Dystonia Musculorum Deformans [dystonia musculorum deformans]

topical
3
Terms

idiopatická torzní dystonie
progresivní torzní spasmus
torzní dystonie
Ziehenova-Oppenheimova nemoc

 

Childhood Torsion Disease
Dystonia Deformans Musculorum
Dystonia Deformans Progressiva
Idiopathic Torsion Dystonia
Oppenheim-Ziehen Disease
Progressive Torsion Spasm
Torsion Disease of Childhood
Torsion Dystonia

Persistent link   https://www.medvik.cz/link/D004422
Definition

A condition characterized by focal DYSTONIA that progresses to involuntary spasmodic contractions of the muscles of the legs, trunk, arms, and face. The hands are often spared, however, sustained axial and limb contractions may lead to a state where the body is grossly contorted. Onset is usually in the first or second decade. Familial patterns of inheritance, primarily autosomal dominant with incomplete penetrance, have been identified. (Adams et al., Principles of Neurology, 6th ed, p1078)

DUI
D004422 MeSH Browser
CUI
M0006936

C Diseases
C10.228.140 Brain Diseases 1 186
C10.228.140.079 Basal Ganglia Diseases 103
C10.228.140.079.294 Chorea Gravidarum 2
C10.228.140.079.357 Dystonia Musculorum Deformans 3
C10.228.140.079.493 Hepatolenticular Degeneration 243
C10.228.140.079.545 Huntington Disease 327
C10.228.140.079.590 Meige Syndrome 9
C10.228.140.079.612 Multiple System Atrophy 60
C10.228.140.079.737 Neuroleptic Malignant Syndrome 48
C10.228.140.079.862 Parkinsonian Disorders 307
C10.228.140.079.882 Supranuclear Palsy, Progressive 51
C10.228.140.079.898 Tourette Syndrome 86
C10.228.662 Movement Disorders 922
C10.228.662.300 Dystonic Disorders 87
C10.228.662.300.200 Dystonia Musculorum Deformans 3
C10.228.662.300.500 Meige Syndrome 9
C10.574.500.024 Alexander Disease 7
C10.574.500.300 Canavan Disease 9
C10.574.500.362 Cockayne Syndrome 4
C10.574.500.497 Huntington Disease 327
C10.574.500.529 Lafora Disease 1
C10.574.500.545 Myotonia Congenita 19
C10.574.500.547 Myotonic Dystrophy 96
C10.574.500.549 Neurofibromatoses 28
C10.574.500.850 Tourette Syndrome 86
C10.574.500.865 Tuberous Sclerosis 145
C16.320.400.024 Alexander Disease 7
C16.320.400.150 Canavan Disease 9
C16.320.400.200 Cockayne Syndrome 4
C16.320.400.430 Huntington Disease 327
C16.320.400.480 Lafora Disease 1
C16.320.400.540 Myotonia Congenita 19
C16.320.400.542 Myotonic Dystrophy 96
C16.320.400.550 Neuroacanthocytosis 6
C16.320.400.560 Neurofibromatoses 28
C16.320.400.820 Tourette Syndrome 86
C16.320.400.880 Tuberous Sclerosis 145

Dystonia 15, myoclonic Disease MeSH Browser

Dystonia 6, torsion Disease MeSH Browser

Dystonia musculorum deformans 4 Disease MeSH Browser

Dystonia musculorum deformans type 1 Disease MeSH Browser

Dystonia musculorum deformans type 2 Disease MeSH Browser

Whispering dysphonia, hereditary Disease MeSH Browser