Achondroplasia [achondroplazie]

topical
71
Terms

achondroplázie
chondrodystrophia fetalis
těžká achondroplazie s opožděným vývojem a acanthosis nigricans
těžká achondroplazie s vývojovým opožděním a hyperpigmentací
těžká achondroplázie s vývojovým opožděním a hyperpigmentací

 

Achondroplasia, Severe, With Developmental Delay And Acanthosis Nigricans
SADDAN
SADDAN Dysplasia
Severe Achondroplasia with Developmental Delay and Acanthosis Nigricans
Skeleton-Skin-Brain Syndrome

Persistent link   https://www.medvik.cz/link/D000130
Definition

An autosomal dominant disorder that is the most frequent form of short-limb dwarfism. Affected individuals exhibit short stature caused by rhizomelic shortening of the limbs, characteristic facies with frontal bossing and mid-face hypoplasia, exaggerated lumbar lordosis, limitation of elbow extension, GENU VARUM, and trident hand. (Online Mendelian Inheritance in Man, http://www.ncbi.nlm.nih.gov/Omim, MIM#100800, April 20, 2001)

DUI
D000130 MeSH Browser
CUI
M0000205

C Diseases
C05.116 Bone Diseases 792
C05.116.099.343 Dwarfism 97
C05.116.099.343.110 Achondroplasia 71
C05.116.099.343.110.500 Thanatophoric Dysplasia 7
C05.116.099.343.250 Cockayne Syndrome 4
C05.116.099.343.347 Congenital Hypothyroidism 151
C05.116.099.343.445 Dwarfism, Pituitary 50
C05.116.099.343.679 Laron Syndrome 1
C05.116.099.343.796 Mulibrey Nanism 1
C05.116.099.343.957 Weill-Marchesani Syndrome 1
C05.116.099.708 Osteochondrodysplasias 123
C05.116.099.708.017 Achondroplasia 71
C05.116.099.708.017.500 Thanatophoric Dysplasia 7
C05.116.099.708.025 Acquired Hyperostosis Syndrome 21
C05.116.099.708.180 Camurati-Engelmann Syndrome 6
C05.116.099.708.195 Chondrodysplasia Punctata 6
C05.116.099.708.207 Cleidocranial Dysplasia 7
C05.116.099.708.327 Ellis-Van Creveld Syndrome 11
C05.116.099.708.338 Enchondromatosis 12
C05.116.099.708.375 Fibrous Dysplasia of Bone 47
C05.116.099.708.486 Hyperostosis Frontalis Interna 3
C05.116.099.708.534 Kashin-Beck Disease
C05.116.099.708.582 Langer-Giedion Syndrome 7
C05.116.099.708.670 Osteochondroma 16
C05.116.099.708.685 Osteogenesis Imperfecta 106
C05.116.099.708.702 Osteosclerosis 38
C05.116.099.708.779 Pycnodysostosis 2
C05.116.099.708.857 Short Rib-Polydactyly Syndrome 3
C16.320.240 Dwarfism 97
C16.320.240.500 Achondroplasia 71
C16.320.240.500.500 Thanatophoric Dysplasia 7
C16.320.240.562 Cockayne Syndrome 4
C16.320.240.625 Congenital Hypothyroidism 151
C16.320.240.750 Laron Syndrome 1
C16.320.240.875 Mulibrey Nanism 1
C16.320.240.937 Silver-Russell Syndrome 3

Achondrogenesis type 1A Disease MeSH Browser

Achondrogenesis type 1B Disease MeSH Browser

Achondrogenesis type 2 Disease MeSH Browser

Achondrogenesis, type 3 Disease MeSH Browser

Achondrogenesis, type 4 Disease MeSH Browser

Achondroplasia and Swiss type agammaglobulinemia Disease MeSH Browser

Achondroplastic dwarfism Disease MeSH Browser

Baby rattle pelvic dysplasia Disease MeSH Browser

Dyssegmental dysplasia, Rolland-Desbuquois type Disease MeSH Browser

Pseudoachondroplasia Disease MeSH Browser

Pseudoachondroplastic dysplasia 2 Disease MeSH Browser

Short-Limb Skeletal Dysplasia with Severe Combined Immunodeficiency Disease MeSH Browser