Genetic Diseases, Inborn [genetické nemoci vrozené]

topical
1 213
Terms

dědičné nemoci
monogenně dědičné choroby
monogenní genetické choroby
monogenní nemoci
monogenní onemocnění

 

Genetic Diseases
Genetic Disorders
Hereditary Disease
Hereditary Diseases
Inborn Genetic Diseases
Single-Gene Defects

Persistent link   https://www.medvik.cz/link/D030342
Definition

Diseases that are caused by genetic mutations present during embryo or fetal development, although they may be observed later in life. The mutations may be inherited from a parent's genome or they may be acquired in utero.

Annotation
general; prefer /genet with specific diseases
obecné nebo nevymezené, dej přednost konkrétnějšímu deskriptoru nemoci s podheslem /genetika
DUI
D030342 MeSH Browser
CUI
M0385531
History note
2002
Public note
2002; for HEREDITARY DISEASES see HEREDITARY DISEASES 1968-2001

C Diseases
C01 Infections 2 026
C04 Neoplasms 12 774
C11 Eye Diseases 1 489
C16.300 Fetal Diseases 825
C16.320.051 Alagille Syndrome 19
C16.320.100 Brugada Syndrome 40
C16.320.129 CADASIL 8
C16.320.165 CHARGE Syndrome 1
C16.320.170 Cherubism 1
C16.320.180 Chromosome Disorders 259
C16.320.184 Ciliopathies 9
C16.320.188 Costello Syndrome 3
C16.320.190 Cystic Fibrosis 1 328
C16.320.215 Donohue Syndrome 1
C16.320.240 Dwarfism 97
C16.320.306 Frasier Syndrome
C16.320.314 GATA2 Deficiency 1
C16.320.365 Hemoglobinopathies 68
C16.320.467 Kallmann Syndrome 10
C16.320.480 Kartagener Syndrome 46
C16.320.488 Laminopathies 2
C16.320.540 Marfan Syndrome 105
C16.320.577 Muscular Dystrophies 140
C16.320.728 Osteochondrodysplasias 123
C16.320.784 Pelger-Huet Anomaly 7
C16.320.812 Pycnodysostosis 2
C16.320.925 Werner Syndrome 14

ACTH Deficiency, Isolated Disease MeSH Browser

Adrenocortical Hypofunction, Chronic Primary Congenital Disease MeSH Browser

Alpha-2-Deficient Collagen Disease Disease MeSH Browser

Atrial Standstill Disease MeSH Browser

Cerebral Palsy, Ataxic, Autosomal Recessive Disease MeSH Browser

Cirrhosis, Familial Disease MeSH Browser

Corticosteroid-Binding Globulin Deficiency Disease MeSH Browser

Cryoglobulinemia, Familial Mixed Disease MeSH Browser

Epistaxis, Hereditary Disease MeSH Browser

Hepatic Fibrosis, Congenital Disease MeSH Browser

Hereditary Myopathy with Early Respiratory Failure Disease MeSH Browser

Histiocytosis, Familial Lipochrome Disease MeSH Browser

Interstitial Pneumonitis, Desquamative, Familial Disease MeSH Browser

Neutropenia, Nonimmune Chronic Idiopathic, Adult Disease MeSH Browser

Parotidomegaly, Hereditary Bilateral Disease MeSH Browser

Platelet Glycoprotein IV Deficiency Disease MeSH Browser

Prolactin Deficiency, Isolated Disease MeSH Browser

Pulmonary Alveolar Microlithiasis Disease MeSH Browser

Rh Deficiency Syndrome Disease MeSH Browser