genetické nemoci vázané na chromozom X [Genetic Diseases, X-Linked]

tematický
59
Termíny

genetické nemoci vázané na chromozóm X

 

Genetic Diseases, X-Chromosome Linked
X-Linked Genetic Diseases

Perzistentní odkaz   https://www.medvik.cz/link/D040181
Definice

Dědičné nemoci vázané na mutace genů na chromozomu X (u lidí či jiných druhů nesoucích chromozom X). Patří sem také zvířecí modely nemocí vázaných na chromozom X u lidí.

Genetic diseases that are linked to gene mutations on the X CHROMOSOME in humans (X CHROMOSOME, HUMAN) or the X CHROMOSOME in other species. Included here are animal models of human X-linked diseases.

DUI
D040181 MeSH Prohlížeč
CUI
M0420489
Předchozí užití
Genetic Diseases, Inborn (1966-2002); Linkage (Genetics) (1984-2002); specific disease/Genetics (1984-2002)
Historická pozn.
2003
Veřejná pozn.
2003

C Nemoci
C01 infekce 2 026
C04 nádory 12 774
C11 oční nemoci 1 489
C16.320.051 Alagillův syndrom 19
C16.320.100 Brugadův syndrom 40
C16.320.129 CADASIL 8
C16.320.165 CHARGE syndrom 1
C16.320.170 cherubismus 1
C16.320.184 ciliopatie 9
C16.320.188 Costellův syndrom 3
C16.320.190 cystická fibróza 1 328
C16.320.215 Donohueův syndrom 1
C16.320.240 nanismus 97
C16.320.306 syndrom Frasier
C16.320.314 deficit GATA2 1
C16.320.322.030 Aicardiho syndrom
C16.320.322.068 Barthův syndrom 6
C16.320.322.092 choroideremie 3
C16.320.322.100 Dentova choroba 1
C16.320.322.108 dyskeratosis congenita 9
C16.320.322.124 Fabryho nemoc 187
C16.320.322.201 glykogenóza typu IIb 11
C16.320.322.217 glykogenóza typu VIII
C16.320.322.235 hemofilie B 214
C16.320.365 hemoglobinopatie 68
C16.320.467 Kallmannův syndrom 10
C16.320.488 laminopatie 2
C16.320.540 Marfanův syndrom 105
C16.320.577 svalové dystrofie 140
C16.320.728 osteochondrodysplazie 123
C16.320.812 pyknodysostóza 2
C16.320.925 Wernerův syndrom 14

Aarskog Syndrome Disease MeSH Prohlížeč

Abruzzo Erickson syndrome Disease MeSH Prohlížeč

Achromatopsia incomplete, X-linked Disease MeSH Prohlížeč

Adrenal Hypoplasia, Congenital, with Precocious Puberty Disease MeSH Prohlížeč

Agammaglobulinemia, X-linked, type 2 Disease MeSH Prohlížeč

Aland Island Eye Disease Disease MeSH Prohlížeč

Alpha-Thalassemia Myelodysplasia Syndrome Disease MeSH Prohlížeč

Alport Syndrome, Mental Retardation, Midface Hypoplasia, and Elliptocytosis Disease MeSH Prohlížeč

Alzheimer Disease 16 Disease MeSH Prohlížeč

Anemia, Nonspherocytic Hemolytic, Due To G6pd Deficiency Disease MeSH Prohlížeč

Anemia, X-Linked, without Thrombocytopenia Disease MeSH Prohlížeč

Anemia, sideroblastic spinocerebellar ataxia Disease MeSH Prohlížeč

Anencephaly and spina bifida X-linked Disease MeSH Prohlížeč

Aneurysm, Intracranial Berry, 5 Disease MeSH Prohlížeč

Angioma serpiginosum, X-linked Disease MeSH Prohlížeč

Arthrogryposis multiplex congenita, distal, X-linked Disease MeSH Prohlížeč

Arthrogryposis, X-Linked, Type V Disease MeSH Prohlížeč

Arts syndrome Disease MeSH Prohlížeč

Atypical Mycobacteriosis, Familial, X-Linked 2 Disease MeSH Prohlížeč

Bornholm Eye Disease Disease MeSH Prohlížeč

Brain Anomalies, Retardation, Ectodermal Dysplasia, Skeletal Malformations, Hirschsprung Disease, Ear-Eye Anomalies, Cleft Palate-Cryptorchidism, And Kidney Dysplasia-Hypoplasia Disease MeSH Prohlížeč

Branchial arch syndrome X-linked Disease MeSH Prohlížeč

Brunner Syndrome Disease MeSH Prohlížeč

Bruton type agammaglobulinemia Disease MeSH Prohlížeč

Bullous Dystrophy, Hereditary Macular Type Disease MeSH Prohlížeč

Cardiac valvular dysplasia, X-linked Disease MeSH Prohlížeč

Cardiomyopathy, Dilated, 3A Disease MeSH Prohlížeč

Cataract, congenital, with microcornea or slight microphthalmia Disease MeSH Prohlížeč

Chromosome Xp11.23-P11.22 Duplication Syndrome Disease MeSH Prohlížeč

Chromosome Xq28 Duplication Syndrome Disease MeSH Prohlížeč

Cleft Palate with Ankyloglossia Disease MeSH Prohlížeč

Cleft palate X-linked Disease MeSH Prohlížeč

Cone Dystrophy, X-Linked, 1 Disease MeSH Prohlížeč

Cone dystrophy, x-linked, with tapetal-like sheen Disease MeSH Prohlížeč

Cone-Rod Dystrophy, X-Linked, 2 Disease MeSH Prohlížeč

Cone-Rod Dystrophy, X-Linked, 3 Disease MeSH Prohlížeč

Cone-Rod Dystrophy, X-Linked, Type 1 Disease MeSH Prohlížeč

Congenital Heart Defects, X-Linked Disease MeSH Prohlížeč

Congenital Hemidysplasia with Ichthyosiform Erythroderma and Limb Defects Disease MeSH Prohlížeč

Congenital alopecia X-linked Disease MeSH Prohlížeč

Congenital idiopathic intestinal pseudoobstruction Disease MeSH Prohlížeč

Corpus Callosum, Partial Agenesis of, X-Linked Disease MeSH Prohlížeč

Craniofacioskeletal Syndrome Disease MeSH Prohlížeč

Deafness, High-Frequency Sensorineural, X-Linked Disease MeSH Prohlížeč

Deafness, X-Linked 1 Disease MeSH Prohlížeč

Deafness, X-Linked 3 Disease MeSH Prohlížeč

Deafness, X-Linked 4 Disease MeSH Prohlížeč

Deafness, X-Linked 5 Disease MeSH Prohlížeč

Dent Disease 2 Disease MeSH Prohlížeč

Dent disease 1 Disease MeSH Prohlížeč

Dyserythropoietic Anemia with Thrombocytopenia Disease MeSH Prohlížeč

Dystonia 3, Torsion, X-Linked Disease MeSH Prohlížeč

Ectodermal Dysplasia, Anhidrotic, with Immunodeficiency, Osteopetrosis, and Lymphedema Disease MeSH Prohlížeč

Ectodermal dysplasia, hypohidrotic, with immune deficiency Disease MeSH Prohlížeč

Ehlers-Danlos syndrome type 5 Disease MeSH Prohlížeč

Epidermodysplasia Verruciformis, X-Linked Disease MeSH Prohlížeč

Epilepsy, Female-Restricted, with Mental Retardation Disease MeSH Prohlížeč

Epilepsy, X-Linked, with Variable Learning Disabilities and Behavior Disorders Disease MeSH Prohlížeč

Episodic Muscle Weakness, X-Linked Disease MeSH Prohlížeč

Exudative Vitreoretinopathy, Familial, X-Linked Recessive Disease MeSH Prohlížeč

Fetal akinesia syndrome, X-linked Disease MeSH Prohlížeč

Fg Syndrome 5 Disease MeSH Prohlížeč

Glycogen Storage Disease, Type IXA2 Disease MeSH Prohlížeč

Glycogen Storage Disease, Type IXD Disease MeSH Prohlížeč

Heterotaxy, visceral, X-linked Disease MeSH Prohlížeč

Heterotopia, Periventricular Nodular, with Frontometaphyseal Dysplasia Disease MeSH Prohlížeč

Heterotopia, Periventricular, Ehlers-Danlos Variant Disease MeSH Prohlížeč

Hodgkin disease, X-linked pseudoautosomal Disease MeSH Prohlížeč

Hydrocephalus With Cerebellar Agenesis Disease MeSH Prohlížeč

Hydrocephalus, X-Linked, with Congenital Idiopathic Intestinal Pseudoobstruction Disease MeSH Prohlížeč

Hydrocephalus, X-linked Disease MeSH Prohlížeč

Hyperekplexia and Epilepsy Disease MeSH Prohlížeč

Hypertrichosis congenital generalized X-linked Disease MeSH Prohlížeč

Hypogammaglobulinemia and Isolated growth hormone deficiency, X-linked Disease MeSH Prohlížeč

Hypogammaglobulinemia, X-Linked Disease MeSH Prohlížeč

Hypoparathyroidism, X-Linked Disease MeSH Prohlížeč

Hypospadias 1, X-Linked Disease MeSH Prohlížeč

Hypospadias 2, X-Linked Disease MeSH Prohlížeč

Ichthyosis, X-Linked, Complicated Disease MeSH Prohlížeč

Immune Dysregulation, Polyendocrinopathy, Enteropathy, X-Linked Syndrome Disease MeSH Prohlížeč

Immunodeficiency, X-Linked, with Deficiency of 115,000 Dalton Surface Glycoprotein Disease MeSH Prohlížeč

Joubert Syndrome 10 Disease MeSH Prohlížeč

Keratosis Follicularis Spinulosa Decalvans, X-Linked Disease MeSH Prohlížeč

Leigh Syndrome, X-Linked Disease MeSH Prohlížeč

Liver Glycogenosis, X-Linked, Type II Disease MeSH Prohlížeč

Lymphoproliferative Syndrome, X-Linked, 2 Disease MeSH Prohlížeč

MASA (Mental Retardation, Aphasia, Shuffling Gait, Adducted Thumbs) Syndrome Disease MeSH Prohlížeč

Macrothrombocytopenia, X-Linked Disease MeSH Prohlížeč

Macular Dystrophy, X-Linked Disease MeSH Prohlížeč

Major Affective Disorder 2 Disease MeSH Prohlížeč

Martin-Probst Deafness-Mental Retardation Syndrome Disease MeSH Prohlížeč

Megalocornea Disease MeSH Prohlížeč

Membranoproliferative Glomerulonephritis, X-Linked Disease MeSH Prohlížeč

Mental Retardation, Skeletal Dysplasia, and Abducens Palsy Disease MeSH Prohlížeč

Mental Retardation, X-Linked, Syndromic 12 Disease MeSH Prohlížeč

Mental Retardation, X-Linked, Syndromic, Christianson Type Disease MeSH Prohlížeč

Mental Retardation, X-Linked, Syndromic, Turner Type Disease MeSH Prohlížeč

Mental Retardation, X-Linked, Syndromic, Zdhhc9-Related Disease MeSH Prohlížeč

Mental Retardation, X-Linked, With Panhypopituitarism Disease MeSH Prohlížeč

Mental Retardation, X-Linked, Znf711-Related Disease MeSH Prohlížeč

Microphthalmia, Isolated, with Coloboma 1 Disease MeSH Prohlížeč

Microphthalmia, syndromic 7 Disease MeSH Prohlížeč

Midline Defects, X-Linked Disease MeSH Prohlížeč

Modifier, X-Linked, for Neurofunctional Defects Disease MeSH Prohlížeč

Multiple Pterygium Syndrome, X-Linked Disease MeSH Prohlížeč

Muscular Dystrophy, Progressive Pectorodorsal Disease MeSH Prohlížeč

Myopathy, Reducing Body, X-Linked, Childhood-Onset Disease MeSH Prohlížeč

Myopathy, Reducing Body, X-Linked, Early-Onset, Severe Disease MeSH Prohlížeč

Myopathy, X-Linked, with Excessive Autophagy Disease MeSH Prohlížeč

Myopia 1 Disease MeSH Prohlížeč

Myopia 13 Disease MeSH Prohlížeč

NEMO mutation with immunodeficiency Disease MeSH Prohlížeč

Nance-Horan syndrome Disease MeSH Prohlížeč

Nasodigitoacoustic syndrome Disease MeSH Prohlížeč

Nephrogenic Syndrome of Inappropriate Antidiuresis Disease MeSH Prohlížeč

Nephrolithiasis, X-Linked Recessive, with Renal Failure Disease MeSH Prohlížeč

Neural tube defects X-linked Disease MeSH Prohlížeč

Neuropathy, Hereditary Sensory, X-Linked Disease MeSH Prohlížeč

Neutropenia, Severe Congenital, X-Linked Disease MeSH Prohlížeč

Night blindness, congenital stationary Disease MeSH Prohlížeč

Norrie disease Disease MeSH Prohlížeč

Nystagmus 5, Infantile Periodic Alternating Disease MeSH Prohlížeč

Ophthalmoplegia, External, and Myopia Disease MeSH Prohlížeč

Opitz GBBB Syndrome, X-Linked Disease MeSH Prohlížeč

Optic atrophy, X-linked Disease MeSH Prohlížeč

Ovarian Dysgenesis 2 Disease MeSH Prohlížeč

Panhypopituitarism X-linked Disease MeSH Prohlížeč

Parathyroid Glands, Agenesis Of Disease MeSH Prohlížeč

Parkinson Disease 12 Disease MeSH Prohlížeč

Parkinsonism, early onset with mental retardation Disease MeSH Prohlížeč

Phosphoglycerate Kinase 1 Deficiency Disease MeSH Prohlížeč

Pigmentary Disorder, Reticulate, with Systemic Manifestations Disease MeSH Prohlížeč

Premature Ovarian Failure 2a Disease MeSH Prohlížeč

Progressive hearing loss stapes fixation Disease MeSH Prohlížeč

Properdin Deficiency, Type II Disease MeSH Prohlížeč

Properdin Deficiency, Type III Disease MeSH Prohlížeč

Properdin deficiency, X-linked Disease MeSH Prohlížeč

Prostate Cancer, Hereditary, X-Linked 2 Disease MeSH Prohlížeč

Protoporphyria, Erythropoietic, X-Linked Dominant Disease MeSH Prohlížeč

Proud Syndrome Disease MeSH Prohlížeč

Ptosis, Hereditary Congenital 2 Disease MeSH Prohlížeč

Radial Ray Deficiency, X-Linked Disease MeSH Prohlížeč

Radiation Sensitivity of Natural Killer Activity Disease MeSH Prohlížeč

Radius absent anogenital anomalies Disease MeSH Prohlížeč

Reticuloendotheliosis, X-linked Disease MeSH Prohlížeč

Retinitis Pigmentosa 3 Disease MeSH Prohlížeč

Retinitis Pigmentosa 34 Disease MeSH Prohlížeč

Retinitis Pigmentosa 6 Disease MeSH Prohlížeč

Retinitis Pigmentosa, X-Linked, And Sinorespiratory Infections, With Or Without Deafness Disease MeSH Prohlížeč

Rolandic Epilepsy, Mental Retardation, and Speech Dyspraxia, X-Linked Disease MeSH Prohlížeč

Russell-Silver Syndrome, X-Linked Disease MeSH Prohlížeč

Short Stature, Idiopathic, X-Linked Disease MeSH Prohlížeč

Simpson-Golabi-Behmel Syndrome, Type 2 Disease MeSH Prohlížeč

Simpson-Golabi-Behmel syndrome Disease MeSH Prohlížeč

Skeletal dysplasia coarse facies mental retardation Disease MeSH Prohlížeč

Spastic Paraplegia 34, X-Linked Disease MeSH Prohlížeč

Spastic paraplegia 16, X-linked Disease MeSH Prohlížeč

Spastic paraplegia 2, X-linked Disease MeSH Prohlížeč

Spina Bifida, X-Linked Disease MeSH Prohlížeč

Spinal Muscular Atrophy, Distal, X-Linked 3 Disease MeSH Prohlížeč

Spinocerebellar Ataxia, X-Linked 1 Disease MeSH Prohlížeč

Spinocerebellar Ataxia, X-Linked 5 Disease MeSH Prohlížeč

Spinocerebellar ataxia, X-linked, 3 Disease MeSH Prohlížeč

Split-Hand Foot Malformation 2 Disease MeSH Prohlížeč

Spondyloepimetaphyseal Dysplasia, X-Linked Disease MeSH Prohlížeč

Spondylometaphyseal Dysplasia, X-Linked Disease MeSH Prohlížeč

Surfactant Metabolism Dysfunction, Pulmonary, 4 Disease MeSH Prohlížeč

Terminal Osseous Dysplasia and Pigmentary Defects Disease MeSH Prohlížeč

Testicular Germ Cell Tumor 1 Disease MeSH Prohlížeč

Thrombocytopenia 1 Disease MeSH Prohlížeč

Thrombocytopenia, Platelet Dysfunction, Hemolysis, and Imbalanced Globin Synthesis Disease MeSH Prohlížeč

Thrombocytopenia, X-Linked, Intermittent Disease MeSH Prohlížeč

Thrombocytosis, Familial X-Linked Disease MeSH Prohlížeč

Thrombophilia, X-Linked, Due To Factor Ix Defect Disease MeSH Prohlížeč

Thyroxine-Binding Globulin Deficiency Disease MeSH Prohlížeč

Tooth Agenesis, Selective, X-Linked, 1 Disease MeSH Prohlížeč

Torticollis keloids cryptorchidism renal dysplasia Disease MeSH Prohlížeč

VACTERL Association With Hydrocephalus Disease MeSH Prohlížeč

Vasquez Hurst Sotos syndrome Disease MeSH Prohlížeč

Vesicoureteral Reflux, X-Linked Disease MeSH Prohlížeč

Von Willebrand Disease, X-Linked Form Disease MeSH Prohlížeč

Wells Jankovic syndrome Disease MeSH Prohlížeč

Wieacker syndrome Disease MeSH Prohlížeč

X Inactivation, Familial Skewed, 1 Disease MeSH Prohlížeč

X Inactivation, Familial Skewed, 2 Disease MeSH Prohlížeč

X-Linked Chondrodysplasia Punctata 1 Disease MeSH Prohlížeč

X-Linked Infantile Nystagmus Disease MeSH Prohlížeč

X-linked sideroblastic anemia Disease MeSH Prohlížeč

X-linked tetra-amelia Disease MeSH Prohlížeč