Hemophilia B [hemofilie B]

topical
214
Terms

Christmasova choroba
Christmasova nemoc

 

Christmas Disease
Deficiency, Factor IX
F9 Deficiency
Factor IX Deficiency
Haemophilia B
Hemophilia B Leyden
Hemophilia B(M)
Plasma Thromboplastin Component Deficiency

Persistent link   https://www.medvik.cz/link/D002836
Definition

A deficiency of blood coagulation factor IX inherited as an X-linked disorder. (Also known as Christmas Disease, after the first patient studied in detail, not the holy day.) Historical and clinical features resemble those in classic hemophilia (HEMOPHILIA A), but patients present with fewer symptoms. Severity of bleeding is usually similar in members of a single family. Many patients are asymptomatic until the hemostatic system is stressed by surgery or trauma. Treatment is similar to that for hemophilia A. (From Cecil Textbook of Medicine, 19th ed, p1008)

DUI
D002836 MeSH Browser
CUI
M0004363
History note
1999(1966)
Public note
1999; see CHRISTMAS DISEASE 1966-1998; for HEMOPHILIA B see CHRISTMAS DISEASE 1974-1998; for Hemophilia B Leyden see FACTOR IX 1990-2012

C Diseases
C15.378.100.100.037 Activated Protein C Resistance 105
C15.378.100.100.056 Afibrinogenemia 39
C15.378.100.100.075 Antithrombin III Deficiency 24
C15.378.100.100.080 Bernard-Soulier Syndrome 9
C15.378.100.100.300 Factor V Deficiency 7
C15.378.100.100.310 Factor VII Deficiency 6
C15.378.100.100.320 Factor X Deficiency 2
C15.378.100.100.325 Factor XI Deficiency 12
C15.378.100.100.330 Factor XII Deficiency 8
C15.378.100.100.335 Factor XIII Deficiency 4
C15.378.100.100.500 Hemophilia A 688
C15.378.100.100.510 Hemophilia B 214
C15.378.100.100.515 Hermanski-Pudlak Syndrome 7
C15.378.100.100.550 Hypoprothrombinemias 4
C15.378.100.100.690 Protein C Deficiency 31
C15.378.100.100.820 Thrombasthenia 7
C15.378.100.100.900 von Willebrand Diseases 103
C15.378.100.100.970 Wiskott-Aldrich Syndrome 20
C15.378.100.141.036 Activated Protein C Resistance 105
C15.378.100.141.072 Afibrinogenemia 39
C15.378.100.141.300 Factor V Deficiency 7
C15.378.100.141.310 Factor VII Deficiency 6
C15.378.100.141.320 Factor X Deficiency 2
C15.378.100.141.325 Factor XI Deficiency 12
C15.378.100.141.330 Factor XII Deficiency 8
C15.378.100.141.335 Factor XIII Deficiency 4
C15.378.100.141.500 Hemophilia A 688
C15.378.100.141.510 Hemophilia B 214
C15.378.100.141.550 Hypoprothrombinemias 4
C15.378.100.141.900 von Willebrand Diseases 103
C15.378.463.067 Afibrinogenemia 39
C15.378.463.080 Bernard-Soulier Syndrome 9
C15.378.463.300 Factor V Deficiency 7
C15.378.463.310 Factor VII Deficiency 6
C15.378.463.320 Factor X Deficiency 2
C15.378.463.325 Factor XI Deficiency 12
C15.378.463.330 Factor XII Deficiency 8
C15.378.463.335 Factor XIII Deficiency 4
C15.378.463.500 Hemophilia A 688
C15.378.463.510 Hemophilia B 214
C15.378.463.515 Hemostatic Disorders 49
C15.378.463.550 Hypoprothrombinemias 4
C15.378.463.810 Thrombasthenia 7
C15.378.463.825 Thrombocythemia, Essential 93
C15.378.463.841 Vitamin K Deficiency 42
C15.378.463.920 von Willebrand Diseases 103
C15.378.463.960 Wiskott-Aldrich Syndrome 20
C16.320.099.056 Afibrinogenemia 39
C16.320.099.080 Bernard-Soulier Syndrome 9
C16.320.099.300 Factor V Deficiency 7
C16.320.099.310 Factor VII Deficiency 6
C16.320.099.320 Factor X Deficiency 2
C16.320.099.325 Factor XI Deficiency 12
C16.320.099.330 Factor XII Deficiency 8
C16.320.099.335 Factor XIII Deficiency 4
C16.320.099.417 Gray Platelet Syndrome 1
C16.320.099.500 Hemophilia A 688
C16.320.099.510 Hemophilia B 214
C16.320.099.515 Hermanski-Pudlak Syndrome 7
C16.320.099.550 Hypoprothrombinemias 4
C16.320.099.690 Protein C Deficiency 31
C16.320.099.820 Thrombasthenia 7
C16.320.099.920 von Willebrand Diseases 103
C16.320.099.970 Wiskott-Aldrich Syndrome 20
C16.320.322.030 Aicardi Syndrome
C16.320.322.068 Barth Syndrome 6
C16.320.322.092 Choroideremia 3
C16.320.322.100 Dent Disease 1
C16.320.322.108 Dyskeratosis Congenita 9
C16.320.322.124 Fabry Disease 187
C16.320.322.186 Focal Dermal Hypoplasia 6
C16.320.322.235 Hemophilia B 214
C16.320.322.241 Ichthyosis, X-Linked 9
C16.320.322.562 Muscular Dystrophy, Duchenne 133
C16.320.322.937 Wiskott-Aldrich Syndrome 20