Myotonia Congenita [myotonia congenita]

topical
18
Terms

ataxia muscularis
autozomálně dominantní myotonia congenita
Beckerova choroba
Beckerova forma MC
Beckerova kongenitální myotonie
Beckerova nemoc
generalizovaná myotonie
kongenitální myotonie
myotonia congenita, autozomálně dominantní
myotonia congenita, Beckerova forma
myotonia congenita, Thomsenova forma
myotonia levior
Thomsenova choroba
Thomsenova forma MC
Thomsenova kongenitální myotonie
Thomsenova nemoc
Thomsenův syndrom
vrozená myotonie
vrozená myotonie dominantní, Thomsenova
vrozená recesivní myotonie, Beckerova

 

Batten Turner Congenital Myopathy
Batten-Turner Congenital Myopathy
Becker Disease
Becker Generalized Myotonia
Congenital Myotonia
Generalized Myotonia of Becker
Generalized Myotonia of Thomsen
Myopathy, Congenital
Myotonia Congenita, Autosomal Dominant
Myotonia Congenita, Autosomal Recessive
Myotonia Levior
Myotonia, Generalized
Myotonia, Generalized, Becker
Thomsen Disease
Thomsen's Disease
Thomsens Disease

Persistent link   https://www.medvik.cz/link/D009224
Definition

Inherited myotonic disorders with early childhood onset MYOTONIA. Muscular hypertrophy is common and myotonia may impair ambulation and other movements. It is classified as Thomsen (autosomal dominant) or Becker (autosomal recessive) generalized myotonia mainly based on the inheritance pattern. Becker type is also clinically more severe. An autosomal dominant variant with milder symptoms and later onset is known as myotonia levior. Mutations in the voltage-dependent skeletal muscle chloride channel are associated with the disorders.

DUI
D009224 MeSH Browser
CUI
M0014373

C Diseases
C05.651.662 Myotonic Disorders 23
C05.651.662.500 Myotonia Congenita 18
C05.651.662.750 Myotonic Dystrophy 96
C10.574.500.024 Alexander Disease 6
C10.574.500.300 Canavan Disease 9
C10.574.500.362 Cockayne Syndrome 4
C10.574.500.497 Huntington Disease 326
C10.574.500.529 Lafora Disease 1
C10.574.500.545 Myotonia Congenita 18
C10.574.500.547 Myotonic Dystrophy 96
C10.574.500.549 Neurofibromatoses 28
C10.574.500.850 Tourette Syndrome 86
C10.574.500.865 Tuberous Sclerosis 144
C10.668.491 Muscular Diseases 557
C10.668.491.606 Myotonic Disorders 23
C10.668.491.606.500 Myotonia Congenita 18
C10.668.491.606.750 Myotonic Dystrophy 96
C16.320.400.024 Alexander Disease 6
C16.320.400.150 Canavan Disease 9
C16.320.400.200 Cockayne Syndrome 4
C16.320.400.430 Huntington Disease 326
C16.320.400.480 Lafora Disease 1
C16.320.400.540 Myotonia Congenita 18
C16.320.400.542 Myotonic Dystrophy 96
C16.320.400.550 Neuroacanthocytosis 6
C16.320.400.560 Neurofibromatoses 28
C16.320.400.820 Tourette Syndrome 86
C16.320.400.880 Tuberous Sclerosis 144

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