vrozené srdeční vady [Heart Defects, Congenital]
- Termíny
-
abnormality srdce
kongenitální srdeční vady
srdce - defekty kongenitální
srdce - vady vrozené
srdeční abnormality
vrozené vady srdce
-
Abnormality, Heart
Congenital Heart Defect
Congenital Heart Defects
Congenital Heart Disease
Defects, Congenital Heart
Heart Abnormalities
Heart Defect, Congenital
Heart, Malformation Of
Vrozené vývojové vady postihující srdce (patří k nejčastějším VVV). Kombinace různých anatomických anomálií jednotlivých struktur a přilehlých cév. Vady se dělí podle morfologického defektu nebo funkčně. (cit. Velký lékařský slovník online, 2013 http://lekarske.slovniky.cz/ )
Developmental abnormalities involving structures of the heart. These defects are present at birth but may be discovered later in life.
- Anotace
- general only; do not use as coordinate for specific term /abnorm; cyanotic defects probably go here but do not also index under CYANOSIS unless especially discussed
- DUI
- D006330 MeSH Prohlížeč
- CUI
- M0009950
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Aarskog Syndrome Disease MeSH Prohlížeč
Al Gazali Aziz Salem syndrome Disease MeSH Prohlížeč
Amastia, Bilateral, With Ureteral Triplication And Dysmorphism Disease MeSH Prohlížeč
Aplasia Cutis Congenita, Congenital Heart Defect, And Frontonasal Cysts Disease MeSH Prohlížeč
Arterial Occlusive Disease, Progressive, with Hypertension, Heart Defects, Bone Fragility, and Brachysyndactyly Disease MeSH Prohlížeč
Baetz-Greenwalt syndrome Disease MeSH Prohlížeč
Beemer Ertbruggen syndrome Disease MeSH Prohlížeč
Bixler Christian Gorlin syndrome Disease MeSH Prohlížeč
Blepharophimosis syndrome Ohdo type Disease MeSH Prohlížeč
Bonneau Syndrome Disease MeSH Prohlížeč
Burn-Mckeown syndrome Disease MeSH Prohlížeč
Cardiac Malformation, Cleft Lip-Palate, Microcephaly and Digital Anomalies Disease MeSH Prohlížeč
Cardiac Valvular Defect, Developmental Disease MeSH Prohlížeč
Cardiac valvular dysplasia, X-linked Disease MeSH Prohlížeč
Cardioauditory syndrome of Sanchez Cascos Disease MeSH Prohlížeč
Cardiocranial syndrome Disease MeSH Prohlížeč
Cardiofaciocutaneous syndrome Disease MeSH Prohlížeč
Chromosome 1q21.1 Duplication Syndrome Disease MeSH Prohlížeč
Chromosome 6pter-P24 Deletion Syndrome Disease MeSH Prohlížeč
Cleft Palate, Cardiac Defect, Genital Anomalies, and Ectrodactyly Disease MeSH Prohlížeč
Congenital Heart Defects, X-Linked Disease MeSH Prohlížeč
Conotruncal cardiac defects Disease MeSH Prohlížeč
Corpus Callosum, Agenesis of, with Facial Anomalies and Robin Sequence Disease MeSH Prohlížeč
Cranioacrofacial Syndrome Disease MeSH Prohlížeč
Craniofacial Abnormalities, Cataracts, Congenital Heart Disease, Sacral Neural Tube Defects, and Growth and Developmental Retardation Disease MeSH Prohlížeč
Craniofaciofrontodigital Syndrome Disease MeSH Prohlížeč
Deafness, Congenital Heart Defects, and Posterior Embryotoxon Disease MeSH Prohlížeč
Distichiasis with Congenital Anomalies of the Heart and Peripheral Vasculature Disease MeSH Prohlížeč
Ectrodactyly cardiopathy dysmorphism Disease MeSH Prohlížeč
Ectrodactyly of Lower Limbs, Congenital Heart Defect, and Micrognathia Disease MeSH Prohlížeč
Ellis Yale Winter syndrome Disease MeSH Prohlížeč
Emanuel syndrome Disease MeSH Prohlížeč
Faciocardiomelic Dysplasia, Lethal Disease MeSH Prohlížeč
Faciocardiomelic Syndrome Disease MeSH Prohlížeč
Faciocardiorenal syndrome Disease MeSH Prohlížeč
Familial anomalous origin of right pulmonary artery Disease MeSH Prohlížeč
Fragile Site 16p12 Disease MeSH Prohlížeč
Frontoocular Syndrome Disease MeSH Prohlížeč
Gay Feinmesser Cohen syndrome Disease MeSH Prohlížeč
Genito palato cardiac syndrome Disease MeSH Prohlížeč
Growth and Developmental Retardation, Ocular Ptosis, Cardiac Defect, and Anal Atresia Disease MeSH Prohlížeč
Heart defects limb shortening Disease MeSH Prohlížeč
Heart-hand syndrome, Slovenian type Disease MeSH Prohlížeč
Heart-hand syndrome, Spanish type Disease MeSH Prohlížeč
Hecht Scott syndrome Disease MeSH Prohlížeč
Hirschsprung Disease with Heart Defects, Laryngeal Anomalies, and Preaxial Polydactyly Disease MeSH Prohlížeč
Hirschsprung Disease, Cardiac Defects, and Autonomic Dysfunction Disease MeSH Prohlížeč
Hittner Hirsch Kreh syndrome Disease MeSH Prohlížeč
Ho Kaufman Mcalister syndrome Disease MeSH Prohlížeč
Holt-Oram syndrome Disease MeSH Prohlížeč
Holzgreve Wagner Rehder syndrome Disease MeSH Prohlížeč
Hydrolethalus syndrome Disease MeSH Prohlížeč
Kasznica Carlson Coppedge syndrome Disease MeSH Prohlížeč
Kleefstra Syndrome Disease MeSH Prohlížeč
Lowry Maclean syndrome Disease MeSH Prohlížeč
Malpuech facial clefting syndrome Disease MeSH Prohlížeč
McDonough syndrome Disease MeSH Prohlížeč
McKusick Kaufman syndrome Disease MeSH Prohlížeč
McPherson Clemens syndrome Disease MeSH Prohlížeč
Mehta Lewis Patton syndrome Disease MeSH Prohlížeč
Mexican Cardiomelic Dysplasia Disease MeSH Prohlížeč
Microcephaly seizures mental retardation heart disorders Disease MeSH Prohlížeč
Microcephaly, Congenital Heart Disease, Unilateral Renal Agenesis, and Hyposegmented Lungs Disease MeSH Prohlížeč
Noncompaction of Left Ventricular Myocardium with Congenital Heart Defects Disease MeSH Prohlížeč
Orstavik Lindemann Solberg syndrome Disease MeSH Prohlížeč
Pancreatic Hypoplasia, Congenital, with Diabetes Mellitus and Congenital Heart Disease Disease MeSH Prohlížeč
Pilotto syndrome Disease MeSH Prohlížeč
Powell Chandra Saal syndrome Disease MeSH Prohlížeč
Pseudodiastrophic dysplasia Disease MeSH Prohlížeč
Pulmonary Atresia with Intact Ventricular Septum Disease MeSH Prohlížeč
Right ventricle hypoplasia Disease MeSH Prohlížeč
Rommen Mueller Sybert syndrome Disease MeSH Prohlížeč
Saal Bulas syndrome Disease MeSH Prohlížeč
Sacral meningocele conotruncal heart defects Disease MeSH Prohlížeč
Scimitar Anomaly, Multiple Cardiac Malformations, and Craniofacial and Central Nervous System Abnormalities Disease MeSH Prohlížeč
Short QT Syndrome 1 Disease MeSH Prohlížeč
Short QT Syndrome 2 Disease MeSH Prohlížeč
Short QT Syndrome 3 Disease MeSH Prohlížeč
Simpson-Golabi-Behmel syndrome Disease MeSH Prohlížeč
Sonoda syndrome Disease MeSH Prohlížeč
Steinfeld Syndrome Disease MeSH Prohlížeč
Stratton-Parker Syndrome Disease MeSH Prohlížeč
Subaortic Stenosis, Membranous Disease MeSH Prohlížeč
TARP syndrome Disease MeSH Prohlížeč
Tabatznik syndrome Disease MeSH Prohlížeč
Tamari Goodman syndrome Disease MeSH Prohlížeč
Ter Haar syndrome Disease MeSH Prohlížeč
Thomas syndrome Disease MeSH Prohlížeč
Uhl anomaly Disease MeSH Prohlížeč
VACTERL association Disease MeSH Prohlížeč
VATER association Disease MeSH Prohlížeč
Vater Association With Hydrocephalus Disease MeSH Prohlížeč
Vater-Like Defects with Pulmonary Hypertension, Laryngeal Webs, and Growth Deficiency Disease MeSH Prohlížeč
Ventricular extrasystoles perodactyly Robin sequence Disease MeSH Prohlížeč
Verloove-Vanhorick Brubakk syndrome Disease MeSH Prohlížeč
Young Simpson syndrome Disease MeSH Prohlížeč
Zunich neuroectodermal syndrome Disease MeSH Prohlížeč
aorto-atrial tunnel Disease MeSH Prohlížeč
Užší termíny
- Alagillův syndrom
- anomálie koronárních cév
- aorto-ventrikulární tunel
- arytmogenní dysplazie pravé komory
- Barthův syndrom
- bikuspidální aortální chlopeň
- cor triatriatum
- crisscross srdce
- čtyřcípá aortální chlopeň
- defekty srdečního septa
- dextrokardie
- Ebsteinova anomálie
- ectopia cordis
- Eisenmengerův syndrom
- Fallotova tetralogie
- Fallotova trilogie
- heterotaxe
- izolovaná nekompaktnost myokardu komor
- jednokomorové srdce
- koarktace aorty
- levokardie
- Marfanův syndrom
- Noonanové syndrom
- otevřená tepenná dučej
- Patauův syndrom
- syndrom delece 22q11
- syndrom dlouhého QT
- syndrom hypoplazie levého srdce
- syndrom Noonanové s mnohočetnými pihami
- syndrom trizomie 18
- transpozice velkých cév
- trikuspidální atrézie
- Turnerův syndrom
- Wolffův-Parkinsonův-Whiteův syndrom