Myasthenic Syndromes, Congenital [kongenitální myastenické syndromy]

topical
21
Terms

kongenitální myastenické syndromy, postsynaptické
kongenitální myastenické syndromy, presynaptické
kongenitální myastenie
myastenické syndromy vrozené
vrozené myastenické syndromy

 

Congenital Myasthenia
Congenital Myasthenia Gravis
Congenital Myasthenic Syndrome
Congenital Myasthenic Syndromes
Congenital Myasthenic Syndromes, Postsynaptic
Congenital Myasthenic Syndromes, Presynaptic
Congenital Slow-Channel Myasthenic Syndrome
Congenital Slow-Channel Myasthenic Syndromes
Myasthenia Gravis, Congenital
Myasthenic Syndrome, Congenital, Slow-Channel
Myasthenic Syndromes, Congenital, Slow Channel
Postsynaptic Congenital Myasthenic Syndrome
Postsynaptic Congenital Myasthenic Syndromes
Presynaptic Congenital Myasthenic Syndrome
Presynaptic Congenital Myasthenic Syndromes
Slow-Channel Congenital Myasthenic Syndrome
Slow-Channel Congenital Myasthenic Syndromes

Persistent link   https://www.medvik.cz/link/D020294
Definition

A heterogeneous group of disorders characterized by a congenital defect in neuromuscular transmission at the NEUROMUSCULAR JUNCTION. This includes presynaptic, synaptic, and postsynaptic disorders (that are not of autoimmune origin). The majority of these diseases are caused by mutations of various subunits of the nicotinic acetylcholine receptor (RECEPTORS, NICOTINIC) on the postsynaptic surface of the junction. (From Arch Neurol 1999 Feb;56(2):163-7)

Annotation
do not confuse with MYASTHENIA GRAVIS, NEONATAL, a transient condition seen in neonates born to myasthenic mothers
DUI
D020294 MeSH Browser
CUI
M0328231
Previous indexing
Myasthenia Gravis/congenital (1970-1999)
History note
2000
Public note
2000

C Diseases
C10.668.758.200 Botulism 71
C10.668.758.725 Myasthenia Gravis 422
C16.320.051 Alagille Syndrome 19
C16.320.100 Brugada Syndrome 40
C16.320.129 CADASIL 8
C16.320.165 CHARGE Syndrome 1
C16.320.170 Cherubism 1
C16.320.180 Chromosome Disorders 260
C16.320.184 Ciliopathies 9
C16.320.188 Costello Syndrome 3
C16.320.190 Cystic Fibrosis 1 330
C16.320.215 Donohue Syndrome 1
C16.320.240 Dwarfism 99
C16.320.306 Frasier Syndrome
C16.320.314 GATA2 Deficiency 2
C16.320.365 Hemoglobinopathies 68
C16.320.467 Kallmann Syndrome 10
C16.320.480 Kartagener Syndrome 46
C16.320.488 Laminopathies 2
C16.320.540 Marfan Syndrome 105
C16.320.577 Muscular Dystrophies 141
C16.320.728 Osteochondrodysplasias 125
C16.320.784 Pelger-Huet Anomaly 7
C16.320.812 Pycnodysostosis 2
C16.320.925 Werner Syndrome 14

Congenital myasthenic syndrome ib Disease MeSH Browser

Endplate Acetylcholinesterase Deficiency Disease MeSH Browser

Myasthenia, Congenital, Refractory to Acetylcholinesterase Inhibitors Disease MeSH Browser

Myasthenia, Familial Infantile, 1 Disease MeSH Browser

Myasthenia, Limb-Girdle, Autoimmune Disease MeSH Browser

Myasthenia, Limb-Girdle, with Tubular Aggregates Disease MeSH Browser

Myasthenic Syndrome due to Mutation in SCN4A Disease MeSH Browser

Myasthenic Syndrome, Congenital, Associated with Facial Dysmorphism Disease MeSH Browser

Myasthenic Syndrome, Congenital, Fast-Channel Disease MeSH Browser

Myasthenic Syndrome, Congenital, Ie Disease MeSH Browser

Myasthenic Syndrome, Congenital, with Facial Dysmorphism, associated with Acetylcholine Receptor Deficiency Disease MeSH Browser

Myasthenic syndrome, congenital, postsynaptic slow-channel Disease MeSH Browser

Myasthenic syndrome, congenital, type Id Disease MeSH Browser

Myopathy, Congenital, Compton-North Disease MeSH Browser

Pierson syndrome Disease MeSH Browser