vrozené srdeční vady [Heart Defects, Congenital]

tematický
1 563
Termíny

abnormality srdce
kongenitální srdeční vady
srdce - defekty kongenitální
srdce - vady vrozené
srdeční abnormality
vrozené vady srdce

 

Abnormality, Heart
Congenital Heart Defect
Congenital Heart Defects
Congenital Heart Disease
Defects, Congenital Heart
Heart Abnormalities
Heart Defect, Congenital
Heart, Malformation Of

Perzistentní odkaz   https://www.medvik.cz/link/D006330
Definice

Vrozené vývojové vady postihující srdce (patří k nejčastějším VVV). Kombinace různých anatomických anomálií jednotlivých struktur a přilehlých cév. Vady se dělí podle morfologického defektu nebo funkčně. (cit. Velký lékařský slovník online, 2013 http://lekarske.slovniky.cz/ )

Developmental abnormalities involving structures of the heart. These defects are present at birth but may be discovered later in life.

Anotace
general only; do not use as coordinate for specific term /abnorm; cyanotic defects probably go here but do not also index under CYANOSIS unless especially discussed
DUI
D006330 MeSH Prohlížeč
CUI
M0009950

C Nemoci
C14.240.400 vrozené srdeční vady 1 563
C14.240.400.021 syndrom delece 22q11 2
C14.240.400.044 Alagillův syndrom 19
C14.240.400.090 koarktace aorty 203
C14.240.400.172 Barthův syndrom 6
C14.240.400.200 cor triatriatum 3
C14.240.400.210 anomálie koronárních cév 119
C14.240.400.220 crisscross srdce 1
C14.240.400.280 dextrokardie 21
C14.240.400.340 otevřená tepenná dučej 108
C14.240.400.395 Ebsteinova anomálie 46
C14.240.400.422 ectopia cordis 1
C14.240.400.450 Eisenmengerův syndrom 23
C14.240.400.560 defekty srdečního septa 164
C14.240.400.592 heterotaxe 7
C14.240.400.701 levokardie 2
C14.240.400.725 Marfanův syndrom 105
C14.240.400.787 Noonanové syndrom 52
C14.240.400.849 Fallotova tetralogie 163
C14.240.400.915 transpozice velkých cév 109
C14.240.400.920 trikuspidální atrézie 11
C14.240.400.960 Fallotova trilogie 2
C14.240.400.970 Patauův syndrom 6
C14.240.400.975 syndrom trizomie 18 5
C14.240.400.980 Turnerův syndrom 272
C14.240.400.990 jednokomorové srdce 3
C14.240.850 cévní malformace 58
C14.280 nemoci srdce 2 874
C14.280.067 srdeční arytmie 2 797
C14.280.155 srdeční tamponáda 125
C14.280.195 kardiomegalie 443
C14.280.238 kardiomyopatie 1 059
C14.280.260 kardiotoxicita 142
C14.280.282 endokarditida 336
C14.280.358 aneurysma srdce 70
C14.280.383 srdeční zástava 620
C14.280.400 vrozené srdeční vady 1 563
C14.280.400.044 syndrom delece 22q11 2
C14.280.400.090 koarktace aorty 203
C14.280.400.172 Barthův syndrom 6
C14.280.400.200 cor triatriatum 3
C14.280.400.210 anomálie koronárních cév 119
C14.280.400.220 crisscross srdce 1
C14.280.400.280 dextrokardie 21
C14.280.400.340 otevřená tepenná dučej 108
C14.280.400.395 Ebsteinova anomálie 46
C14.280.400.450 Eisenmengerův syndrom 23
C14.280.400.560 defekty srdečního septa 164
C14.280.400.592 heterotaxe 7
C14.280.400.701 levokardie 2
C14.280.400.725 Marfanův syndrom 105
C14.280.400.787 Noonanové syndrom 52
C14.280.400.849 Fallotova tetralogie 163
C14.280.400.915 transpozice velkých cév 109
C14.280.400.920 trikuspidální atrézie 11
C14.280.400.960 Fallotova trilogie 2
C14.280.400.970 Patauův syndrom 6
C14.280.400.975 syndrom trizomie 18 5
C14.280.400.980 Turnerův syndrom 272
C14.280.400.990 jednokomorové srdce 3
C14.280.434 srdeční selhání 4 591
C14.280.459 nádory srdce 288
C14.280.470 ruptura srdce 30
C14.280.695 perikardiální efuze 169
C14.280.720 perikarditida 234
C14.280.763 pneumoperikard 11
C14.280.832 cor pulmonale 249
C14.280.874 revmatická karditida 107
C14.280.945 komorová dysfunkce 94
C16.131 vrozené vady 1 753
C16.131.240.400 vrozené srdeční vady 1 563
C16.131.240.400.021 syndrom delece 22q11 2
C16.131.240.400.044 Alagillův syndrom 19
C16.131.240.400.090 koarktace aorty 203
C16.131.240.400.118 aorto-ventrikulární tunel 1
C16.131.240.400.172 Barthův syndrom 6
C16.131.240.400.200 cor triatriatum 3
C16.131.240.400.210 anomálie koronárních cév 119
C16.131.240.400.220 crisscross srdce 1
C16.131.240.400.280 dextrokardie 21
C16.131.240.400.340 otevřená tepenná dučej 108
C16.131.240.400.395 Ebsteinova anomálie 46
C16.131.240.400.422 ectopia cordis 1
C16.131.240.400.450 Eisenmengerův syndrom 23
C16.131.240.400.560 defekty srdečního septa 164
C16.131.240.400.592 heterotaxe 7
C16.131.240.400.625 syndrom hypoplazie levého srdce 34
C16.131.240.400.701 levokardie 2
C16.131.240.400.715 syndrom dlouhého QT 218
C16.131.240.400.720 Marfanův syndrom 105
C16.131.240.400.784 Noonanové syndrom 52
C16.131.240.400.849 Fallotova tetralogie 163
C16.131.240.400.915 transpozice velkých cév 109
C16.131.240.400.920 trikuspidální atrézie 11
C16.131.240.400.960 Fallotova trilogie 2
C16.131.240.400.965 Patauův syndrom 6
C16.131.240.400.968 syndrom trizomie 18 5
C16.131.240.400.970 Turnerův syndrom 272
C16.131.240.400.975 jednokomorové srdce 3
C16.131.240.850 cévní malformace 58

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Amastia, Bilateral, With Ureteral Triplication And Dysmorphism Disease MeSH Prohlížeč

Aplasia Cutis Congenita, Congenital Heart Defect, And Frontonasal Cysts Disease MeSH Prohlížeč

Arterial Occlusive Disease, Progressive, with Hypertension, Heart Defects, Bone Fragility, and Brachysyndactyly Disease MeSH Prohlížeč

Baetz-Greenwalt syndrome Disease MeSH Prohlížeč

Beemer Ertbruggen syndrome Disease MeSH Prohlížeč

Bixler Christian Gorlin syndrome Disease MeSH Prohlížeč

Blepharophimosis syndrome Ohdo type Disease MeSH Prohlížeč

Bonneau Syndrome Disease MeSH Prohlížeč

Burn-Mckeown syndrome Disease MeSH Prohlížeč

Cardiac Malformation, Cleft Lip-Palate, Microcephaly and Digital Anomalies Disease MeSH Prohlížeč

Cardiac Valvular Defect, Developmental Disease MeSH Prohlížeč

Cardiac valvular dysplasia, X-linked Disease MeSH Prohlížeč

Cardioauditory syndrome of Sanchez Cascos Disease MeSH Prohlížeč

Cardiocranial syndrome Disease MeSH Prohlížeč

Cardiofaciocutaneous syndrome Disease MeSH Prohlížeč

Chromosome 1q21.1 Duplication Syndrome Disease MeSH Prohlížeč

Chromosome 6pter-P24 Deletion Syndrome Disease MeSH Prohlížeč

Cleft Palate, Cardiac Defect, Genital Anomalies, and Ectrodactyly Disease MeSH Prohlížeč

Congenital Heart Defects, X-Linked Disease MeSH Prohlížeč

Conotruncal cardiac defects Disease MeSH Prohlížeč

Corpus Callosum, Agenesis of, with Facial Anomalies and Robin Sequence Disease MeSH Prohlížeč

Cranioacrofacial Syndrome Disease MeSH Prohlížeč

Craniofacial Abnormalities, Cataracts, Congenital Heart Disease, Sacral Neural Tube Defects, and Growth and Developmental Retardation Disease MeSH Prohlížeč

Craniofaciofrontodigital Syndrome Disease MeSH Prohlížeč

Deafness, Congenital Heart Defects, and Posterior Embryotoxon Disease MeSH Prohlížeč

Distichiasis with Congenital Anomalies of the Heart and Peripheral Vasculature Disease MeSH Prohlížeč

Ectrodactyly cardiopathy dysmorphism Disease MeSH Prohlížeč

Ectrodactyly of Lower Limbs, Congenital Heart Defect, and Micrognathia Disease MeSH Prohlížeč

Ellis Yale Winter syndrome Disease MeSH Prohlížeč

Emanuel syndrome Disease MeSH Prohlížeč

Faciocardiomelic Dysplasia, Lethal Disease MeSH Prohlížeč

Faciocardiomelic Syndrome Disease MeSH Prohlížeč

Faciocardiorenal syndrome Disease MeSH Prohlížeč

Familial anomalous origin of right pulmonary artery Disease MeSH Prohlížeč

Fragile Site 16p12 Disease MeSH Prohlížeč

Frontoocular Syndrome Disease MeSH Prohlížeč

Gay Feinmesser Cohen syndrome Disease MeSH Prohlížeč

Genito palato cardiac syndrome Disease MeSH Prohlížeč

Growth and Developmental Retardation, Ocular Ptosis, Cardiac Defect, and Anal Atresia Disease MeSH Prohlížeč

Heart defects limb shortening Disease MeSH Prohlížeč

Heart-hand syndrome, Slovenian type Disease MeSH Prohlížeč

Heart-hand syndrome, Spanish type Disease MeSH Prohlížeč

Hecht Scott syndrome Disease MeSH Prohlížeč

Hirschsprung Disease with Heart Defects, Laryngeal Anomalies, and Preaxial Polydactyly Disease MeSH Prohlížeč

Hirschsprung Disease, Cardiac Defects, and Autonomic Dysfunction Disease MeSH Prohlížeč

Hittner Hirsch Kreh syndrome Disease MeSH Prohlížeč

Ho Kaufman Mcalister syndrome Disease MeSH Prohlížeč

Holt-Oram syndrome Disease MeSH Prohlížeč

Holzgreve Wagner Rehder syndrome Disease MeSH Prohlížeč

Hydrolethalus syndrome Disease MeSH Prohlížeč

Kasznica Carlson Coppedge syndrome Disease MeSH Prohlížeč

Kleefstra Syndrome Disease MeSH Prohlížeč

Lowry Maclean syndrome Disease MeSH Prohlížeč

Malpuech facial clefting syndrome Disease MeSH Prohlížeč

McDonough syndrome Disease MeSH Prohlížeč

McKusick Kaufman syndrome Disease MeSH Prohlížeč

McPherson Clemens syndrome Disease MeSH Prohlížeč

Mehta Lewis Patton syndrome Disease MeSH Prohlížeč

Mexican Cardiomelic Dysplasia Disease MeSH Prohlížeč

Microcephaly seizures mental retardation heart disorders Disease MeSH Prohlížeč

Microcephaly, Congenital Heart Disease, Unilateral Renal Agenesis, and Hyposegmented Lungs Disease MeSH Prohlížeč

Noncompaction of Left Ventricular Myocardium with Congenital Heart Defects Disease MeSH Prohlížeč

Orstavik Lindemann Solberg syndrome Disease MeSH Prohlížeč

Pancreatic Hypoplasia, Congenital, with Diabetes Mellitus and Congenital Heart Disease Disease MeSH Prohlížeč

Pilotto syndrome Disease MeSH Prohlížeč

Powell Chandra Saal syndrome Disease MeSH Prohlížeč

Pseudodiastrophic dysplasia Disease MeSH Prohlížeč

Pulmonary Atresia with Intact Ventricular Septum Disease MeSH Prohlížeč

Right ventricle hypoplasia Disease MeSH Prohlížeč

Rommen Mueller Sybert syndrome Disease MeSH Prohlížeč

Saal Bulas syndrome Disease MeSH Prohlížeč

Sacral meningocele conotruncal heart defects Disease MeSH Prohlížeč

Scimitar Anomaly, Multiple Cardiac Malformations, and Craniofacial and Central Nervous System Abnormalities Disease MeSH Prohlížeč

Short QT Syndrome 1 Disease MeSH Prohlížeč

Short QT Syndrome 2 Disease MeSH Prohlížeč

Short QT Syndrome 3 Disease MeSH Prohlížeč

Simpson-Golabi-Behmel syndrome Disease MeSH Prohlížeč

Sonoda syndrome Disease MeSH Prohlížeč

Steinfeld Syndrome Disease MeSH Prohlížeč

Stratton-Parker Syndrome Disease MeSH Prohlížeč

Subaortic Stenosis, Membranous Disease MeSH Prohlížeč

TARP syndrome Disease MeSH Prohlížeč

Tabatznik syndrome Disease MeSH Prohlížeč

Tamari Goodman syndrome Disease MeSH Prohlížeč

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Thomas syndrome Disease MeSH Prohlížeč

Uhl anomaly Disease MeSH Prohlížeč

VACTERL association Disease MeSH Prohlížeč

VATER association Disease MeSH Prohlížeč

Vater Association With Hydrocephalus Disease MeSH Prohlížeč

Vater-Like Defects with Pulmonary Hypertension, Laryngeal Webs, and Growth Deficiency Disease MeSH Prohlížeč

Ventricular extrasystoles perodactyly Robin sequence Disease MeSH Prohlížeč

Verloove-Vanhorick Brubakk syndrome Disease MeSH Prohlížeč

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