Brugada Syndrome [Brugadův syndrom]

topical
40
Terms

Brugada syndrom
Brugadův syndrom - EKG
Brugadův syndrom typ 1
EKG obraz Brugadova syndromu
EKG syndromu Brugadových
syndrom Brugadových

 

Brugada ECG Pattern
Brugada Syndrome 1
Brugada Type ECG Pattern
Right Bundle Branch Block, ST Segment Elevation, and Sudden Death Syndrome
Sudden Unexplained Death Syndrome
Sudden Unexplained Nocturnal Death Syndrome
Sudden Unexplained Nocturnal Death Syndrome (SUNDS)

Persistent link   https://www.medvik.cz/link/D053840
Definition

An autosomal dominant defect of cardiac conduction that is characterized by an abnormal ST-segment in leads V1-V3 on the ELECTROCARDIOGRAM resembling a right BUNDLE-BRANCH BLOCK; high risk of VENTRICULAR TACHYCARDIA; or VENTRICULAR FIBRILLATION; SYNCOPAL EPISODE; and possible sudden death. This syndrome is linked to mutations of gene encoding the cardiac SODIUM CHANNEL alpha subunit.

DUI
D053840 MeSH Browser
CUI
M0496826
Previous indexing
Arrhythmia (1996-2006)
History note
2007
Public note
2007

C Diseases
C14.280 Heart Diseases 2 860
C14.280.067 Arrhythmias, Cardiac 2 786
C14.280.067.093 Arrhythmia, Sinus 40
C14.280.067.198 Atrial Fibrillation 2 056
C14.280.067.248 Atrial Flutter 139
C14.280.067.319 Bradycardia 274
C14.280.067.322 Brugada Syndrome 40
C14.280.067.441 Commotio Cordis 5
C14.280.067.558 Heart Block 232
C14.280.067.565 Long QT Syndrome 217
C14.280.067.672 Parasystole 1
C14.280.067.780 Pre-Excitation Syndromes 17
C14.280.067.845 Tachycardia 468
C14.280.067.922 Ventricular Fibrillation 389
C14.280.067.961 Ventricular Flutter 13
C14.280.123.250 Brugada Syndrome 40
C14.280.123.500 Heart Block 232
C14.280.123.625 Long QT Syndrome 217
C14.280.123.750 Pre-Excitation Syndromes 17
C14.280.123.875 Tachycardia 468
C16.320.051 Alagille Syndrome 19
C16.320.100 Brugada Syndrome 40
C16.320.129 CADASIL 8
C16.320.165 CHARGE Syndrome 1
C16.320.170 Cherubism 1
C16.320.180 Chromosome Disorders 259
C16.320.184 Ciliopathies 9
C16.320.188 Costello Syndrome 3
C16.320.190 Cystic Fibrosis 1 328
C16.320.215 Donohue Syndrome 1
C16.320.240 Dwarfism 97
C16.320.306 Frasier Syndrome
C16.320.314 GATA2 Deficiency 1
C16.320.365 Hemoglobinopathies 68
C16.320.467 Kallmann Syndrome 10
C16.320.480 Kartagener Syndrome 46
C16.320.488 Laminopathies 2
C16.320.540 Marfan Syndrome 105
C16.320.577 Muscular Dystrophies 140
C16.320.728 Osteochondrodysplasias 123
C16.320.784 Pelger-Huet Anomaly 7
C16.320.812 Pycnodysostosis 2
C16.320.925 Werner Syndrome 14