vrozené poruchy glykosylace [Congenital Disorders of Glycosylation]

tematický
30
Termíny

glykoproteinový syndrom deficitu sacharidů
kongenitální poruchy glykosylace

 

Carbohydrate-Deficient Glycoprotein Syndrome
Glycoprotein Syndrome, Carbohydrate-Deficient

Perzistentní odkaz   https://www.medvik.cz/link/D018981
Definice

Geneticky heterogenní skupina dědičných poruch, které vyplývají z chybné glykosylace N-glykoproteinů.

A genetically heterogeneous group of heritable disorders resulting from defects in protein N-glycosylation.

DUI
D018981 MeSH Prohlížeč
CUI
M0028352
Předchozí užití
Carbohydrate Metabolism, Inborn Errors (1991-1995); Glycoproteins (1977-1995)
Historická pozn.
2011(1996)
Veřejná pozn.
2011; CARBOHYDRATE-DEFICIENT GLYCOPROTEIN SYNDROME (1996-2010)

C Nemoci
C16.320.565.202.125 vrozené poruchy glykosylace 30
C16.320.565.202.303 fukosidóza 2
C16.320.565.202.355 galaktosemie 44
C16.320.565.202.449 glykogenóza 45
C16.320.565.202.460 primární hyperoxalurie 10
C16.320.565.202.589 nesnášenlivost laktózy 132
C16.320.565.202.670 mukolipidózy 10
C16.320.565.202.715 mukopolysacharidózy 81
C18.452 metabolické nemoci 1 200
C18.452.648.202.125 vrozené poruchy glykosylace 30
C18.452.648.202.303 fukosidóza 2
C18.452.648.202.355 galaktosemie 44
C18.452.648.202.449 glykogenóza 45
C18.452.648.202.460 primární hyperoxalurie 10
C18.452.648.202.589 nesnášenlivost laktózy 132
C18.452.648.202.670 mukolipidózy 10
C18.452.648.202.715 mukopolysacharidózy 81

Coloboma, Ocular, And Ichthyosis, Brain Malformations, And Endocrine Abnormalities Disease MeSH Prohlížeč

Congenital Disorder Of Glycosylation, Type I-IIX Disease MeSH Prohlížeč

Congenital Disorder Of Glycosylation, Type IIB Disease MeSH Prohlížeč

Congenital Disorder Of Glycosylation, Type IIF Disease MeSH Prohlížeč

Congenital Disorder Of Glycosylation, Type IIH Disease MeSH Prohlížeč

Congenital Disorder Of Glycosylation, Type IIID Disease MeSH Prohlížeč

Congenital Disorder Of Glycosylation, Type Im Disease MeSH Prohlížeč

Congenital Disorder Of Glycosylation, Type In Disease MeSH Prohlížeč

Congenital Disorder of Glycosylation, Type Io Disease MeSH Prohlížeč

Congenital disorder of glycosylation type 1A Disease MeSH Prohlížeč

Congenital disorder of glycosylation type 1B Disease MeSH Prohlížeč

Congenital disorder of glycosylation type 1C Disease MeSH Prohlížeč

Congenital disorder of glycosylation type 1D Disease MeSH Prohlížeč

Congenital disorder of glycosylation type 1E Disease MeSH Prohlížeč

Congenital disorder of glycosylation type 1F Disease MeSH Prohlížeč

Congenital disorder of glycosylation type 1G Disease MeSH Prohlížeč

Congenital disorder of glycosylation type 1H Disease MeSH Prohlížeč

Congenital disorder of glycosylation type 1I Disease MeSH Prohlížeč

Congenital disorder of glycosylation type 1J Disease MeSH Prohlížeč

Congenital disorder of glycosylation type 1K Disease MeSH Prohlížeč

Congenital disorder of glycosylation type 1L Disease MeSH Prohlížeč

Congenital disorder of glycosylation type 1X Disease MeSH Prohlížeč

Congenital disorder of glycosylation type 2A Disease MeSH Prohlížeč

Congenital disorder of glycosylation type 2D Disease MeSH Prohlížeč

Congenital disorder of glycosylation type 2E Disease MeSH Prohlížeč

Congenital disorder of glycosylation type II Disease MeSH Prohlížeč

Congenital disorder of glycosylation, type 2C Disease MeSH Prohlížeč

Congenital disorder of glycosylation, type 2G Disease MeSH Prohlížeč

NGLY1 deficiency Disease MeSH Prohlížeč