Ehlers-Danlos Syndrome [Ehlersův-Danlosův syndrom]

topical
51
Terms

Cutis Elastica
Ehlers Danlos Disease
Ehlers-Danlos Disease

Persistent link   https://www.medvik.cz/link/D004535
Definition

A heterogeneous group of autosomally inherited COLLAGEN DISEASES caused by defects in the synthesis or structure of FIBRILLAR COLLAGEN. There are numerous subtypes: classical, hypermobility, vascular, and others. Common clinical features include hyperextensible skin and joints, skin fragility and reduced wound healing capability.

DUI
D004535 MeSH Browser
CUI
M0007138

C Diseases
C14.907 Vascular Diseases 1 790
C14.907.454 Hemostatic Disorders 49
C14.907.454.140 Cryoglobulinemia 72
C14.907.454.240 Ehlers-Danlos Syndrome 51
C14.907.454.385 Hemangioma, Cavernous 53
C14.907.454.460 Multiple Myeloma 1 782
C14.907.454.530 Pseudoxanthoma Elasticum 13
C14.907.454.800 Scurvy 28
C14.907.454.810 Shwartzman Phenomenon 10
C15.378.463.515 Hemostatic Disorders 49
C15.378.463.515.140 Cryoglobulinemia 72
C15.378.463.515.240 Ehlers-Danlos Syndrome 51
C15.378.463.515.240.500 Ehlers-Danlos Syndrome, Type IV
C15.378.463.515.385 Hemangioma, Cavernous 53
C15.378.463.515.460 Multiple Myeloma 1 782
C15.378.463.515.530 Pseudoxanthoma Elasticum 13
C15.378.463.515.550 Purpura, Hyperglobulinemic 4
C15.378.463.515.580 IgA Vasculitis 76
C15.378.463.515.800 Scurvy 28
C15.378.463.515.810 Shwartzman Phenomenon 10
C15.378.463.515.960 Waldenstrom Macroglobulinemia 112
C16.131.831 Skin Abnormalities 51
C16.131.831.066 Acrodermatitis 66
C16.131.831.108 Carney Complex 8
C16.131.831.150 Dyskeratosis Congenita 9
C16.131.831.350 Ectodermal Dysplasia 33
C16.131.831.428 Ehlers-Danlos Syndrome 51
C16.131.831.493 Epidermolysis Bullosa 108
C16.131.831.512 Ichthyosis 62
C16.131.831.580 Incontinentia Pigmenti 19
C16.131.831.675 Port-Wine Stain 5
C16.131.831.720 Prolidase Deficiency
C16.131.831.766 Pseudoxanthoma Elasticum 13
C16.131.831.775 Rothmund-Thomson Syndrome 7
C16.131.831.812 Sclerema Neonatorum 2
C16.131.831.936 Xeroderma Pigmentosum 25
C16.320.850.080 Albinism 17
C16.320.850.180 Cutis Laxa 10
C16.320.850.190 Darier Disease 26
C16.320.850.210 Dermatitis, Atopic 1 445
C16.320.850.235 Dyskeratosis Congenita 9
C16.320.850.250 Ectodermal Dysplasia 33
C16.320.850.260 Ehlers-Danlos Syndrome 51
C16.320.850.275 Epidermolysis Bullosa 108
C16.320.850.405 Ichthyosis Vulgaris 5
C16.320.850.408 Ichthyosis, X-Linked 9
C16.320.850.420 Incontinentia Pigmenti 19
C16.320.850.475 Keratoderma, Palmoplantar 15
C16.320.850.647 Monilethrix 1
C16.320.850.673 Netherton Syndrome 2
C16.320.850.700 Pemphigus, Benign Familial 11
C16.320.850.730 Porokeratosis 11
C16.320.850.738 Porphyria, Erythropoietic 11
C16.320.850.742 Porphyrias, Hepatic 26
C16.320.850.746 Prolidase Deficiency
C16.320.850.750 Pseudoxanthoma Elasticum 13
C16.320.850.765 Rothmund-Thomson Syndrome 7
C16.320.850.820 Sjogren-Larsson Syndrome 4
C16.320.850.970 Xeroderma Pigmentosum 25
C17.300.200 Collagen Diseases 183
C17.300.200.310 Ehlers-Danlos Syndrome 51
C17.300.200.425 Keloid 79
C17.300.200.495 Necrobiotic Disorders 3
C17.300.200.517 Nephritis, Hereditary 60
C17.300.200.540 Osteogenesis Imperfecta 106
C17.800 Skin Diseases 2 799
C17.800.804 Skin Abnormalities 51
C17.800.804.066 Acrodermatitis 66
C17.800.804.108 Anetoderma 5
C17.800.804.150 Dyskeratosis Congenita 9
C17.800.804.350 Ectodermal Dysplasia 33
C17.800.804.428 Ehlers-Danlos Syndrome 51
C17.800.804.493 Epidermolysis Bullosa 108
C17.800.804.512 Ichthyosis 62
C17.800.804.580 Incontinentia Pigmenti 19
C17.800.804.675 Port-Wine Stain 5
C17.800.804.766 Pseudoxanthoma Elasticum 13
C17.800.804.775 Rothmund-Thomson Syndrome 7
C17.800.804.812 Sclerema Neonatorum 2
C17.800.804.936 Xeroderma Pigmentosum 25
C17.800.827.080 Albinism 17
C17.800.827.180 Cutis Laxa 10
C17.800.827.190 Darier Disease 26
C17.800.827.210 Dermatitis, Atopic 1 445
C17.800.827.235 Dyskeratosis Congenita 9
C17.800.827.250 Ectodermal Dysplasia 33
C17.800.827.260 Ehlers-Danlos Syndrome 51
C17.800.827.275 Epidermolysis Bullosa 108
C17.800.827.405 Ichthyosis Vulgaris 5
C17.800.827.408 Ichthyosis, X-Linked 9
C17.800.827.420 Incontinentia Pigmenti 19
C17.800.827.475 Keratoderma, Palmoplantar 15
C17.800.827.602 Monilethrix 1
C17.800.827.610 Muir-Torre Syndrome 10
C17.800.827.655 Netherton Syndrome 2
C17.800.827.700 Pemphigus, Benign Familial 11
C17.800.827.730 Porokeratosis 11
C17.800.827.738 Porphyria, Erythropoietic 11
C17.800.827.742 Porphyrias, Hepatic 26
C17.800.827.750 Pseudoxanthoma Elasticum 13
C17.800.827.775 Rothmund-Thomson Syndrome 7
C17.800.827.820 Sjogren-Larsson Syndrome 4
C17.800.827.970 Xeroderma Pigmentosum 25

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