Chondrodysplasia Punctata [chondrodysplasia punctata]

topical
6
Terms

chondrodysplasia punctata Conradiho-Hünermannova
Conradi-Hünermannova nemoc
Conradiho nemoc

 

Chondrodysplasia Punctata 2, X-Linked
Chondrodysplasia Punctata 2, X-Linked Dominant
Chondrodystrophia Calcificans Congenita
Conradi Hunermann Happle Syndrome
Conradi-Hunermann Syndrome
Conradi-Hünermann Syndrome
Conradi-Hunermann-Happle Syndrome
Conradi-Hünermann-Happle Syndrome
Dysplasia Epiphysialis Punctata
Epiphyses, Stippled
Happle Syndrome
Hunermann-Conradi Syndrome
Stippled Epiphyses
X-Linked Chondrodysplasia Punctata 2
X-Linked Dominant Chondrodysplasia Punctata

Persistent link   https://www.medvik.cz/link/D002806
Definition

A heterogeneous group of bone dysplasias, the common character of which is stippling of the epiphyses in infancy. The group includes a severe autosomal recessive form (CHONDRODYSPLASIA PUNCTATA, RHIZOMELIC), an autosomal dominant form (Conradi-Hunermann syndrome), and a milder X-linked form. Metabolic defects associated with impaired peroxisomes are present only in the rhizomelic form.

Annotation
spell entry term name Hunermann with an umlaut in titles & translations; CHONDRODYSPLASIA PUNCTATA, RHIZOMELIC is also available
DUI
D002806 MeSH Browser
CUI
M0004308
History note
1985(1964)
Public note
1985; see CHONDRODYSTROPHIA CALCIFICANS CONGENITA 1967-1984

C Diseases
C01 Infections 2 027
C04 Neoplasms 12 832
C05.116 Bone Diseases 796
C05.116.099.708 Osteochondrodysplasias 125
C05.116.099.708.017 Achondroplasia 71
C05.116.099.708.025 Acquired Hyperostosis Syndrome 21
C05.116.099.708.180 Camurati-Engelmann Syndrome 6
C05.116.099.708.195 Chondrodysplasia Punctata 6
C05.116.099.708.207 Cleidocranial Dysplasia 7
C05.116.099.708.327 Ellis-Van Creveld Syndrome 11
C05.116.099.708.338 Enchondromatosis 13
C05.116.099.708.375 Fibrous Dysplasia of Bone 47
C05.116.099.708.486 Hyperostosis Frontalis Interna 3
C05.116.099.708.534 Kashin-Beck Disease
C05.116.099.708.582 Langer-Giedion Syndrome 7
C05.116.099.708.670 Osteochondroma 16
C05.116.099.708.685 Osteogenesis Imperfecta 106
C05.116.099.708.702 Osteosclerosis 38
C05.116.099.708.779 Pycnodysostosis 2
C05.116.099.708.857 Short Rib-Polydactyly Syndrome 3
C11 Eye Diseases 1 495

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X-Linked Chondrodysplasia Punctata 1 Disease MeSH Browser