Familial Multiple Lipomatosis [familiární mnohočetná lipomatóza]

topical
Terms

adiposis dolorosa typu III
Dercumova choroba typu III
Dercumova nemoc typu III
familiální mnohočetná lipomatóza
lipoma dolorosa

 

Adiposis Dolorosa Type III
Dercum's Disease Type III
Familial Multiple Lipomas
Lipoma Dolorosa

Definition

A rare autosomal disorder characterized by numerous encapsulated lipomas on the trunk and extremities. The lipomas are usually not painful but can cause pain when growing. In rare cases, one lipoma can become painful and progress to multiple painful lipomas; it is then referred to as Dercum's Disease Type III

DUI
D000071070 MeSH Browser
CUI
M000612991
Previous indexing
Lipomatosis (1973-2016)
History note
2017
Public note
2017

C Diseases
C16.320.051 Alagille Syndrome 19
C16.320.100 Brugada Syndrome 40
C16.320.129 CADASIL 8
C16.320.165 CHARGE Syndrome 1
C16.320.170 Cherubism 1
C16.320.180 Chromosome Disorders 259
C16.320.184 Ciliopathies 9
C16.320.188 Costello Syndrome 3
C16.320.190 Cystic Fibrosis 1 328
C16.320.215 Donohue Syndrome 1
C16.320.240 Dwarfism 97
C16.320.306 Frasier Syndrome
C16.320.314 GATA2 Deficiency 1
C16.320.365 Hemoglobinopathies 68
C16.320.467 Kallmann Syndrome 10
C16.320.480 Kartagener Syndrome 46
C16.320.488 Laminopathies 2
C16.320.540 Marfan Syndrome 105
C16.320.577 Muscular Dystrophies 140
C16.320.728 Osteochondrodysplasias 123
C16.320.784 Pelger-Huet Anomaly 7
C16.320.812 Pycnodysostosis 2
C16.320.925 Werner Syndrome 14
C17.800 Skin Diseases 2 796
C17.800.463 Lipomatosis 36
C17.800.463.249 Adiposis Dolorosa 2
C18.452 Metabolic Diseases 1 196
C18.452.584.718 Lipomatosis 36
C18.452.584.718.500 Adiposis Dolorosa 2
C18.452.584.718.875 Shwachman-Diamond Syndrome 2