Ichthyosiform Erythroderma, Congenital [erythrodermia ichthyosiformis congenita]

topical
8
Terms

erythrodermia ichthyosiformis congenita, suchá forma
erythrodermia ichthyosiformis congenita, vlhká forma
vrozená ichtyoziformní erytrodermie
vrozená primární erytrodermie

 

Congenital Ichthyosiform Erythroderma
Congenital Ichthyosiform Erythroderma, Dry Type
Congenital Ichthyosiform Erythroderma, Wet Type
Erythroderma, Congenital Ichthyosiform

Persistent link   https://www.medvik.cz/link/D016113
Definition

Designation for several severe forms of ichthyosis, present at birth, that are characterized by hyperkeratotic scaling. Infants may be born encased in a collodion membrane which begins shedding within 24 hours. This is followed in about two weeks by persistent generalized scaling. The forms include bullous (HYPERKERATOSIS, EPIDERMOLYTIC), non-bullous (ICHTHYOSIS, LAMELLAR), wet type, and dry type.

Annotation
an ichthyosis rather than an erythroderma; do not use /congen & do not coord with INFANT, NEWBORN, DISEASES
DUI
D016113 MeSH Browser
CUI
M0024612
Previous indexing
Ichthyosis (1966-1990)
History note
91
Public note
91

C Diseases
C16.131.831 Skin Abnormalities 51
C16.131.831.512 Ichthyosis 62
C16.131.831.512.400.375 Hyperkeratosis, Epidermolytic 20
C16.131.831.512.400.410 Ichthyosis, Lamellar 22
C16.131.831.512.400.705 Netherton Syndrome 2
C16.131.831.512.408 Ichthyosis Bullosa of Siemens 3
C16.131.831.512.410 Ichthyosis Vulgaris 5
C16.131.831.512.420 Ichthyosis, X-Linked 9
C16.131.831.512.723 Sjogren-Larsson Syndrome 4
C16.320.850.080 Albinism 17
C16.320.850.180 Cutis Laxa 10
C16.320.850.190 Darier Disease 26
C16.320.850.210 Dermatitis, Atopic 1 444
C16.320.850.235 Dyskeratosis Congenita 9
C16.320.850.250 Ectodermal Dysplasia 33
C16.320.850.260 Ehlers-Danlos Syndrome 51
C16.320.850.275 Epidermolysis Bullosa 108
C16.320.850.400.375 Hyperkeratosis, Epidermolytic 20
C16.320.850.400.410 Ichthyosis, Lamellar 22
C16.320.850.405 Ichthyosis Vulgaris 5
C16.320.850.408 Ichthyosis, X-Linked 9
C16.320.850.420 Incontinentia Pigmenti 19
C16.320.850.475 Keratoderma, Palmoplantar 15
C16.320.850.647 Monilethrix 1
C16.320.850.673 Netherton Syndrome 2
C16.320.850.700 Pemphigus, Benign Familial 11
C16.320.850.730 Porokeratosis 11
C16.320.850.738 Porphyria, Erythropoietic 11
C16.320.850.742 Porphyrias, Hepatic 26
C16.320.850.746 Prolidase Deficiency
C16.320.850.750 Pseudoxanthoma Elasticum 13
C16.320.850.765 Rothmund-Thomson Syndrome 7
C16.320.850.820 Sjogren-Larsson Syndrome 4
C16.320.850.970 Xeroderma Pigmentosum 25
C16.614.492 Ichthyosis 62
C16.614.492.400.375 Hyperkeratosis, Epidermolytic 20
C16.614.492.400.410 Ichthyosis, Lamellar 22
C16.614.492.400.705 Netherton Syndrome 2
C16.614.492.420 Ichthyosis, X-Linked 9
C16.614.492.723 Sjogren-Larsson Syndrome 4
C17.800 Skin Diseases 2 796
C17.800.428 Keratosis 133
C17.800.428.333 Ichthyosis 62
C17.800.428.333.250.375 Hyperkeratosis, Epidermolytic 20
C17.800.428.333.250.410 Ichthyosis, Lamellar 22
C17.800.428.333.250.705 Netherton Syndrome 2
C17.800.428.333.330 Ichthyosis Bullosa of Siemens 3
C17.800.428.333.410 Ichthyosis Vulgaris 5
C17.800.428.333.420 Ichthyosis, X-Linked 9
C17.800.428.333.723 Sjogren-Larsson Syndrome 4
C17.800.804 Skin Abnormalities 51
C17.800.804.512 Ichthyosis 62
C17.800.804.512.400.375 Hyperkeratosis, Epidermolytic 20
C17.800.804.512.400.410 Ichthyosis, Lamellar 22
C17.800.804.512.400.705 Netherton Syndrome 2
C17.800.804.512.405 Ichthyosis Bullosa of Siemens 3
C17.800.804.512.410 Ichthyosis Vulgaris 5
C17.800.804.512.420 Ichthyosis, X-Linked 9
C17.800.804.512.723 Sjogren-Larsson Syndrome 4
C17.800.827.080 Albinism 17
C17.800.827.180 Cutis Laxa 10
C17.800.827.190 Darier Disease 26
C17.800.827.210 Dermatitis, Atopic 1 444
C17.800.827.235 Dyskeratosis Congenita 9
C17.800.827.250 Ectodermal Dysplasia 33
C17.800.827.260 Ehlers-Danlos Syndrome 51
C17.800.827.275 Epidermolysis Bullosa 108
C17.800.827.400.375 Hyperkeratosis, Epidermolytic 20
C17.800.827.400.410 Ichthyosis, Lamellar 22
C17.800.827.405 Ichthyosis Vulgaris 5
C17.800.827.408 Ichthyosis, X-Linked 9
C17.800.827.420 Incontinentia Pigmenti 19
C17.800.827.475 Keratoderma, Palmoplantar 15
C17.800.827.602 Monilethrix 1
C17.800.827.610 Muir-Torre Syndrome 10
C17.800.827.655 Netherton Syndrome 2
C17.800.827.700 Pemphigus, Benign Familial 11
C17.800.827.730 Porokeratosis 11
C17.800.827.738 Porphyria, Erythropoietic 11
C17.800.827.742 Porphyrias, Hepatic 26
C17.800.827.750 Pseudoxanthoma Elasticum 13
C17.800.827.775 Rothmund-Thomson Syndrome 7
C17.800.827.820 Sjogren-Larsson Syndrome 4
C17.800.827.970 Xeroderma Pigmentosum 25