Arrhythmogenic Right Ventricular Dysplasia [arytmogenní dysplazie pravé komory]

topical
60
Terms

arytmogenní kardiomyopatie pravé komory

 

Arrhythmogenic Right Ventricular Cardiomyopathy
Arrhythmogenic Right Ventricular Cardiomyopathy-Dysplasia
Arrhythmogenic Right Ventricular Dysplasia-Cardiomyopathy
ARVD-C
Right Ventricular Dysplasia, Arrhythmogenic
Ventricular Dysplasia, Right, Arrhythmogenic

Persistent link   https://www.medvik.cz/link/D019571
Definition

A congenital cardiomyopathy that is characterized by infiltration of adipose and fibrous tissue into the RIGHT VENTRICLE wall and loss of myocardial cells. Primary injuries usually are at the free wall of right ventricular and right atria resulting in ventricular and supraventricular arrhythmias.

DUI
D019571 MeSH Browser
CUI
M0029061
Previous indexing
Arrhythmia (1981-1992); Heart Ventricle (1978-1997); Myocardial Diseases (1981-1997); Tachycardia (1978-1992); Tachycardia, Ventricular (1993-1997)
History note
98
Public note
98

C Diseases
C14.240.400 Heart Defects, Congenital 1 563
C14.240.400.021 22q11 Deletion Syndrome 2
C14.240.400.044 Alagille Syndrome 19
C14.240.400.090 Aortic Coarctation 203
C14.240.400.172 Barth Syndrome 6
C14.240.400.200 Cor Triatriatum 3
C14.240.400.210 Coronary Vessel Anomalies 119
C14.240.400.220 Crisscross Heart 1
C14.240.400.280 Dextrocardia 21
C14.240.400.340 Ductus Arteriosus, Patent 108
C14.240.400.395 Ebstein Anomaly 46
C14.240.400.422 Ectopia Cordis 1
C14.240.400.450 Eisenmenger Complex 23
C14.240.400.560 Heart Septal Defects 164
C14.240.400.592 Heterotaxy Syndrome 7
C14.240.400.695 LEOPARD Syndrome 11
C14.240.400.701 Levocardia 2
C14.240.400.725 Marfan Syndrome 105
C14.240.400.787 Noonan Syndrome 52
C14.240.400.849 Tetralogy of Fallot 163
C14.240.400.920 Tricuspid Atresia 11
C14.240.400.960 Trilogy of Fallot 2
C14.240.400.970 Trisomy 13 Syndrome 6
C14.240.400.975 Trisomy 18 Syndrome 5
C14.240.400.980 Turner Syndrome 272
C14.240.400.990 Univentricular Heart 3
C14.280 Heart Diseases 2 874
C14.280.238 Cardiomyopathies 1 059
C14.280.238.057 Cardiomyopathy, Alcoholic 16
C14.280.238.070 Cardiomyopathy, Dilated 341
C14.280.238.100 Cardiomyopathy, Hypertrophic 510
C14.280.238.190 Chagas Cardiomyopathy 5
C14.280.238.235 Diabetic Cardiomyopathies 68
C14.280.238.281 Endocardial Fibroelastosis 20
C14.280.238.406 Endomyocardial Fibrosis 31
C14.280.238.510 Kearns-Sayre Syndrome 11
C14.280.238.625 Myocarditis 378
C14.280.238.812 Sarcoglycanopathies 2
C14.280.238.906 Takotsubo Cardiomyopathy 79
C14.280.400 Heart Defects, Congenital 1 563
C14.280.400.044 22q11 Deletion Syndrome 2
C14.280.400.090 Aortic Coarctation 203
C14.280.400.172 Barth Syndrome 6
C14.280.400.200 Cor Triatriatum 3
C14.280.400.210 Coronary Vessel Anomalies 119
C14.280.400.220 Crisscross Heart 1
C14.280.400.280 Dextrocardia 21
C14.280.400.340 Ductus Arteriosus, Patent 108
C14.280.400.395 Ebstein Anomaly 46
C14.280.400.450 Eisenmenger Complex 23
C14.280.400.560 Heart Septal Defects 164
C14.280.400.592 Heterotaxy Syndrome 7
C14.280.400.695 LEOPARD Syndrome 11
C14.280.400.701 Levocardia 2
C14.280.400.725 Marfan Syndrome 105
C14.280.400.787 Noonan Syndrome 52
C14.280.400.849 Tetralogy of Fallot 163
C14.280.400.920 Tricuspid Atresia 11
C14.280.400.960 Trilogy of Fallot 2
C14.280.400.970 Trisomy 13 Syndrome 6
C14.280.400.975 Trisomy 18 Syndrome 5
C14.280.400.980 Turner Syndrome 272
C14.280.400.990 Univentricular Heart 3
C16.131.240.400 Heart Defects, Congenital 1 563
C16.131.240.400.021 22q11 Deletion Syndrome 2
C16.131.240.400.044 Alagille Syndrome 19
C16.131.240.400.090 Aortic Coarctation 203
C16.131.240.400.118 Aortico-Ventricular Tunnel 1
C16.131.240.400.172 Barth Syndrome 6
C16.131.240.400.186 Bicuspid Aortic Valve Disease 17
C16.131.240.400.200 Cor Triatriatum 3
C16.131.240.400.210 Coronary Vessel Anomalies 119
C16.131.240.400.220 Crisscross Heart 1
C16.131.240.400.280 Dextrocardia 21
C16.131.240.400.340 Ductus Arteriosus, Patent 108
C16.131.240.400.395 Ebstein Anomaly 46
C16.131.240.400.422 Ectopia Cordis 1
C16.131.240.400.450 Eisenmenger Complex 23
C16.131.240.400.560 Heart Septal Defects 164
C16.131.240.400.592 Heterotaxy Syndrome 7
C16.131.240.400.625 Hypoplastic Left Heart Syndrome 34
C16.131.240.400.685 LEOPARD Syndrome 11
C16.131.240.400.701 Levocardia 2
C16.131.240.400.715 Long QT Syndrome 218
C16.131.240.400.720 Marfan Syndrome 105
C16.131.240.400.784 Noonan Syndrome 52
C16.131.240.400.817 Quadricuspid Aortic Valve
C16.131.240.400.849 Tetralogy of Fallot 163
C16.131.240.400.915 Transposition of Great Vessels 109
C16.131.240.400.920 Tricuspid Atresia 11
C16.131.240.400.960 Trilogy of Fallot 2
C16.131.240.400.965 Trisomy 13 Syndrome 6
C16.131.240.400.968 Trisomy 18 Syndrome 5
C16.131.240.400.970 Turner Syndrome 272
C16.131.240.400.975 Univentricular Heart 3
C16.131.240.400.980 Wolff-Parkinson-White Syndrome 85

Arrhythmogenic Right Ventricular Dysplasia, Familial, 1 Disease MeSH Browser

Arrhythmogenic Right Ventricular Dysplasia, Familial, 10 Disease MeSH Browser

Arrhythmogenic Right Ventricular Dysplasia, Familial, 11 Disease MeSH Browser

Arrhythmogenic Right Ventricular Dysplasia, Familial, 12 Disease MeSH Browser

Arrhythmogenic Right Ventricular Dysplasia, Familial, 2 Disease MeSH Browser

Arrhythmogenic Right Ventricular Dysplasia, Familial, 3 Disease MeSH Browser

Arrhythmogenic Right Ventricular Dysplasia, Familial, 4 Disease MeSH Browser

Arrhythmogenic Right Ventricular Dysplasia, Familial, 5 Disease MeSH Browser

Arrhythmogenic Right Ventricular Dysplasia, Familial, 6 Disease MeSH Browser

Arrhythmogenic Right Ventricular Dysplasia, Familial, 7 Disease MeSH Browser

Arrhythmogenic Right Ventricular Dysplasia, Familial, 8 Disease MeSH Browser

Arrhythmogenic Right Ventricular Dysplasia, Familial, 9 Disease MeSH Browser

Naxos disease Disease MeSH Browser