Wilms Tumor [Wilmsův nádor]

topical
112
Terms

adenomyosarkom ledviny
nefroblastom
oboustranný Wilmsův nádor
Wilmsův nádor oboustranný
Wilmsův tumor
Wilmsův tumor bilaterální

 

Bilateral Wilms Tumor
Nephroblastoma
Wilms Tumor 1
Wilms' Tumor

Persistent link   https://www.medvik.cz/link/D009396
Definition

A malignant kidney tumor, caused by the uncontrolled multiplication of renal stem (blastemal), stromal (STROMAL CELLS), and epithelial (EPITHELIAL CELLS) elements. However, not all three are present in every case. Several genes or chromosomal areas have been associated with Wilms tumor which is usually found in childhood as a firm lump in a child's side or ABDOMEN.

Annotation
coordinate IM with KIDNEY NEOPLASMS (IM); /genet: consider also GENES, WILMS TUMOR
DUI
D009396 MeSH Browser
CUI
M0014630
History note
2006 (1963)
Public note
2006; see NEPHROBLASTOMA 1994-2005, WILMS' TUMOR 1991-1993, see NEPHROBLASTOMA 1963-1990

C Diseases
C04 Neoplasms 12 774
C04.557.435.075 Adenolymphoma 25
C04.557.435.090 Adenoma, Pleomorphic 47
C04.557.435.108 Adenomyoepithelioma 1
C04.557.435.110 Adenomyoma 17
C04.557.435.135 Adenosarcoma 8
C04.557.435.250 Carcinoma, Adenosquamous 19
C04.557.435.290 Carcinosarcoma 25
C04.557.435.295 Composite Lymphoma 3
C04.557.435.380 Hepatoblastoma 27
C04.557.435.500 Mesenchymoma 26
C04.557.435.525 Mixed Tumor, Malignant 7
C04.557.435.530 Mixed Tumor, Mesodermal 1
C04.557.435.540 Mixed Tumor, Mullerian 7
C04.557.435.585 Myoepithelioma 23
C04.557.435.595 Wilms Tumor 112
C04.557.435.595.220 Denys-Drash Syndrome 2
C04.557.435.595.950 WAGR Syndrome 3
C04.557.435.600 Nephroma, Mesoblastic 5
C04.557.435.675 Pulmonary Blastoma 8
C04.557.435.710 Rhabdoid Tumor 25
C04.557.435.850 Thymoma 81
C04.588.945 Urogenital Neoplasms 123
C04.588.945.947 Urologic Neoplasms 294
C04.588.945.947.535 Kidney Neoplasms 2 092
C04.588.945.947.535.160 Carcinoma, Renal Cell 1 117
C04.588.945.947.535.585 Wilms Tumor 112
C04.588.945.947.535.585.220 Denys-Drash Syndrome 2
C04.588.945.947.535.585.950 WAGR Syndrome 3
C04.588.945.947.535.790 Nephroma, Mesoblastic 5
C04.700.600 Li-Fraumeni Syndrome 39
C04.700.631 Neurofibromatoses 28
C04.700.700 Tuberous Sclerosis 141
C04.700.900 Wilms Tumor 112
C04.700.900.220 Denys-Drash Syndrome 2
C04.700.900.950 WAGR Syndrome 3
C12.050.351.937 Urogenital Neoplasms 123
C12.050.351.937.820 Urologic Neoplasms 294
C12.050.351.937.820.535 Kidney Neoplasms 2 092
C12.050.351.937.820.535.160 Carcinoma, Renal Cell 1 117
C12.050.351.937.820.535.585 Wilms Tumor 112
C12.050.351.937.820.535.585.220 Denys-Drash Syndrome 2
C12.050.351.937.820.535.585.950 WAGR Syndrome 3
C12.050.351.937.820.535.790 Nephroma, Mesoblastic 5
C12.050.351.968 Urologic Diseases 834
C12.050.351.968.419 Kidney Diseases 3 060
C12.050.351.968.419.473 Kidney Neoplasms 2 092
C12.050.351.968.419.473.160 Carcinoma, Renal Cell 1 117
C12.050.351.968.419.473.372 Nephroma, Mesoblastic 5
C12.050.351.968.419.473.585 Wilms Tumor 112
C12.050.351.968.419.473.585.220 Denys-Drash Syndrome 2
C12.050.351.968.419.473.585.950 WAGR Syndrome 3
C12.200.758 Urogenital Neoplasms 123
C12.200.758.820 Urologic Neoplasms 294
C12.200.758.820.750 Kidney Neoplasms 2 092
C12.200.758.820.750.160 Carcinoma, Renal Cell 1 117
C12.200.758.820.750.372 Nephroma, Mesoblastic 5
C12.200.758.820.750.585 Wilms Tumor 112
C12.200.758.820.750.585.220 Denys-Drash Syndrome 2
C12.200.758.820.750.585.950 WAGR Syndrome 3
C12.200.777 Urologic Diseases 834
C12.200.777.419 Kidney Diseases 3 060
C12.200.777.419.473 Kidney Neoplasms 2 092
C12.200.777.419.473.160 Carcinoma, Renal Cell 1 117
C12.200.777.419.473.372 Nephroma, Mesoblastic 5
C12.200.777.419.473.585 Wilms Tumor 112
C12.200.777.419.473.585.220 Denys-Drash Syndrome 2
C12.200.777.419.473.585.950 WAGR Syndrome 3
C12.900.820 Urologic Neoplasms 294
C12.900.820.535 Kidney Neoplasms 2 092
C12.900.820.535.160 Carcinoma, Renal Cell 1 117
C12.900.820.535.585 Wilms Tumor 112
C12.900.820.535.585.220 Denys-Drash Syndrome 2
C12.900.820.535.585.950 WAGR Syndrome 3
C12.900.820.535.790 Nephroma, Mesoblastic 5
C12.950.419 Kidney Diseases 3 060
C12.950.419.473 Kidney Neoplasms 2 092
C12.950.419.473.160 Carcinoma, Renal Cell 1 117
C12.950.419.473.372 Nephroma, Mesoblastic 5
C12.950.419.473.585 Wilms Tumor 112
C12.950.419.473.585.220 Denys-Drash Syndrome 2
C12.950.419.473.585.950 WAGR Syndrome 3
C12.950.983 Urologic Neoplasms 294
C12.950.983.535 Kidney Neoplasms 2 092
C12.950.983.535.160 Carcinoma, Renal Cell 1 117
C12.950.983.535.585 Wilms Tumor 112
C12.950.983.535.585.220 Denys-Drash Syndrome 2
C12.950.983.535.585.950 WAGR Syndrome 3
C12.950.983.535.790 Nephroma, Mesoblastic 5
C16.320.700.100 Adenomatous Polyposis Coli 92
C16.320.700.175 Basal Cell Nevus Syndrome 33
C16.320.700.212 Birt-Hogg-Dube Syndrome 8
C16.320.700.305 Dysplastic Nevus Syndrome 17
C16.320.700.600 Li-Fraumeni Syndrome 39
C16.320.700.633 Neurofibromatoses 28
C16.320.700.667 Peutz-Jeghers Syndrome 37
C16.320.700.700 Tuberous Sclerosis 141
C16.320.700.900 Wilms Tumor 112
C16.320.700.900.220 Denys-Drash Syndrome 2
C16.320.700.900.950 WAGR Syndrome 3

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