive. There are many forms (called LGMDs) involving genes encoding muscle membrane proteins such as the sarcoglycan (SARCOGLYCANS) complex that interacts with DYSTROPHIN. The disease is characterized by progressing wasting and weakness of the proximal muscles of arms and legs around the HIPS and SHOULDERS (the pelvic and shoulder girdles).

DUI
D049288 MeSH Browser
CUI
M0335588
Previous indexing
Muscular Dystrophies (1966-2004)
History note
2005; use MUSCULAR DYSTROPHIES 2000-2004
Public note
2005; see MUSCULAR DYSTROPHIES 2000-2004

C Diseases
C05.651.534.500 Muscular Dystrophies 141
C05.651.534.500.074 Distal Myopathies 3
C05.651.534.500.280.500 Sarcoglycanopathies 2
C05.651.534.500.300 Muscular Dystrophy, Duchenne 136
C05.651.534.500.500 Myotonic Dystrophy 96
C10.668.491 Muscular Diseases 557
C10.668.491.175.500 Muscular Dystrophies 141
C10.668.491.175.500.074 Distal Myopathies 3
C10.668.491.175.500.112 Glycogen Storage Disease Type VII
C10.668.491.175.500.149 Muscular Dystrophies, Limb-Girdle 22
C10.668.491.175.500.149.500 Sarcoglycanopathies 2
C10.668.491.175.500.300 Muscular Dystrophy, Duchenne 136
C10.668.491.175.500.350 Muscular Dystrophy, Emery-Dreifuss 18
C10.668.491.175.500.450 Muscular Dystrophy, Oculopharyngeal 3
C10.668.491.175.500.500 Myotonic Dystrophy 96
C16.320.577 Muscular Dystrophies 141
C16.320.577.074 Distal Myopathies 3
C16.320.577.280.500 Sarcoglycanopathies 2
C16.320.577.300 Muscular Dystrophy, Duchenne 136
C16.320.577.500 Myotonic Dystrophy 96
C16.320.577.750 Walker-Warburg Syndrome 4

Beta-sarcoglycanopathy Disease MeSH Browser

Dysferlinopathy Disease MeSH Browser

Epidermolysa bullosa simplex and limb girdle muscular dystrophy Disease MeSH Browser

Inclusion Body Myopathy With Early-Onset Paget Disease And Frontotemporal Dementia Disease MeSH Browser

Limb-Girdle Muscular Dystrophy, Type 1G Disease MeSH Browser

Limb-girdle muscular dystrophy autosomal recessive Disease MeSH Browser

Limb-girdle muscular dystrophy type 2A Disease MeSH Browser

Limb-girdle muscular dystrophy type 2H Disease MeSH Browser

Limb-girdle muscular dystrophy, type 1B Disease MeSH Browser

Limb-girdle muscular dystrophy, type 2B Disease MeSH Browser

Muscular Dystrophy, Hemizygous Lethal Type Disease MeSH Browser

Muscular Dystrophy, Limb-Girdle, Type 1C Disease MeSH Browser

Muscular Dystrophy, Limb-Girdle, Type 1D Disease MeSH Browser

Muscular Dystrophy, Limb-Girdle, Type 1E Disease MeSH Browser

Muscular Dystrophy, Limb-Girdle, Type 1F Disease MeSH Browser

Muscular Dystrophy, Limb-Girdle, Type 2G Disease MeSH Browser

Muscular Dystrophy, Limb-Girdle, Type 2I Disease MeSH Browser

Muscular Dystrophy, Limb-Girdle, Type 2J Disease MeSH Browser

Muscular Dystrophy, Limb-Girdle, Type 2L Disease MeSH Browser

Muscular Dystrophy, Limb-Girdle, Type 2M Disease MeSH Browser

Muscular dystrophy, limb-girdle, type 1A Disease MeSH Browser

Myopathy, limb-girdle, with bone fragility Disease MeSH Browser