Multiple System Atrophy [multisystémová atrofie]

topical
56
Terms

mnohotná systémová atrofie
syndrom mnohotné systémové atrofie
syndrom multisystémové atrofie

 

Multiple System Atrophy Syndrome
Multisystem Atrophy
Multisystemic Atrophy

Persistent link   https://www.medvik.cz/link/D019578
Definition

A syndrome complex composed of three conditions which represent clinical variants of the same disease process: STRIATONIGRAL DEGENERATION; SHY-DRAGER SYNDROME; and the sporadic form of OLIVOPONTOCEREBELLAR ATROPHIES. Clinical features include autonomic, cerebellar, and basal ganglia dysfunction. Pathologic examination reveals atrophy of the basal ganglia, cerebellum, pons, and medulla, with prominent loss of autonomic neurons in the brain stem and spinal cord. (From Adams et al., Principles of Neurology, 6th ed, p1076; Baillieres Clin Neurol 1997 Apr;6(1):187-204; Med Clin North Am 1999 Mar;83(2):381-92)

Annotation
a specific neurodegenerative syndrome complex; not for atrophy in other systems
DUI
D019578 MeSH Browser
CUI
M0029076
Previous indexing
Autonomic Nervous System Diseases (1981-1997); Brain Diseases (1981-1993); Nervous System Diseases (1969-1997); Shy-Drager Syndrome (1981-1997)
History note
1998
Public note
1998

C Diseases
C10.177.575.300 Dysautonomia, Familial 7
C10.177.575.550 Multiple System Atrophy 56
C10.177.575.550.375 Olivopontocerebellar Atrophies 21
C10.177.575.550.750 Shy-Drager Syndrome 5
C10.177.575.550.875 Striatonigral Degeneration 4
C10.177.575.600 Orthostatic Intolerance 7
C10.177.575.650 Pure Autonomic Failure
C10.228.140 Brain Diseases 1 178
C10.228.140.079 Basal Ganglia Diseases 100
C10.228.140.079.294 Chorea Gravidarum 2
C10.228.140.079.357 Dystonia Musculorum Deformans 3
C10.228.140.079.493 Hepatolenticular Degeneration 243
C10.228.140.079.545 Huntington Disease 322
C10.228.140.079.590 Meige Syndrome 9
C10.228.140.079.612 Multiple System Atrophy 56
C10.228.140.079.612.600 Olivopontocerebellar Atrophies 21
C10.228.140.079.612.700 Shy-Drager Syndrome 5
C10.228.140.079.612.800 Striatonigral Degeneration 4
C10.228.140.079.737 Neuroleptic Malignant Syndrome 46
C10.228.140.079.862 Parkinsonian Disorders 301
C10.228.140.079.882 Supranuclear Palsy, Progressive 50
C10.228.140.079.898 Tourette Syndrome 86
C10.228.662 Movement Disorders 914
C10.228.662.037 Akathisia, Drug-Induced 29
C10.228.662.075 Angelman Syndrome 35
C10.228.662.262 Dyskinesias 88
C10.228.662.300 Dystonic Disorders 81
C10.228.662.350 Essential Tremor 55
C10.228.662.550 Multiple System Atrophy 56
C10.228.662.550.600 Olivopontocerebellar Atrophies 21
C10.228.662.550.700 Shy-Drager Syndrome 5
C10.228.662.550.800 Striatonigral Degeneration 4
C10.228.662.600 Parkinsonian Disorders 301
C10.228.662.825 Tic Disorders 25
C10.574.928 Synucleinopathies 28
C10.574.928.500 Lewy Body Disease 115
C10.574.928.625 Multiple System Atrophy 56
C10.574.928.750 Parkinson Disease 1 580

Multiple system atrophy (MSA) with orthostatic hypotension Disease MeSH Browser