Stargardt Disease [Stargardtova nemoc]

topical
6
Terms

fundus flavimaculatus
juvenilní makulární degenerace
makulární degenerace juvenilní
makulární dystrofie se skvrnami, typ 1
Stargardtova choroba
Stargardtova makulární degenerace
Stargardtova nemoc 1

 

Fundus Flavimaculatus
Juvenile Macular Degeneration
Macular Degeneration, Juvenile
Macular Dystrophy With Flecks, Type 1
Stargardt Disease 1
Stargardt Macular Degeneration

Definition

A juvenile-onset macular dystrophy characterized by progressive loss of VISUAL ACUITY with normal acuity in peripheral VISUAL FIELDS. Other associated clinical features may include LIPOFUSCIN fundus autofluorescence, atrophy of the RETINAL PIGMENT EPITHELIUM, loss of color vision, PHOTOPHOBIA and PARACENTRAL SCOTOMA. Germline mutations in the ABCA4 gene have been identified in recessive and dominant diseases.

DUI
D000080362 MeSH Browser
CUI
M000612272
History note
2020(2010)
Public note
2020; STARGARDT DISEASE was indexed under MACULAR DEGENERATION 2010-2019

C Diseases
C11 Eye Diseases 1 489
C11.270.019 Aicardi Syndrome
C11.270.040 Albinism 17
C11.270.060 Aniridia 18
C11.270.142 Choroideremia 3
C11.270.147 Coloboma 14
C11.270.151 Cone Dystrophy
C11.270.468 Gyrate Atrophy 1
C11.270.612 Retinal Degeneration 75
C11.270.660 Retinal Dysplasia 4
C11.270.684 Retinitis Pigmentosa 55
C11.270.862 Retinoblastoma 159
C11.270.872 Stargardt Disease 6
C11.768 Retinal Diseases 402
C11.768.585 Retinal Degeneration 75
C11.768.585.439 Macular Degeneration 469
C11.768.585.439.122 Geographic Atrophy 10
C11.768.585.439.245 Macular Edema 207
C11.768.585.439.339 Stargardt Disease 6
C11.768.585.439.433 Vitelliform Macular Dystrophy 5
C11.768.585.439.622 Wet Macular Degeneration 43
C16.320.290.019 Aicardi Syndrome
C16.320.290.040 Albinism 17
C16.320.290.078 Aniridia 18
C16.320.290.142 Choroideremia 3
C16.320.290.152 Cone-Rod Dystrophies
C16.320.290.235 Duane Retraction Syndrome 9
C16.320.290.410 Graves Ophthalmopathy 57
C16.320.290.468 Gyrate Atrophy 1
C16.320.290.612 Optic Nerve Hypoplasia 1
C16.320.290.660 Retinal Dysplasia 4
C16.320.290.684 Retinitis Pigmentosa 55
C16.320.290.724 Stargardt Disease 6
C16.320.290.842 Weill-Marchesani Syndrome 1