Long QT Syndrome [syndrom dlouhého QT]

topical
218
Terms

LQTS
syndrom dlouhého intevalu QT

 

Electrocardiogram QT Prolonged

Persistent link   https://www.medvik.cz/link/D008133
Definition

A condition that is characterized by episodes of fainting (SYNCOPE) and varying degree of ventricular arrhythmia as indicated by the prolonged QT interval. The inherited forms are caused by mutation of genes encoding cardiac ion channel proteins. The two major forms are ROMANO-WARD SYNDROME and JERVELL-LANGE NIELSEN SYNDROME.

DUI
D008133 MeSH Browser
CUI
M0012684
Previous indexing
Arrhythmia (1966-1985); Tachycardia (1966-1985)
History note
1991(1986); use ARRHYTHMIA 1986-1990
Public note
1991; see ARRHYTHMIA 1986-1990

C Diseases
C14.280 Heart Diseases 2 874
C14.280.067 Arrhythmias, Cardiac 2 797
C14.280.067.093 Arrhythmia, Sinus 40
C14.280.067.198 Atrial Fibrillation 2 069
C14.280.067.248 Atrial Flutter 140
C14.280.067.319 Bradycardia 275
C14.280.067.322 Brugada Syndrome 40
C14.280.067.441 Commotio Cordis 5
C14.280.067.558 Heart Block 232
C14.280.067.565 Long QT Syndrome 218
C14.280.067.565.070 Andersen Syndrome 2
C14.280.067.565.440 Jervell-Lange Nielsen Syndrome 2
C14.280.067.565.720 Romano-Ward Syndrome 8
C14.280.067.672 Parasystole 1
C14.280.067.780 Pre-Excitation Syndromes 17
C14.280.067.845 Tachycardia 469
C14.280.067.922 Ventricular Fibrillation 390
C14.280.067.961 Ventricular Flutter 13
C14.280.123.250 Brugada Syndrome 40
C14.280.123.500 Heart Block 232
C14.280.123.625 Long QT Syndrome 218
C14.280.123.625.070 Andersen Syndrome 2
C14.280.123.625.440 Jervell-Lange Nielsen Syndrome 2
C14.280.123.625.720 Romano-Ward Syndrome 8
C14.280.123.750 Pre-Excitation Syndromes 17
C14.280.123.875 Tachycardia 469
C16.131.240.400 Heart Defects, Congenital 1 563
C16.131.240.400.021 22q11 Deletion Syndrome 2
C16.131.240.400.044 Alagille Syndrome 19
C16.131.240.400.090 Aortic Coarctation 203
C16.131.240.400.118 Aortico-Ventricular Tunnel 1
C16.131.240.400.172 Barth Syndrome 6
C16.131.240.400.186 Bicuspid Aortic Valve Disease 17
C16.131.240.400.200 Cor Triatriatum 3
C16.131.240.400.210 Coronary Vessel Anomalies 119
C16.131.240.400.220 Crisscross Heart 1
C16.131.240.400.280 Dextrocardia 21
C16.131.240.400.340 Ductus Arteriosus, Patent 108
C16.131.240.400.395 Ebstein Anomaly 46
C16.131.240.400.422 Ectopia Cordis 1
C16.131.240.400.450 Eisenmenger Complex 23
C16.131.240.400.560 Heart Septal Defects 164
C16.131.240.400.592 Heterotaxy Syndrome 7
C16.131.240.400.625 Hypoplastic Left Heart Syndrome 34
C16.131.240.400.685 LEOPARD Syndrome 11
C16.131.240.400.701 Levocardia 2
C16.131.240.400.715 Long QT Syndrome 218
C16.131.240.400.715.070 Andersen Syndrome 2
C16.131.240.400.715.440 Jervell-Lange Nielsen Syndrome 2
C16.131.240.400.715.720 Romano-Ward Syndrome 8
C16.131.240.400.720 Marfan Syndrome 105
C16.131.240.400.784 Noonan Syndrome 52
C16.131.240.400.817 Quadricuspid Aortic Valve
C16.131.240.400.849 Tetralogy of Fallot 163
C16.131.240.400.915 Transposition of Great Vessels 109
C16.131.240.400.920 Tricuspid Atresia 11
C16.131.240.400.960 Trilogy of Fallot 2
C16.131.240.400.965 Trisomy 13 Syndrome 6
C16.131.240.400.968 Trisomy 18 Syndrome 5
C16.131.240.400.970 Turner Syndrome 272
C16.131.240.400.975 Univentricular Heart 3
C16.131.240.400.980 Wolff-Parkinson-White Syndrome 85
C23.550.073 Arrhythmias, Cardiac 2 797
C23.550.073.093 Arrhythmia, Sinus 40
C23.550.073.198 Atrial Fibrillation 2 069
C23.550.073.248 Atrial Flutter 140
C23.550.073.300 Bradycardia 275
C23.550.073.425 Heart Block 232
C23.550.073.547 Long QT Syndrome 218
C23.550.073.547.070 Andersen Syndrome 2
C23.550.073.547.720 Romano-Ward Syndrome 8
C23.550.073.670 Parasystole 1
C23.550.073.845 Tachycardia 469
C23.550.073.922 Ventricular Fibrillation 390
C23.550.073.961 Ventricular Flutter 13

Long QT syndrome type 3 Disease MeSH Browser

Long Qt Syndrome 10 Disease MeSH Browser

Long Qt Syndrome 11 Disease MeSH Browser

Long Qt Syndrome 12 Disease MeSH Browser

Long Qt Syndrome 2 Disease MeSH Browser

Long Qt Syndrome 2-3 Disease MeSH Browser

Long Qt Syndrome 2-5 Disease MeSH Browser

Long Qt Syndrome 3 Disease MeSH Browser

Long Qt Syndrome 3-6 Disease MeSH Browser

Long Qt Syndrome 4 Disease MeSH Browser

Long Qt Syndrome 5 Disease MeSH Browser

Long Qt Syndrome 6 Disease MeSH Browser

Long Qt Syndrome 9 Disease MeSH Browser

Timothy syndrome Disease MeSH Browser