Nevus, Sebaceous of Jadassohn [Jadassohnův sebaceózní névus]

topical
7
Terms

Feuersteinův-Mimsův syndrom
ILVEN
inflamatorní lineární verukosní epidermální névus
inflamatorní lineární verukózní epidermální névus
Jadassohnův naevus sebaceus
lineární naevus sebaceus
lineární sebaceózní névus
lineární verukosní epidermální névus
lineární verukózní epidermální névus
naevus sebaceus
Schimmelpenningův syndrom
Schimmelpenningův-Feuersteinův-Mimsův syndrom
verukosní névus
verukózní névus

 

Feuerstein-Mims Syndrome
Inflammatory Linear Verrucose Epidermal Nevus
Inflammatory Linear Verrucous Epidermal Naevus
Jadassohn Nevus Phakomatosis
Linear Sebaceous Nevus Syndrome
Linear Verrucous Epidermal Nevus
Nevus Sebaceus of Jadassohn
Nevus, Linear Sebaceous
Organoid Nevus Phakomatosis
Schimmelpenning Syndrome
Schimmelpenning-Feuerstein-Mims Syndrome
Sebaceous Nevus of Jadassohn
Sebaceous Nevus Syndrome, Linear
Verrucous Epidermal Nevus
Verrucous Nevus

Persistent link   https://www.medvik.cz/link/D054000
Definition

A syndrome characterized by lesions occurring on the face, scalp, or neck which consist of congenital hypoplastic malformations of cutaneous structures and which over time undergo verrucous hyperplasia. Additionally it is associated with neurological symptoms and skeletal, ophthalmological, urogenital, and cardiovascular abnormalities.

DUI
D054000 MeSH Browser
CUI
M0499750
Previous indexing
Nevus or specifics (1967-2007)
History note
2010 (2008)
Public note
2010; see NEVUS SEBACEOUS OF JADASSOHN 2008-2009

C Diseases
C04 Neoplasms 12 762
C04.557.665 Nevi and Melanomas 63
C04.557.665.560 Nevus 144
C04.557.665.560.260 Dysplastic Nevus Syndrome 17
C04.557.665.560.580 Nevus, Halo 1
C04.557.665.560.590 Nevus, Intradermal 7
C04.557.665.560.615 Nevus, Pigmented 104
C04.557.665.560.700 Nevus, Sebaceous of Jadassohn 7
C10.562.600 Neurofibromatoses 28
C10.562.850 Tuberous Sclerosis 141
C16.131.077.019 22q11 Deletion Syndrome 2
C16.131.077.065 Alagille Syndrome 19
C16.131.077.095 Angelman Syndrome 35
C16.131.077.121 Barth Syndrome 6
C16.131.077.130 Basal Cell Nevus Syndrome 32
C16.131.077.137 Bloom Syndrome 11
C16.131.077.229 Carney Complex 8
C16.131.077.245 Ciliopathies 9
C16.131.077.250 Cockayne Syndrome 4
C16.131.077.256 Costello Syndrome 3
C16.131.077.262 Cri-du-Chat Syndrome 11
C16.131.077.272 De Lange Syndrome 4
C16.131.077.299 Deaf-Blind Disorders 65
C16.131.077.313 Donohue Syndrome 1
C16.131.077.327 Down Syndrome 510
C16.131.077.350 Ectodermal Dysplasia 33
C16.131.077.371 Fraser Syndrome 2
C16.131.077.393 Gardner Syndrome 20
C16.131.077.401 Heterotaxy Syndrome 7
C16.131.077.410 Holoprosencephaly 8
C16.131.077.445 Incontinentia Pigmenti 19
C16.131.077.509 Laurence-Moon Syndrome 6
C16.131.077.525 LEOPARD Syndrome 11
C16.131.077.537 Loeys-Dietz Syndrome 7
C16.131.077.550 Marfan Syndrome 105
C16.131.077.578 Mobius Syndrome 10
C16.131.077.592 Monilethrix 1
C16.131.077.606 Nail-Patella Syndrome 8
C16.131.077.619 Netherton Syndrome 2
C16.131.077.676 Orofaciodigital Syndromes 7
C16.131.077.696 Pentalogy of Cantrell 1
C16.131.077.703 POEMS Syndrome 34
C16.131.077.717 Polycystic Kidney Diseases 82
C16.131.077.730 Prader-Willi Syndrome 91
C16.131.077.735 Prolidase Deficiency
C16.131.077.740 Proteus Syndrome 8
C16.131.077.745 Prune Belly Syndrome 3
C16.131.077.804 Rubinstein-Taybi Syndrome 12
C16.131.077.855 Silver-Russell Syndrome 3
C16.131.077.860 Smith-Lemli-Opitz Syndrome 30
C16.131.077.879 Smith-Magenis Syndrome 2
C16.131.077.889 Sotos Syndrome 4
C16.131.077.919 Trisomy 13 Syndrome 6
C16.131.077.929 Trisomy 18 Syndrome 5
C16.131.077.938 Waardenburg Syndrome 10
C16.131.077.941 Weill-Marchesani Syndrome 1
C16.131.077.970 Zellweger Syndrome 10