Polycystic Kidney Diseases [polycystická choroba ledvin]

topical
82
Terms

ledviny - polycystické nemoci
polycystické ledviny
polycystické onemocnění ledvin

 

Kidney, Polycystic
Polycystic Kidney
Polycystic Kidney Disease
Polycystic Kidneys
Polycystic Renal Disease

Persistent link   https://www.medvik.cz/link/D007690
Definition

Hereditary diseases that are characterized by the progressive expansion of a large number of tightly packed CYSTS within the KIDNEYS. They include diseases with autosomal dominant and autosomal recessive inheritance.

Annotation
KIDNEY, CYSTIC and MULTICYSTIC DYSPLASTIC KIDNEY are also available; prefer specifics
DUI
D007690 MeSH Browser
CUI
M0012031
History note
1991
Public note
1991; see POLYCYSTIC KIDNEY 1991-2000

C Diseases
C12.050.351.968 Urologic Diseases 834
C12.050.351.968.419 Kidney Diseases 3 060
C12.050.351.968.419.403 Kidney Diseases, Cystic 148
C12.050.351.968.419.403.500 Medullary Sponge Kidney 3
C12.050.351.968.419.403.750 Multicystic Dysplastic Kidney 15
C12.050.351.968.419.403.875 Polycystic Kidney Diseases 82
C12.050.351.968.419.403.875.500 Polycystic Kidney, Autosomal Dominant 121
C12.050.351.968.419.403.875.510 Polycystic Kidney, Autosomal Recessive 29
C12.200.777 Urologic Diseases 834
C12.200.777.419 Kidney Diseases 3 060
C12.200.777.419.403 Kidney Diseases, Cystic 148
C12.200.777.419.403.500 Medullary Sponge Kidney 3
C12.200.777.419.403.750 Multicystic Dysplastic Kidney 15
C12.200.777.419.403.875 Polycystic Kidney Diseases 82
C12.200.777.419.403.875.500 Polycystic Kidney, Autosomal Dominant 121
C12.200.777.419.403.875.510 Polycystic Kidney, Autosomal Recessive 29
C12.950.419 Kidney Diseases 3 060
C12.950.419.403 Kidney Diseases, Cystic 148
C12.950.419.403.500 Medullary Sponge Kidney 3
C12.950.419.403.750 Multicystic Dysplastic Kidney 15
C12.950.419.403.875 Polycystic Kidney Diseases 82
C12.950.419.403.875.500 Polycystic Kidney, Autosomal Dominant 121
C12.950.419.403.875.510 Polycystic Kidney, Autosomal Recessive 29
C16.131.077.019 22q11 Deletion Syndrome 2
C16.131.077.065 Alagille Syndrome 19
C16.131.077.095 Angelman Syndrome 35
C16.131.077.121 Barth Syndrome 6
C16.131.077.130 Basal Cell Nevus Syndrome 33
C16.131.077.137 Bloom Syndrome 11
C16.131.077.229 Carney Complex 8
C16.131.077.245 Ciliopathies 9
C16.131.077.250 Cockayne Syndrome 4
C16.131.077.256 Costello Syndrome 3
C16.131.077.262 Cri-du-Chat Syndrome 11
C16.131.077.272 De Lange Syndrome 4
C16.131.077.299 Deaf-Blind Disorders 65
C16.131.077.313 Donohue Syndrome 1
C16.131.077.327 Down Syndrome 510
C16.131.077.350 Ectodermal Dysplasia 33
C16.131.077.371 Fraser Syndrome 2
C16.131.077.393 Gardner Syndrome 20
C16.131.077.401 Heterotaxy Syndrome 7
C16.131.077.410 Holoprosencephaly 8
C16.131.077.445 Incontinentia Pigmenti 19
C16.131.077.509 Laurence-Moon Syndrome 6
C16.131.077.525 LEOPARD Syndrome 11
C16.131.077.537 Loeys-Dietz Syndrome 7
C16.131.077.550 Marfan Syndrome 105
C16.131.077.578 Mobius Syndrome 10
C16.131.077.592 Monilethrix 1
C16.131.077.606 Nail-Patella Syndrome 8
C16.131.077.619 Netherton Syndrome 2
C16.131.077.676 Orofaciodigital Syndromes 7
C16.131.077.696 Pentalogy of Cantrell 1
C16.131.077.703 POEMS Syndrome 35
C16.131.077.717 Polycystic Kidney Diseases 82
C16.131.077.730 Prader-Willi Syndrome 92
C16.131.077.735 Prolidase Deficiency
C16.131.077.740 Proteus Syndrome 8
C16.131.077.745 Prune Belly Syndrome 3
C16.131.077.804 Rubinstein-Taybi Syndrome 12
C16.131.077.855 Silver-Russell Syndrome 3
C16.131.077.860 Smith-Lemli-Opitz Syndrome 30
C16.131.077.879 Smith-Magenis Syndrome 2
C16.131.077.889 Sotos Syndrome 4
C16.131.077.919 Trisomy 13 Syndrome 6
C16.131.077.929 Trisomy 18 Syndrome 5
C16.131.077.938 Waardenburg Syndrome 10
C16.131.077.941 Weill-Marchesani Syndrome 1
C16.131.077.970 Zellweger Syndrome 10
C16.320.184 Ciliopathies 9
C16.320.184.063 Alstrom Syndrome 1
C16.320.184.125 Bardet-Biedl Syndrome 18
C16.320.184.250 Caroli Disease 6
C16.320.184.500 Ciliary Motility Disorders 57
C16.320.184.625 Polycystic Kidney Diseases 82
C16.320.184.750 von Hippel-Lindau Disease 56

Arima syndrome Disease MeSH Browser

Cerebellar Vermis Aplasia with Associated Features suggesting Smith-Lemli-Opitz Syndrome and Meckel Syndrome Disease MeSH Browser

Daneman Davy Mancer syndrome Disease MeSH Browser

Meckel Syndrome, Type 4 Disease MeSH Browser

Meckel Syndrome, Type 5 Disease MeSH Browser

Meckel Syndrome, Type 6 Disease MeSH Browser

Meckel syndrome type 1 Disease MeSH Browser

Meckel syndrome type 2 Disease MeSH Browser

Meckel syndrome type 3 Disease MeSH Browser

Meckel-Like Cerebrorenodigital Syndrome Disease MeSH Browser

Polycystic Kidney, Cataract, and Congenital Blindness Disease MeSH Browser

Polycystic kidney disease, type 1 Disease MeSH Browser

Potter Type III Polycystic Kidney Disease Disease MeSH Browser