Huntington Disease [Huntingtonova nemoc]

topical
326
Terms

Huntingtonova chorea
Huntingtonova chorea - pozdní nástup
Huntingtonova chorea akineticko-rigidní
Huntingtonova chorea u mladistvých
Huntingtonova choroba
Huntingtonova nemoc - akinetický strnulý typ
Huntingtonova nemoc - pozdní nástup
Huntingtonova nemoc s pozdním nástupem
Huntingtonova nemoc u mladistvých
juvenilní Huntingtonova nemoc

 

Akinetic-Rigid Variant of Huntington Disease
Chorea, Chronic Progressive Hereditary (Huntington)
Chronic Progressive Hereditary Chorea (Huntington)
Huntington Chorea
Huntington Chronic Progressive Hereditary Chorea
Huntington Disease, Akinetic-Rigid Variant
Huntington Disease, Juvenile
Huntington Disease, Juvenile-Onset
Huntington Disease, Late Onset
Huntington's Chorea
Huntington's Disease
Juvenile Huntington Disease
Juvenile-Onset Huntington Disease
Late-Onset Huntington Disease
Progressive Chorea, Chronic Hereditary (Huntington)
Progressive Chorea, Hereditary, Chronic (Huntington)

Persistent link   https://www.medvik.cz/link/D006816
Definition

A familial disorder inherited as an autosomal dominant trait and characterized by the onset of progressive CHOREA and DEMENTIA in the fourth or fifth decade of life. Common initial manifestations include paranoia; poor impulse control; DEPRESSION; HALLUCINATIONS; and DELUSIONS. Eventually intellectual impairment; loss of fine motor control; ATHETOSIS; and diffuse chorea involving axial and limb musculature develops, leading to a vegetative state within 10-15 years of disease onset. The juvenile variant has a more fulminant course including SEIZURES; ATAXIA; dementia; and chorea. (From Adams et al., Principles of Neurology, 6th ed, pp1060-4)

DUI
D006816 MeSH Browser
CUI
M0010660
History note
2000(1963)
Public note
2000; see HUNTINGTON'S DISEASE 1993-1999; for HUNTINGTON DISEASE see HUNTINGTON'S DISEASE 1993-1999, see HUNTINGTON CHOREA 1977-1992, see CHOREA, HEREDITARY 1963-1976

C Diseases
C10.228.140 Brain Diseases 1 183
C10.228.140.079 Basal Ganglia Diseases 103
C10.228.140.079.294 Chorea Gravidarum 2
C10.228.140.079.357 Dystonia Musculorum Deformans 3
C10.228.140.079.493 Hepatolenticular Degeneration 243
C10.228.140.079.545 Huntington Disease 326
C10.228.140.079.590 Meige Syndrome 9
C10.228.140.079.612 Multiple System Atrophy 58
C10.228.140.079.737 Neuroleptic Malignant Syndrome 46
C10.228.140.079.862 Parkinsonian Disorders 304
C10.228.140.079.882 Supranuclear Palsy, Progressive 50
C10.228.140.079.898 Tourette Syndrome 86
C10.228.140.380 Dementia 2 205
C10.228.140.380.070 AIDS Dementia Complex 26
C10.228.140.380.100 Alzheimer Disease 2 653
C10.228.140.380.132 Aphasia, Primary Progressive 18
C10.228.140.380.165 Creutzfeldt-Jakob Syndrome 246
C10.228.140.380.230 Dementia, Vascular 195
C10.228.140.380.278 Huntington Disease 326
C10.228.140.380.326 Kluver-Bucy Syndrome 1
C10.228.140.380.422 Lewy Body Disease 118
C10.228.140.380.711 Mixed Dementias
C10.228.662 Movement Disorders 918
C10.228.662.262 Dyskinesias 89
C10.228.662.262.249 Chorea 86
C10.228.662.262.249.500 Chorea Gravidarum 2
C10.228.662.262.249.750 Huntington Disease 326
C10.228.662.262.249.937 Neuroacanthocytosis 6
C10.574.500.024 Alexander Disease 6
C10.574.500.300 Canavan Disease 9
C10.574.500.362 Cockayne Syndrome 4
C10.574.500.497 Huntington Disease 326
C10.574.500.529 Lafora Disease 1
C10.574.500.545 Myotonia Congenita 18
C10.574.500.547 Myotonic Dystrophy 96
C10.574.500.549 Neurofibromatoses 28
C10.574.500.850 Tourette Syndrome 86
C10.574.500.865 Tuberous Sclerosis 144
C16.320.400.024 Alexander Disease 6
C16.320.400.150 Canavan Disease 9
C16.320.400.200 Cockayne Syndrome 4
C16.320.400.430 Huntington Disease 326
C16.320.400.480 Lafora Disease 1
C16.320.400.540 Myotonia Congenita 18
C16.320.400.542 Myotonic Dystrophy 96
C16.320.400.550 Neuroacanthocytosis 6
C16.320.400.560 Neurofibromatoses 28
C16.320.400.820 Tourette Syndrome 86
C16.320.400.880 Tuberous Sclerosis 144

F Psychiatry and Psychology
F03.615.250 Cognition Disorders 1 334
F03.615.250.400 Huntington Disease 326
F03.615.250.700 Cognitive Dysfunction 472
F03.615.400 Dementia 2 205
F03.615.400.050 AIDS Dementia Complex 26
F03.615.400.100 Alzheimer Disease 2 653
F03.615.400.300 Creutzfeldt-Jakob Syndrome 246
F03.615.400.350 Dementia, Vascular 195
F03.615.400.390 Huntington Disease 326
F03.615.400.431 Kluver-Bucy Syndrome 1
F03.615.400.512 Lewy Body Disease 118
F03.615.400.756 Mixed Dementias

Huntington Disease-Like 1 Disease MeSH Browser

Huntington Disease-Like 3 Disease MeSH Browser

Westphal disease Disease MeSH Browser