Steroid 17-alpha-Hydroxylase [steroid-17-alfa-hydroxylasa]

topical
21
Terms

17-alfa-hydroxylasa
17-alfa-hydroxyláza
17-alfa-hydroxyprogesteronaldolasa
17-alfa-hydroxyprogesteronaldoláza
17,20-desmolasa
17,20-desmoláza
17,20-lyasa
17,20-lyáza
CYP17
cytochrom P-450(17 alfa)
P450(c17)
steroid-17-alfa-hydroxyláza
steroid-17-alfa-monooxygenasa

 

17 alpha-Hydroxylase
17 alpha-Hydroxylase Cytochrome P-450
17 alpha-Hydroxyprogesterone Aldolase
17,20-Desmolase
17,20-Lyase
CYP17
Cytochrome P-450(17 alpha)
Cytochrome P-450(17-alpha)
Cytochrome P450(17 alpha)
Hydroxyprogesterone Aldolase
P450(c17)
Steroid 17 alpha-Hydroxylase
Steroid 17 alpha-Monooxygenase
Steroid 17-Hydroxylase
Steroid 17-Monooxygenase
Steroid-17-Hydroxylase

Persistent link   https://www.medvik.cz/link/D013254
Definition

A microsomal cytochrome P450 enzyme that catalyzes the 17-alpha-hydroxylation of progesterone or pregnenolone and subsequent cleavage of the residual two carbons at C17 in the presence of molecular oxygen and NADPH-FERRIHEMOPROTEIN REDUCTASE. This enzyme, encoded by CYP17 gene, generates precursors for glucocorticoid, androgen, and estrogen synthesis. Defects in CYP17 gene cause congenital adrenal hyperplasia (ADRENAL HYPERPLASIA, CONGENITAL) and abnormal sexual differentiation.

DUI
D013254 MeSH Browser
CUI
M0020523
CAS
Steroid, hydrogen-donor:oxygen oxidoreductase (17 alpha-hydroxylating)
Previous indexing
Steroid Hydroxylases (1973-1977)
History note
2003 (1978)
Public note
2003; see STEROID 17 ALPHA-MONOOXYGENASE 1997-2002, see STEROID 17-HYDROXYLASE 1991-1996, see STEROID HYDROXYLASES 1990; for STEROID-17-HYDROXYLASE see STEROID HYDROXYLASES 1978-1989; for 17,20-LYASE see 17 ALPHA-HYDROXYPROGESTERONE ALDOLASE 1996-1997

D Chemicals and Drugs
D08.244 Cytochromes 121
D08.244.453.487.500 Steroid 17-alpha-Hydroxylase 21
D08.244.453.915 Steroid Hydroxylases 16
D08.244.453.915.025 Cholesterol 24-Hydroxylase
D08.244.453.915.050 Cytochrome P-450 CYP11B2 11
D08.244.453.915.099 Aromatase 72
D08.244.453.915.200 Cholesterol 7-alpha-Hydroxylase 19
D08.244.453.915.730 Steroid 12-alpha-Hydroxylase 1
D08.244.453.915.737 Steroid 16-alpha-Hydroxylase 5
D08.244.453.915.748 Steroid 17-alpha-Hydroxylase 21
D08.244.453.915.750 Steroid 11-beta-Hydroxylase 3
D08.244.453.915.760 Steroid 21-Hydroxylase 63
D08.244.453.915.880 Sterol 14-Demethylase 2
D08.811 Enzymes 1 547
D08.811.682 Oxidoreductases 446
D08.811.682.690 Oxygenases 76
D08.811.682.690.708 Mixed Function Oxygenases 68
D08.811.682.690.708.170 Cytochrome P-450 Enzyme System 692
D08.811.682.690.708.170.444 Cytochrome P450 Family 17
D08.811.682.690.708.170.444.500 Steroid 17-alpha-Hydroxylase 21
D08.811.682.690.708.170.915 Steroid Hydroxylases 16
D08.811.682.690.708.170.915.025 Cholesterol 24-Hydroxylase
D08.811.682.690.708.170.915.050 Cytochrome P-450 CYP11B2 11
D08.811.682.690.708.170.915.099 Aromatase 72
D08.811.682.690.708.170.915.150 Cholestanetriol 26-Monooxygenase 4
D08.811.682.690.708.170.915.200 Cholesterol 7-alpha-Hydroxylase 19
D08.811.682.690.708.170.915.212 Cholesterol Side-Chain Cleavage Enzyme 6
D08.811.682.690.708.170.915.400 25-Hydroxyvitamin D3 1-alpha-Hydroxylase 3
D08.811.682.690.708.170.915.730 Steroid 12-alpha-Hydroxylase 1
D08.811.682.690.708.170.915.737 Steroid 16-alpha-Hydroxylase 5
D08.811.682.690.708.170.915.748 Steroid 17-alpha-Hydroxylase 21
D08.811.682.690.708.170.915.750 Steroid 11-beta-Hydroxylase 3
D08.811.682.690.708.170.915.760 Steroid 21-Hydroxylase 63
D08.811.682.690.708.170.915.880 Sterol 14-Demethylase 2
D12.776 Proteins 2 577
D12.776.422 Hemeproteins 16
D12.776.422.220 Cytochromes 121
D12.776.422.220.453 Cytochrome P-450 Enzyme System 692
D12.776.422.220.453.487 Cytochrome P450 Family 17
D12.776.422.220.453.487.500 Steroid 17-alpha-Hydroxylase 21
D12.776.422.220.453.915 Steroid Hydroxylases 16
D12.776.422.220.453.915.025 Cholesterol 24-Hydroxylase
D12.776.422.220.453.915.050 Cytochrome P-450 CYP11B2 11
D12.776.422.220.453.915.099 Aromatase 72
D12.776.422.220.453.915.150 Cholestanetriol 26-Monooxygenase 4
D12.776.422.220.453.915.200 Cholesterol 7-alpha-Hydroxylase 19
D12.776.422.220.453.915.212 Cholesterol Side-Chain Cleavage Enzyme 6
D12.776.422.220.453.915.400 25-Hydroxyvitamin D3 1-alpha-Hydroxylase 3
D12.776.422.220.453.915.730 Steroid 12-alpha-Hydroxylase 1
D12.776.422.220.453.915.737 Steroid 16-alpha-Hydroxylase 5
D12.776.422.220.453.915.748 Steroid 17-alpha-Hydroxylase 21
D12.776.422.220.453.915.750 Steroid 11-beta-Hydroxylase 3
D12.776.422.220.453.915.760 Steroid 21-Hydroxylase 63
D12.776.422.220.453.915.880 Sterol 14-Demethylase 2

CYP17A1 protein, human Chemical MeSH Browser

CYP17A1 protein, rat Chemical MeSH Browser

Cyp17a1 protein, mouse Chemical MeSH Browser

cyp17a1 protein, zebrafish Chemical MeSH Browser

cyp17a2 protein, zebrafish Chemical MeSH Browser

pregnenolone 17-alpha-hydroxylase Chemical MeSH Browser

progesterone 17-alpha-hydroxylase Chemical MeSH Browser